HauoraDiseases me ngā Here

Phospholipid syndrome: Take me Diagnosis

syndrome Phospholipid - he māuiuitanga āhua noa o te take mai autoimmune. Ki Kei te maha kitea te papamuri o te mate iaia, tākihi, wheua, me te tahi atu whēkau. I roto i te ngaro o te therapy raruraru e taea arahi ki pōauautanga kino mate o te manawanui noa. Ano, Kei te maha kitea te mate i roto i nga wahine i roto i te hapū, te tumatetenga i te hauora o te whaea me te tamaiti.

O te akoranga, e rapu maha iwi mō ngā mōhiohio atu, tono pātai e pā ana ki te take o te mate. He aha tohumate kia titiro ahau mo? He reira he tātaritanga syndrome phospholipid? Ka taea e rongoā whakarato tikanga whai hua o te maimoatanga?

syndrome Phospholipid: he aha te mea te reira?

Hoki te wā tuatahi kua te mate kua whakaahuatia tata. i whakaputaina kātipa mōhiohio e pā ana ki a ia i roto i te 1980. Mai te mahi i runga i te ako o te reo Ingarihi rheumatologist Grem Hyuz, kei te maha tuku te mate ki rite Hughes syndrome. He hoki ingoa atu - syndrome antiphospholipid, antiphospholipid syndrome antibody.

Syndrome Phospholipid - mate autoimmune i nei ka tīmata te pūnaha ārai mate whakaputa paturopi e patu i ake phospholipids o te tinana. Mai tenei taonga ngā i roto i te membrane o maha taiepa pūtau, me te lesion i raro i taua nui mate:

  • Ko te paturopi te patu i ngā pūtau endothelial hauora, te whakaiti i te āhuatanga tipu, me te kōtuitui anō o prostacyclin, i te mea te kawenga mō te roha o te taiepa oko. Ki te whakamārama o te mate i reira ko te takahi o te mōtepe whakahiato.
  • E kitea ana hoki phospholipids i te taiepa o te platelets ratou, e tika ana ki te nui haere te whakawhāititanga me te whakangaromanga tere.
  • I roto i te aroaro o paturopi he i kitea ai hua i roto i te upoo- toto me te ngoikore hoki o te mahi heparin.
  • Ko te tukanga o te whakangaromanga e kore te Karo me ngā pūtau io.

haamata te toto ki te katinga i te oko toto, hanga clots e whakapōrearea i rere te toto, a konei te mahi o ngā whēkau - na te whakawhanake i te syndrome phospholipid. Take me tohu o te mate o te moni ki te iwi maha. I muri i te katoa, te wawe kitea te mate te, ka whakawhanake iti nga pōauautanga i roto i te manawanui.

Ko te take matua o te mate

He aha e te iwi te whakawhanake syndrome phospholipid? kia rerekē te take. Kei te mohiotia te reira e tino maha te manawanui he predisposition ira. whakawhanake mate, ki te he arā o te pūnaha ārai mate, e hoki etahi take tīmata ki te whakaputa i paturopi ki o te tinana ngā pūtau ake. I roto i tetahi take, kia te mate te tahi mea nā. Ki te rā, i taea e ki te tāutu i te maha o ngā āhuatanga mōrearea pūtaiao:

  • maha whakawhanake syndrome Phospholipid i te aroaro o te microangiopathy, ngā trobotsitopenii, syndrome hemolytic-uremic.
  • āhuatanga Risk ngā atu mate autoimmune pērā i lupus erythematosus, vasculitis, Scleroderma.
  • maha whakawhanake ma'i i roto i te aroaro o te mate pukupuku i te manawanui.
  • āhuatanga Risk ngā mate hopuhopu. He fakatu'utāmaki ngā he mononucleosis hopuhopu me AIDS.
  • kia puta paturopi i hoki.
  • Kei te mohiotia te reira e kia whakawhanake i te mate i roto i te tūroro te whiwhi etahi rongoā, tae atu ki ngā whakawhānau hormonal, psychotropics, "novokainamid" me te t. D.

Noatia, he mea nui ki te kitea i roto i te aha kua whakawhanakehia te manawanui he syndrome phospholipid. kia tāutuhia te tātaritanga me te maimoatanga me te mea taea faaore i te take pakiaka o te mate.

Ko te hinganga o te pūnaha Cardiovascular ka syndrome phospholipid

Toto me te toto oko - enei tuatahi "ūnga" e pā te syndrome phospholipid. Tohu o reira tei runga i te atamira o te mate. clots toto te tikanga hanga i roto i te e alangá tuatahi o oko iti. whati i ratou i te awa toto, haere tahi nei i te kiko ischemia. Ko hauhautanga ki te pa tonu te alangá pā, tahuri ha ma te kiri, me te uaua āta atrophy. arata'i kiko pohokore roa ki necrosis me kikohangatia whai.

Chance, me te hohonu e alangá rua Thrombosis, haere tahi nei i huamo, mamae, nekeneke waimaero. Ka taea te faingataa te syndrome phospholipid i thrombophlebitis (mumura o te taiepa iaia), tahi e te i te kirika, Chills, whero kiri i roto i te lesion me koi, mamae koi.

te hanganga o clots toto i roto i te oko toto nui e taea arahi ki te whanaketanga o te pathologies e whai ake nei:

  • syndrome te pūtahi o (tahi e te hua koi i roto i te pēhanga i roto i te oko o te tinana o runga);
  • syndrome, iahoki vena cava teitei (mo te huru i homai āhuatanga e edema, cyanosis o te kiri, toto i te ihu, te pukorokoro me te pū kai);
  • syndrome o te iahoki vena cava iho (tahi e te ngangau o te tohanga toto i roto i te wahi o raro o te tinana, e alangá puku, mamae i roto i te waewae, papa, puku, me te tapatapa).

pānga Thrombosis te mahi o te ngakau. E mea pinepine tahi te mate e te whanaketanga o angina, takawhita tamau, infarction myocardial.

kino ki nga whatukuhu, me te tohu matua

arata'i Thrombus hanganga ki tohanga rawakore, e kore anake i roto i te wahi - ka mamae whekau, rawa nga whatukuhu. Ki te whanaketanga o te syndrome phospholipid wā roa-ko reira taea te infarction tākihi pera-ka karanga. haere tahi ana tēnei huru e mamae i roto i te hoki o raro, te whakaiti i te nui o mimi, me te aroaro o te toto i roto i reira o poke.

Ko te katinga kia ārai i te iatuku tākihi, haere tahi nei i mamae koi, whakapairuaki, me te ruaki. Ko te huru kino tenei - ki te mahue kore maimoatia, kia whakawhanake tukanga necrotic. nunu'a Dangerous syndrome phospholipid ngā microangiopathy tākihi i roto i nei e hanga e tika clots toto iti i roto i te glomeruli tākihi. E arata'i pinepine te he tu'unga taua ki te whanaketanga o te täkihi ma'i.

I te tahi taime i reira he tohanga rawakore i roto i te repe adrenal, e tika ana ki te rangirua o ngā taumata hormonal.

He aha ētahi atu whēkau kia pāngia ai?

syndrome Phospholipid - he mate e pānga maha whēkau. Ka rite ki whakahuatia, pā te paturopi kiriuhi pūtau neuronal, e kore e taea e te mahi i waho hopearaa. He maha tūroro amuamu o tamau pāhoahoa kaha e maha e haere tahi i te whanoke, whakapairuaki, me te ruaki. He he he pea o te whanaketanga o ngā disorders hinengaro.

Ētahi tūroro i clots i roto i nga oko toto e whakarato rere toto ki te analyzer whatu. kore auroa o te hāora, me ngā matūkai arata'i ki atrophy o te karere whatu. Thrombosis pea o oko tuaroa ki toto muri. Ētahi o pathologies ocular, kāore, tina heke: noho ataata waimaero ki te manawanui hoki te ora.

I roto i te tukanga pathological kia whai wāhi, me te wheua. maha pāngia iwi osteoporosis reversible, haere tahi nei i deformation o nga wheua me piere auau. More mōrearea Ko te necrosis iroiti o wheua.

Hoki te mate, me te e āhuatanga e pāpaka kiri. E mea pinepine te kiri o nga topito o runga me raro e hanga e uaua pūngāwerewere. I te tahi taime e kite koe i te hunga ponana rawa huru, e rite te iti, pakaruhanga toto anaana. Ētahi tūroro whakawhanake erythema i runga i nga kapu o nga waewae, me kapu. He he he hanganga auau subcutaneous kanokanototo (kahore take kitea), me te toto i raro i te pereti titi. ngangau roa o te kiko arataukai tura'ii te mate e roa ki te whakaora me te uaua ki te hamani.

kitea e matou e ko te syndrome phospholipid. Take me tohu o te mate - take tino. I muri i te katoa o enei āhuatanga ka whakawhirinaki i runga i te talena rata maimoatanga whiriwhiri.

syndrome Phospholipid: tātaritanga

O te akoranga, i roto i tenei take, ko te wa tino nui ki te kitea te aroaro o te mate. Parenga syndrome phospholipid, tō tākuta kia ara i roto i anamnesis. Pana i runga i tenei whakaaro, ki te Ko te ahei o te Thrombosis me venous tuwhenua, materoto auau, tohu o anemia te manawanui. O te akoranga, whakamātautau atu atu.

Analysis o te syndrome phospholipid ngā i roto i te whakatau i te taumata o paturopi ki phospholipids i te toto o te tūroro. I roto i te whānui, te tātaritanga o te toto e taea kite i te whakaiti i roto i te tatau mōtepe, nui haere auau parataiao ngeniwhero, nui haere te maha o leukocytes. E mea pinepine haere tahi te syndrome e anemia hemolytic, taea hoki e te kitea i roto i ngā akoranga taiwhanga.

I tua atu whakamana matū toto. Te manawanui he nui nui haere o globulins kama. Ki te pakaru te māuiuitanga papamuri i ate, faarahi i te nui o bilirubin i te toto, me te kawakore phosphatase. I roto i te aroaro o te mate tākihi taea te kitea hua i roto i te serum creatinine me te tiomimi.

Ētahi tūroro me tūtohu tauwhāiti whakamātautau toto immunological. Hei tauira, e taea te whakahaere rangahau taiwhanga ki te whakatau take rheumatoid me lupus coagulant. A, no te taea kitea toto syndrome phospholipid te aroaro o paturopi ki ngā pūtau toto whero, nui haere lymphocytes. Ki te kahore he māharahara o kino ki te ate, whatukuhu, wheua, i reira ka kia whakamātautau mauhaa, tae atu X-ray, ultrasound atahanga.

He aha e nga pōauautanga o te mate e pā ana te?

Ki te kore maimoatia, ka taea e te syndrome phospholipid arahi ki fifi tino mōrearea. Ki te whakamārama o te mate i roto i te oko toto i hanga clots, i roto iho he mōrearea e. clots toto kutia oko toto, ia mutu tohanga toto noa - kopa, me te kore e okana farii i ngā matūkai nui, me te hāora.

E mea pinepine ki te whakamārama o te mate, whakawhanake tūroro patunga, me infarction myocardial. Ka taea e alangá mo Embolism arahi ki kikohangatia. Ka rite ki whakahuatia i runga ake, kua kitea tūroro ki arā o nga whatukuhu, me repe adrenal. Ko te putanga tino mōrearea o te Embolism pūkahukahu - whakawhanake te ume nei i tenei māuiuitanga, a kahore i roto i te wā katoa, kore he manawanui ki te whakaora i runga i te wā ki te hōhipera.

Hapūtanga i roto i tūroro ki te syndrome phospholipid

Ka rite ki kua whakahuatia, pāngia te syndrome phospholipid te i roto i te hapūtanga. Kia pehea te kino te mate, me te aha ki te mahi i roto i te āhuatanga i taua?

Nā syndrome phospholipid i roto i oko i hanga clots e Toke nga pera e mau ana toto ki te ewe. e kore e kukune riro nui hāora me ngā matūkai, i roto i 95% o ngā take arata'i tenei ki te tahe. Ahakoa, ki te kore e haukotia te hapūtanga, i reira te mea he mōrearea o te abruption placental wawe me te whanaketanga mutunga o preeclampsia, i te mea tino kino hoki e rua whaea me te tamaiti.

Tümanako, kia kia whakamatautauria te wahine i te wā whakamahere. Otiia kei te maha pāngia syndrome phospholipid i roto i te hapūtanga. I roto i te wā, pērā i, he mea tino nui ki te kite i te aroaro o te mate, me te ki te tango i nga mehua e tika ana. Hoki te ārai o te whaea o te Thrombosis heke mai taea te whakaritea ki te anticoagulation i roto i pota iti. I tua atu, kia aroturuki auau wahine kia e taea te tīmata i te tākuta ki te kite abruption placental. Katoa marama torutoru, kua tukinotia whaea expectant ki te whakapakari i therapy, tango teuteu kei roto huaora, ngā kohuke me antioxidants. Ki te huarahi tika, maha mutu humarie hapūtanga.

He aha te mea te maimoatanga?

He aha te ki te kitea he tangata te syndrome phospholipid? Treatment i roto i tenei matatini take, a tei reira ki runga ki te aroaro i roto i te manawanui o etahi pōauautanga. Ka rite ki te whakamārama o te puka clots mate, kei te matua hāngai te therapy i thinning te toto. te tikanga whai wāhi te talena maimoatanga te whakamahi o te maha ngā rōpū o taero:

  • Tuatahi whakaritea anticoagulants o mahi autaki, me māngai antiplatelet ( "ahipirini", "fafati").
  • maha Therapy ngā whiriwhiri kore-steroidal taero anti-inflammatory o takenga, i ngā te "Nimesulide" ranei "Celecoxib".
  • Ki te whai pānga te mate e ki pūnahanaha erythematosus lupus me etahi atu mate autoimmune, kia whakahau i te tākuta maimoatanga pūtaiaki (hormonal taero anti-inflammatory). Me ki tenei kia whakamahia ai, taero immunosuppressive e pehi i te mahi o te pūnaha ārai mate, me te whakaiti i te hanga o paturopi mōrearea.
  • wahine hapu ētahi wā e pâmuhia whakahaere immunoglobulin.
  • Kei te wā tango tūroro whakatakataka kei roto huaora o B. rōpū
  • Hoki hauora whānui, te tiaki i kiriuhi pūtau me oko whakamahia taero, antioxidants, a hoki taka e roto i te matatini o ngā waikawa ngakongako hamanga ( "Omacor", "Mexicor").

Āwhina ki te huru o te manawanui pānga electrophoresis tukanga. A, no te haere mai te reira ki te syndrome phospholipid tuarua, he mea nui ki te whakahaere i te mate tuatahi. Hei tauira, kia riro tūroro ki vasculitis me lupus tika maimoatanga o enei pathologies. Ko reira ano hoki te wa nui ki te kitea ngā mate hopuhopu, me te kawe i te therapy tika tae noa ki te ora oti (ki te taea).

Ko te waitohunga mō ngā tūroro

Ki te pāngia syndrome phospholipid i roto i te wa, ka riro te manawanui te tiaki e tika ana, ko te tino pai te waitohunga. Hei te maka o te mate, ko te kāore e kore e taea, engari ki te rongoā e taea te whakahaere i tona whakahōhā me te maimoatanga taupā o te Thrombosis. āhuatanga mōrearea whakaaro i roto i nei e pā ana te mate i te thrombocytopenia me te pēhanga toto tiketike.

I roto i tetahi take, i raro i te mātakitaki o te rheumatologist kia i roto i te tūroro katoa ki te tātaritanga o "syndrome phospholipid." Na roto i te tātari toutou rite pehea maha e hiahia ana koe ki te haere whakamātautau i te tahi atu mau taote aha kia rongoā kia tangohia rite ki te aroturuki i te āhua o tona ake tinana - ka korero tenei katoa te rata haere.

Similar articles

 

 

 

 

Trending Now

 

 

 

 

Newest

Copyright © 2018 mi.birmiss.com. Theme powered by WordPress.