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Tolosa-Hunt syndrome: tātaritanga me te maimoatanga
Ahakoa te taumata tiketike o te whanaketanga o te rongoā, e kore e etahi mate ako tae noa ki te mutunga. Ki tetahi o enei mate pā ana Tolosa-Hunt syndrome. I reira i reira he tohu anake o te mate, i te take e kore ano tino whakakitea. Te nuinga pea, he tika ki te meka e ko te tino onge te mate, me te he tuwhera kore pera i mua tenei. I tua atu, i te syndrome Tolosa-Hunt maha "masked" i te tahi atu pathologies, a he mea ohie ki te whakapoauau. Ko te tohu matua ko te mate kanohi me raru cranial. Kei te mohiotia te reira e whakaaro tetahi o nga āhuatanga o tenei mate ko ki hei te meka e ohaoha reira iho ki taiki therapy, i muri nei hohoro mai whakapai ake. Heoi, ka taea e matahoki puta i tetahi wa.
Whakamārama syndrome Tolosa-Hunt
Kua puta te whakahua tuatahi o tenei mate ngā tata. I whakaahuatia te reira i roto i 1961 i te ophthalmologist Hunt Ingarangi. I tua atu ki te taitara matua, a ka huaina māuiuitanga kehe pērā i "kamiriona". Ko e tika ana ki te meka i ona tohu rite maha atu mate tenei. I roto ia ratou: pukupuku o te matenga, encephalitis hopuhopu, myositis āmionga, me te ara mate o te pūnaha hematopoietic. I tua atu, i te māuiuitanga o Tolosa-Hunt ka karanga te tohu o te moko o orbital pai e kore e e tika whakaata i te mauri o te raruraru. Ko te pikitia haumanu o te mate tei runga i te aha te huru o ka raru ko roro i pāngia. Nuinga o ngā wā, āhuatanga Tolosa-Hunt syndrome e mamae i roto i te turanga kanohi, ki te ngoikore te neke i te kanohi, diplopia. A, no te tīmata wā kia whakaora taiaki therapy murunga toitü ranei.
Ko te aetiology o te syndrome Tolosa-Hunt
Nā ki te meka e kua te māuiuitanga faaiteraa rerekē, me te tīmata ohorere, e kore te mea te reira ano e taea ki te whakatau i te etiology tangohia. Kei te whai pānga hoki te reira ki te takanga iti o te syndrome. Hoki tenei take, tākuta i kahore ara ki te titiro tika te mate. He maha ngā whakapae, rite ki nei ka taea e te whakawhanake i te māuiuitanga. Tohatoha E wātea ana nga āhuatanga etiological e whai ake nei i roto i te tūroro ki te Tolosa-Hunt syndrome:
- Malformation. fakahu'unga tenei wā te whanaketanga rerekē o te pūnaha iaia o te kanohi. Ka rite ki te hua malformations e whakauru toto venous me matua, e kore e waiho noa. Ko atu noa i roto i nga wahine tenei ofatiraa.
- fakaaoao Autoimmune. Tenei take ko te keu o maha mate. Heoi, ki te whakahoki i te pātai o te aha timata nga pūtau ārai mate ki te whakangaro i te kopa o te tinana, a kore e taea e. I roto i te nuinga o te wā, "fakaaoao" puta i muri i te mamae ahotea, me te roanga o te tukanga hopuhopu nāianei.
- te pukupuku roro rerekē me raru cranial. E nehenehe te reira rite pukupuku mārire me te mate pukupuku.
Syndrome Development Tikanga
Homai te meka e noho tonu i te etiology o te mate unknown, pathogenesis, rawa, e taea e kore te tino tirotiro. Ahakoa o nga take mo te whakawhanake māuiuitanga pā anake etahi hanganga o te kanohi, me te kiko io. Ka rite ki mohiotia te, te ingoa tuarua o mate - he syndrome teitei moko o orbital. e pā ana tenei i te te pathogenesis, mai te hinga o raru kitea me oko toto e haere na roto i te reira. Tuatahi o te katoa i reira he huringa i te rua ophthalmic me uaua. Ka rite ki te hua o te trophism kikokiko fakahohaasi. I tua atu, pakaru reira pakohu cavernous, i te mea tata ki te moko orbital pai. Iatuku tuku reira, hei matia me te hypertrophy kiko. Ka rite ki matau koutou, i roto i te āputa i roto i te cranial e whai ake raru ko: te poraka, tango atu he wahi o te trigeminal me oculomotor. I roto i ētahi wā, te pānga enei takirua katoa. I te wa ano mamae reira i te kaha ki te huri i te 'Afio. I te tahi taime waimaero mahi o tetahi e rua ranei o raru takirua.
Tolosa-Hunt syndrome: tohumate
maha hanga māuiuitanga ite iho i roto i te tau waenganui, me te koroheke. kia pängia ana ki e rua wahine me te tangata tenei syndrome. whakawhanake ohorere te pikitia haumanu o te mate, kahore tetahi preconditions. Wehewehe i te tohu e whai ake nei:
- Mamae i roto i te mara ophthalmic. Hūhi tuatahi puta i roto i te rae, rae, upoko. I muri roa'tu, te kaha o te mamae, atu i te reira ki te kanohi.
- Diplopia. Tenei tohu puta i muri i te whakawhanake mamae. Te āhua i te manawanui ki te hei e nga taonga katoa ki te titiro parawai, e te reira. Te arotahi pakeke titiro.
- Tūkinotanga o te nekeneke o te 'Afio - ophthalmoplegia. E mea pinepine kitea ki tetahi ringa. Tei Ko tōna whānuitanga runga i te kaha me te maha o te raru pāngia.
- Huamo o te kirikamo.
- Exophthalmos. Kitea i roto i te ngaro o te maimoatanga me relapses auau.
- Strabismus. Puta reira ka e patua nga raru i tetahi taha anake.
- kirika iti-māka me te ino.
Ēnei tohumate te tikanga tupu āta, ka whai tahi i te tahi. I roto i ētahi wā e kitea e ratou wā. kia ohorere ngaro Tohu o te mate, tika pera me tona putanga ratou. Heoi, kahore maimoatanga o te māuiuitanga hanga tonu ua ano ano. Ko te auau hohokitanga i te katoa rerekē rite murunga roanga.
Tolosa-Hunt syndrome: māuiuitanga tātaritanga
Ki te tautuhi i tenei māuiuitanga uaua, rite he rite ki te maha atu mate ona tohu. Na reira whakaaro Tolosa-Hunt syndrome te he tātaritanga o te whakarerenga. Ko te manawanui tuatahi ui e pā ana ki te āhuatanga o te mate haereraa (ki te timata, rite nga tohu whakawhanake). I muri i taua, i nga whakamātautau taiwhanga me tātaritanga mauhaa. He mea tino nui ki te pupuri whakamātautau ophthalmic me neurological. Hei aukati pukupuku roro, whakamana MRI te. He mea nui hoki ki te whakahaere ultrasound me X-hihi whakamātautau o nga turanga kanohi. Ko te aroaro o malformations iaia whakaritea e te angiography. I tua atu, tetahi o nga paearu tātaritanga ko te whai huatanga o te ira therapy. Ki te te taiwhanga me whakamātautau mauhaa whakakitea hohoro mutu i muri i maimoatanga kahore huringa korerotia, me tohu, he pea reira, te tātaritanga - Tolosa-Hunt syndrome. whakamahia Prednisolone te ki te hamani i te tino.
tātaritanga pārōnaki ki ētahi atu mate
Ko te mate whakaritea ki ētahi atu pathologies o te kanohi, me te pūnaha io. Ko te mahi tuatahi, ko te ki te aukati i ngā tukanga inflammatory o te roro, me ona meninges, me pukupuku. Ki te whakapae koe meningitis encephalitis ranei, whakamana i te poka lumbar te. I roto i te tikanga ki te ārai pukupuku Koló me tūroro mate pukupuku kiri MRI, scans CT roro me X-hihi o te angaanga. Ko te mate, ko te lymphoma rerekëtanga, cysts o te pakohu cavernous me Thrombosis. Ka rite ki kia puta enei tohu ki pathologies pūnahanaha pērā i sarcoidosis, myositis ohuraa, migraine, etc. I roto i te tikanga ki te hanga i te tātaritanga tika, kia kite i te manawanui mātanga rerekē: .. He ophthalmologist, toketā neave, taote iaia, he tafe'anga.
Maimoatanga o Tolosa-Hunt syndrome
Maimoatanga o Tolosa-Hunt syndrome ko te whakarite o te raau taero e pehi i te pūnaha ārai mate. Hoki tenei whakaaro, nga taero taiaki-kei roto: "Prednisolone", "Hydrocortisone". Enei taero i te pānga i roto i te tahi atu pathologies autoimmune, engari ngaro nga tohu mate i roto i 3-4 ra. syndrome, Tolosa-Hunt maimoatanga ki prednisolone ko i te tātaitanga o te 1-2 mg / taimaha tinana kg. Ki te whakamahia te raau taero i roto i te puka o te otinga, kua whakaritea ai i 500 ki te 1000 mg ia ra. I tua atu, i te whakamahi painkillers me huaora.
Te āhei ki te mahi ki te syndrome Tolosa-Hunt
Ko te tikanga, ka monokia tenei tātaritanga tūroro ora. Me waiho koe tino e te manawanui ko Tolosa-Hunt syndrome. Hauātanga i roto i tenei māuiuitanga he onge. Heoi, ka kia tautapa relapses auau 3 rōpū. kia te manawanui kia whakawhiti ki te mahi marama e kore e rapua e kaha ataata. Ano, ka kore e taea te manawanui mate io tamau peia taraka i te ofatiraa o te kaupapa kanohi me te diplopia.
Syndrome Prevention Tolosa-Hunt
I roto i te mua ki te matapae i te whanaketanga o Tolosa-Hunt syndrome kore e taea, na reira, te ārai tuatahi e kore e tīari. Ki te mea i reira he tohu pērā i te mamae i roto i te kanohi, me te rae, diplopia, kia whakahaere koe i te tātaritanga tino. A, no te Tolosa-Hunt syndrome tika ki te kawe i roto i te ārai tuarua. Kei roto i tēnei therapy taiki wā, tautoko wātea i te mate. Me hoki koe ki te karo i āhuatanga taumaha me ngā tukanga inflammatory.
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