Hauora, Rongoā
Raina e kitea kanohi mua Blashko i runga i te tinana tangata
Äta ki te tauira kanohi tahanga i runga i te tinana tangata puta i raro i te mana o ngā āhuatanga kino endogenous me exogenous. Whakaritea e te māuiuitanga rite raina Blashko. whakakitea Melanogenesis hypopigmentation, pā ana ki te rōpū o mate dermatoses. Ari moni Koló ki pūtaiao. Mahino te parau tumu o te ahua o te puku, he reira taea ki te ārai i te ahua o te tonapuku.
Ko te hītori o te ako o mate kiri
kairangahau German raruraru Dermatological kitea aho Blashko i 1901. tohu ratou he tauira o te ähua, rite i roto i te hanganga ki te tūroro katoa. te ingoa i te mate i muri i te ingoa o te kaiputaiao, tona ingoa ko Alfred.
Dermatologist whakapumautia hononga ki te takanga o te māuiuitanga X-pūira. I te kiri huringa äta hauora i roto i to ratou kukū noa. Ka rite ki te hua o te hekenga huru malanoblastov te hanganga o te tauira rohe kitea. Tūnga o ngā pūtau mutated he ti'aturi i runga i breakdowns io o te tinana. Heoi, e taea raruraru Dermatological te kitea i roto i te kainga tupu congenital o te mate.
Ko te take matua mō ngā ine te kiri tangata o
Te tautuhi i te āhuatanga e whai ake nei te rārangi Mātauranga Blashko i runga i te tinana:
- Chimerism - maha tuku ki rite te huru ina mataara te tangata e rua ngā momo o te DNA. He huinga rerekē o ira pāngia e te hanganga o te ähua i runga i te tinana. whakakitea ēnei pānga tahanga ki iwi e rua rerekē. Take o te māuiuitanga kiri riro te hononga o te hua manu wairakau i te wā wawe o te hapūtanga.
- tāne i te ahotea Human - i hanga te tauira huru te.
- Genetics - huringa i roto i te DNA tangata. Ko te take mo te ahua o te māuiuitanga congenital riro nevi: depigmented, pigmented, sebaceous, rārangi verrucous inflammatory.
- kitea i roto i te kotahi huinga whare herehere o ira te: eke pūtaiao hanganga o te kopa tangata - DNA Mixing ira i roto i embryogenesis. Ahakoa ahu te takenga o te muri kei i te whakatō kākano kotahi.
Ko te āhua o te ahua o te dermatosis
He mea matekiri ki kore mohio i te wā "aho Blashko" - he aha te e aho? Taua raruraru maha i kitea i roto i nga tamariki whanau hou, kaua e nui ake te 2% o e e aro ki te ahua o pathologies. Ko te tīmatanga kei roto mate mōhiohio te hanganga o DNA. whakatika tohu waho rite ki te hua o te tinana ine Endocrinology.
Blashko aho āhuatanga e toru ngā pūtau i roto i te tinana, ko te puna o te mate:
- keratinocytes Epidermal - māuiuitanga riro maha kitea rite ki te hua o te chimerism.
- Ngarahu - kei roto i te papa o raro o te kiriwaho.
- Profiling rohe pūtau ngarahu - arata'i ki te huringa i roto i te tae kiri, haere i roto i te membrane basement ki te kahu o runga o te kiri. kitea ana tēnei āhua i te natura tumu o te hanganga o te tonapuku.
tohu waho
Ko te tuhinga hauora whakarato mōhiohio e pā ana ki te rārangi Blashko: e ko te reira te mate o te kopa tangata, e faaite ake i roto i te take o rahunga i roto i te tinana mo te ora. Hanganga tauira e kitea i runga i te wahi hoki rite te tae o te kararehe: hepapa tiger ranei. Ka taea te kï hoki i te radiation hihi katinga.
Te tae kiri tangata o tei runga i te taonga o te melanin ngarahu. Kei te hanga e te reira i roto i te kopa kiriwaho, ngā paparanga basal melanocytes. Ine i roto i te tukanga o te melanogenesis arata'i ki te huringa tae ngā rangona:
- Hyperpigmentation - tauira huru o wahi pouri i runga i te kiri, kei te mārama kitea i te rakau whakamarumaru taketake.
- Hypopigmentation - mate o te tae o ngā pūtau kiri, hua wahi repa. kite māuiuitanga Rare kore neke atu i te 1% o tamariki whanau hou.
He whakakitenga waho o te tauira mate riro V-āhua, i roto i te puka o curls rārangi mawhatu ranei. E mea pinepine i hanga i runga i enei wahi o te tinana:
- hoki;
- i runga i te taha;
- pokohiwi;
- upoko.
Tātarihia te te raruraru
Raina tuhi Blashko kitea ina haere te tangata irradiated ki te marama hihi katinga, engari mo te ora o uaua taua whakamātautau. Hei ako timata kē te āhua o te tinana i roto i ngā wāhanga whakamua o te mate. I roto i nga tamariki whanau hou, ki nga wahi kanapa o te hypopigmentation i runga i te tinana uaua kite. Ka whiwhi te tamaiti i te huringa nui o te kiri i roto i te tau torutoru.
I runga i te āhua o te pūtau pāngia e te huinga o pūira. Ki te he te reira i te tino rerekē i roto i ngā wāhanga tata o te kiri, te ine kitea i roto i papanga tae. Na kia puta hypopigmentation te tikanga e whai ake nei:
- wahi huru - hiahia i roto i te pūtaiao hoki o nga hanganga pāhiwihiwi. E whakaatu ana te pikitia i te āhua matatini kitea i roto i te puka o here, ngā pūtau chess.
- Paetata - kitea kotahi wahi i roto i te tetahi rohe.
- Whānui - kia haere tahi e mate o whekau.
He aha e ti'a ia tatou ki te ako i te tuhinga i runga i te kiri?
Kua haere rata ki te tātari te kakano o te kopa i pōauautanga kitea i runga i te kiri. Here, te tohu matua ko te raina Blashko, whakawakia te mate te mo te tātaritanga tika. riro nui tenei ka whai raruraru Dermatological:
- chimerism;
- mosaicism;
- zoster;
- nevus;
- tonapuku.
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