Hauora, Diseases me ngā Here
Thrombophilia - he aha te mea te reira? Thrombophilia: Take, tohu, Te tātaritanga me te rongoā
Ko te āhua o te susceptibility o te tinana ki te Thrombosis iaia, e taea auau me te whai i te tauwāhi rerekē, ka karanga thrombophilia. Ka taea e te mate kia rānei ira riro ranei. Kei te tino maha te take o te mate nui haere upoo- toto. Hauora, kia whakaatu i te mate i te momo o te Thrombosis i roto i ngā wāhi rerekē. Ko tino whānui i roto i te taupori Thrombophilia me puta i roto i ngā puka rerekē. titau te mate maimoatanga ki rongoā tikanga hāparapara ranei.
Thrombophilia: he aha te mea te reira?
E pā ana māuiuitanga ki mate o te pūnaha toto, whakakitea i roto i te hehema ki Thrombosis me hemostatic disorders. Maha Thrombosis recurrent i roto i thrombophilia kia te hua o te whētuki, pokanga, ahotea tinana, i roto i te hapū ranei. He mōrearea Herenga no taea arahi reira ki pōauautanga pērā i Embolism pūkahukahu, patu, infarction myocardial, Thrombosis rua hohonu. E mea pinepine e mate puka matatau.
Rangahau, tātaritanga, me te maimoatanga o thrombophilia whai wāhi i roto i te maha o ngā wāhanga o te rongoā. Akoranga Hematology nga āhuatanga o disorders toto, phlebology - tātaritanga me te maimoatanga o te Thrombosis o nga uaua, te tango i clots toto wāhi tākuta iaia. thrombus hanganga hua i roto i te rangirua o te rere toto noa, haere tahi nei i te whanaketanga o ngā āhuatanga mōrearea e te hunga uaua ki te hamani. I roto i te wā ki te ārai i te raruraru, wā me i whakamatauria koe mo te upoo- toto. Ko te täkupu e hoki wahine, mo te tauira, toto venous he 5-10 meneti.
take o
Āhuatanga e meinga te whanaketanga o mate, torutoru. Tata i taea e te katoa fehangahangai he mate pēnei i thrombophilia. He aha te mea te reira huru kino, he maha tūroro ētahi wā e kore e ara mohio me te ani i te tauturu, kaua te mutunga. He he he rārangi o ngā take e taea whai wāhi ki te whanaketanga o te māuiuitanga.
puta tuku (ira ranei) thrombophilia rite ki te hua o te predisposition ira ki te mate. kia hoki heke mua mate toto (thrombocytosis, erythremia, syndrome antiphospholipid) hei te take mo tona whanaketanga. ngā āhuatanga mōrearea atherosclerosis, mate pukupuku, fibrillation Atrial, uaua tīponapona, me mate autoimmune. Ko te tūponotanga o te takanga o piki thrombophilia i muri i te patunga i ngakau ranei whakaeke. I roto i te rohe mōrearea, tūroro e e mōmoma, ārahi i te āhua sedentary, tango te whakawhānau hormonal, e kore e kai i roto i te mua i tukua e te whara nui tafa ranei. I te tau wawe he onge te mate, i te reira maha puta i roto i te iwi pakeke. Kia kore ai te mate ranei, e kore e huru tīmata, e tūtohu ana i te wa ki te wa ki te haere whakamātau mō thrombophilia.
pikitia haumanu
faaiteraa haumanu o mate āhuatanga e ara maeneene me te roanga o te nāianei, na kihai i kite tonu tūroro te huringa i roto i te āhua o te hauora, a kahore e hanga i tetahi amuamu. Ka taea e ngā tawhā Laboratory tātari thrombophilia, he pikitia haumanu taipitopito i roto i ētahi wā, puta reira he torutoru noa nga tau i muri mai. kia puta tohumate Bright ina kua hanga e te katinga. Ko te tohu o te arai o te lumen oko, me te localization o thrombus pā te pakeke o ngā tohu.
Thrombosis matua, meinga nei e clots toto i roto i te lumen iaia o te moenga ia toto, tahi e te hanganga o te thrombus i te lumen o nga oko o te ewe, te mate intrauterine fetal, whakatahe maha, patua o iti hoki coronary whakapeka, patunga rere pūroto.
Thrombosis venous o pito o raro faaite mai tohu haumanu ratou i roto i te puka o huringa arataukai o te kiri, tetere nui o nga topito o raro, te ahua o te mamae, mana'o o pouri i roto i te topito o raro.
Mezentealny Thrombosis intestinal puta ka te katinga toto i roto i te localization o nga oko mesenteric me haere tahi e taua tohu kumete, ruaki, whakapairuaki, mamae maripi-koi rite wewete.
A, no te ate rua Thrombosis whakawhanakehia hydrothorax (Budd-Chiari syndrome), ascites, edema o te taiepa he mārōrō, puku me pito o raro, ruaki whakarihariha me te mamae kino i roto i te rohe epigastric.
hematogenous thrombophilia
pā Thromboses te āhua o te taiepa iaia, hoko i te reira, me te whakaiti i te ātete, te āwhina pōturi iho te rere toto me te whanaketanga o ētahi atu disorders hemodynamic e kua pā ana ki te huringa i roto i te pokey me te upoo-. kāwanatanga Thrombophilic i roto i te maha ngā take e pā ana ki te aroaro o mate iaia pērā i atherosclerosis, te whara intimal iaia, vasculitis toxigenic, ārai ranei takenga hopuhopu. kia tika ki ngā rerekētanga i roto i te āhuatanga o te toto iho, e homai te tika ki te korero e pā ana ki te mate, ko Maha thromboembolism recurrent "thrombophilia hematogenous." pathologies e pā ana ki te whanaketanga o te haafifi i o te tinana ki te whakawhanake i Thrombosis, meinga e abnormalities i coagulation, waimaero pūmanawa toto hemostatic.
Thrombophilia hematogenous i roto i te take mai taea e congenital riro ranei. I runga i te huarahi matua o te huna hoki mate e kua meinga e: huri thrombogenic conjugated, pōrearea mōtepe, fibrinolysis waimaero, inhibition, coagulation ngoikoretanga nui anticoagulant whaiaroaro rerekē hapa ranei. I tua atu, taratahi tetahi whakawhanake rite ki te hua o ngā pānga tarukino ranei wawaotanga hauora thrombophilia iatrogenic.
thrombophilia tuku
Tautuhi Thrombosis congenital tuku ranei e taea e te pūtake o te mau faaiteraa haumanu e whai ake nei: Thrombosis i te wawe tau, take Thrombosis o iatuku pūkahukahu, mesenteric, wahi o raro ko te aamu utuafare, te wāhanga tuatahi o te Thrombosis venous recurrent i mua i te 30 tau o te tau, Thrombosis i roto i hapū wawe, pōauautanga thrombotic. whakaritea thrombophilia tuku ira ranei te i muri i te tātaritanga whānui o tūroro e whai i te mōrea o pōauautanga thrombophilic.
kia whai ahua congenital o te mate i te āhua rerekē. I roto i te tātaritanga o te mate tango ki pūkete tohu ira mō te thrombophilia. Ko te take tuatahi e whai wāhi ki te whanaketanga o te mate - he predisposition ira. I roto i tenei take, e kore ai te mate puta i roto i te ngaro o ngā āhuatanga e tīmata nga tikanga o tona whanaketanga. Ko te tuarua - te irakētanga o ira i roto i te whanaketanga embryonic. Mārika i nui haere hou āhuatanga kukū e maka atu i te irakētanga ira. I roto ia ratou, te hunga e kua ahu mai i ngā mahi a te tangata: pira radiation, te whakamahi o tāpiritanga kai, pharmaceuticals, parahanga taiao (matū whare, kora, patukīrea) ati hangaia. e taea ki te matapae i te tikanga i raro i e taea e modifiable te ira reira, na i whakaaro mutagenesis ki te waiho i te tukanga tupurangi, i puta i tahaki, a kua te kaha ki te huri i te āhuatanga tuku.
kia hoki kia thrombophilia tupu e tika ana ki hanganga ranei irakētanga genomic o pūira tuku iho i nga whakatupuranga o mua. He te whakaturia te āhua o te ira mate: ngoikore tino ranei. I roto i te take tuarua, whakakitea te māuiuitanga ake i roto i ngā āhuatanga katoa.
thrombophilia whiwhi
Ehara i anake riro engari kia whai hoki takenga riro te mate. Ka taea e te manawanui tātari syndrome antiphospholipid (ApS). I reira na roto i nuinga o te wā faaite riro ano thrombophilia. He aha te mea te reira, he aha e nga tikanga o tona whanaketanga, me pehea ki te whawhai i te reira?
syndrome Antiphospholipid Ko te matatini tohumate e fakatahai raraunga taiwhanga me tohu haumanu. Ko te mate tahi e disorders neurological, thrombocytopenia ārai, syndrome mate fetal, venous me te matua Thrombosis. Tohatoha puka o ApS: tuatahi, tuarua me te catastrophic; kōwhiringa serological: seronegative me seropositive. whakatika Syndrome ki neoplastic, hopuhopu, autoimmune mate pāwera ranei rite ki te hua o te ātete tarukino ranei.
kia Development ApS kia pā ana ki taua tikanga rerekē pērā i neoplasm mārere (mate pukupuku, mate lymphoproliferative, kanisā), mate (mycoplasmosis, HIV, pakewakewa), tohanga asymptomatic afa, ma'i täkihi, mate o nga pera piringa me vaolo ngakau, mate ate, mate tūhonohono kikokiko, me mate autoimmune (mate o Crohn, vasculitis pūnahanaha, whakamate).
Thrombophilia i roto i te hapū
I roto i te hapū, maha faaite thrombophilia ira tuku ranei ano mo te wa tuatahi. Ko te matua e tika ana ki te haerenga mai o te tuatoru, te porowhita tohanga placental e kua runga i te pūnaha circulatory o te pikaunga atu tenei. whai wāhi hoki Hanganga o clots toto ki te maha o ngā āhuatanga o te porowhita placental. Ko te ewe he kahore tōiti, tomo te reira toto o te whaea i te pera, na e rerengia ana i roto i te Villi chorionic, rere ki te uho.
Hoki te tinana o te wahine e hapu āhuatanga e nui haere upoo- toto, i te whakaiti i mate toto i roto i te tuku ranei i roto i te hui o te pōauautanga pērā i abruption materoto, me te placental. whai wāhi te reira ki te kaha ake te tūpono o clots toto, me e te roto ratou takoto te ati. Ki te kei te paetata ratou i roto i oko toto e arahi ki te ewe, ngā matūkai, puta hypoxia rere mutu ki te kukune. Tei runga i te taumata o te tanumia o oko toto, me te maha o clots toto, kia aru e pōauautanga kino, whanau taimi halá, materoto, hapūtanga memenge, malformations ranei te mate fetal, iti hoki fetoplacental, abruption placental. puta ratou, te tikanga i muri i te 10 wiki. I roto i te wā mua o thrombophilia i roto i te hapū, ko te tino onge. Ki te whakawhanake i te mate i muri i te 30 wiki, ka mutu te reira i roto i te maha ngā take, abruption placental, iti hoki placental preeclampsia nui ranei. I te whakamātautau kia utu i te tākuta whakarongo ki upoo- toto, he paku rerekē i te paerewa te auau o te wahine "i roto i te" e.
tātaringa
Ko te mau faaiteraa haumanu o Thrombosis whakapumautia i roto i te whare hauora mā te taiwhanga (cytological, matüora, ira, coagulologic) me ngā tūāhua mauhaa. I roto i te ahua me te huru o te tinana e taea te tautuhi i whakapae Thrombosis venous (huamo). E rua venous me te matua tahi e tamau mamae akina me te bloating. I te tahi taime te pāmahana kiri (venous) faarahi i roto i te rohe o te localization. I roto i te matua wahi Thrombosis tata te thrombus kitea te heke i roto i te pāmahana, cyanosis (cyanosis), te mamae koi. Enei tohu - ko nga tohu tuatahi o te thrombophilia, i te mea he take nui ki te haere ki te tohunga enei.
Tika i te hōhipera whakahaere he ako tino o te manawanui. Kia tino ki te tango i te whakamātautau mō te thrombophilia, meatia ultrasound iaia (whakatau te āhua, te rahi me te wāhi o te katinga toto); ki te kawe i roto i rerekē arteriography me venography, e taea ana ki te localize me te tirotiro i te tinana o ngā tukanga thrombotic. Ano, whakamahi radiographic, tikanga radioisotopic, tātari ira o polymorphisms, whakatau i te kukū o te homocysteine.
maimoatanga
Ko te pātai o te upooti'araa i te mate puta i roto i te hunga e fehangahangai ki te tātaritanga o te thrombophilia. He aha te mea te reira, ka pehea ki te mahi ki a ratou i roto i te tikanga ki te karo nunua mamafa? kia whānui maimoatanga mate, me te whai wāhi i te whai wāhitanga o kaiwhakaako o ngā tino: pokanga iaia, phlebology hematologist. I te wā tuatahi, ko te mea e tika ana ki te ako i te tikanga etiopathogenic o te whanaketanga mate. Ka taea te tika hua takatika o te maimoatanga i muri anake i te whakakorenga o nga take pakiaka. He āhuatanga nui o te maimoatanga he kai, i te mea ki te whakakore kai ki cholesterol tiketike, te herenga o te fatty me ngā kai tunua. e tūtohu ana ki te ngā i roto i te kai o hua maroke, hua me huawhenua, otaota hou.
maimoatanga Drug Kei roto whakahaere antiplatelet, kīnaki nei i te whakamahi o te anticoagulation maimoatanga e totó ko, gemodelyutsiey. I roto i ētahi wā he mea e tika ana ki te kawe i te huhu o te wē tio hou ngā ki heparinization. therapy whakauru i whakaritea mo te puka tuku, i te mea e tika ana ki te hē o te antithrombin III.
thrombophilia Easy (whakamātautau toto e tauturu i te whakatau i te āhua), tukinotia ki wē lyophilized (rō-uaua) ranei takoha wē maroke. I roto i te puka kino whakamahia taero fibrinolytic e kua whakahaere i te oko kua pōkia te whakamahi i te pū tōngāmimi. A, no te me kia wehewehea te tātaritanga o te maimoatanga thrombophilia me matatini, te whakarite ora tere, me te tōtika.
ārai
I roto i te tikanga e kore e ki te e fehangahangai ki tenei mate nui ranei ona pōauautanga, āraihia ki te ārai i kia waiho reira ia wā. Tūroro ki thrombophilia pai kawea wē huhu i roto i pota iti me te tarukino subcutaneous "Heparin". Manawanui hoki prophylaxis kia whakahau rongoā e whakakaha te taiepa iaia ( "Trental" rō-uaua "papaverine" waha).
tūtohutia hoki te ārai me te maimoatanga o te thrombophilia te ki te whakamahi i rongoā iwi, pēnei i te tipu hei rongoā. Na, ki te whakaiti i te mahi mōtepe ka āwhina i tea karani karepe wai ranei. toto Rarefy mā te whakamahi i te tincture o Japanese Sophora purapura. I tua atu, he reira e minaminatia ki te hanga i te kai tika, ake haere i roto i te rangi hou, me te hoatu ake mau peu kino.
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