HauoraDiseases me ngā Here

Matimati tauta: Take me te rongoā

He aha e whanau etahi tamariki matimati tauta? He aha e tenei māuiuitanga, a ahakoa e taea kia whakakahoretia atu koe o reira? Pahonoraa ki enei me ētahi atu pātai e pā ana ki te ine whakahuatia rauemi ka ako koe i tenei tuhinga.

ngā mōhiohio whānui e pā ana te māuiuitanga

matimati tauta - he congenital raro whanaketanga alangá. āhuatanga tēnei ine e hononga wāhanga oti ranei o rua, neke atu rānei maihao. I roto i te mahi hauora, matimati tauta i te ingoa motuhake - syndactyly.

Ki tenei mate i roto i te tangata kia waiho he hononga o maihao rua haka, me te underdeveloped, me te tika whakawhanakehia. Ko te putanga o te syndactyly he hē mahi, me te Paku o te e alangá raro.

Ko te koati ki te ine kia tonu kia runanga he geneticist me te tākuta orthopedic. Hei whakaturia te momo o syndactyly, kia kawea i roto i X-ray o te waewae. whakamana maimoatanga o tenei koha e anake i te pokanga. I roto i tenei take, kei te wehea ka whakamahia kirihou me te koha katinga ka tino tika nga matimati e rua tauta.

ētahi tatauranga

ka karanga a Syndactyly whanaketanga rerekē o te maihao, i te mea he hua o te pakaru o te matau o te wehenga. Tikanga, puta tenei i roto i te wā embryonic.

matimati tauta o te tamaiti hou kitea ki te auautanga o te 1 ki te 3000. Me kï hoki, e pā ana ki te syndactyly ko te hawhe o kōhikohiko congenital katoa. kia māuiuitanga waewae peheé rānei te deflection motuhake, me ngā ki ētahi atu hē (hei tauira, maihao hypoplasia, polydactyly me polifalangiey, ectrodactyly, brachydactyly, brachioradialis synostosis, wāwāhi o brushes, ulnar ranei clubhand toropā, me te pera i runga i.).

Tata 60% o ngā tamariki e kua i te matimati tauta (koha whakaahua aroaro i roto i tenei tuhinga), e pā ana abnormalities congenital i roto i te pūnaha musculoskeletal (hei tauira, pseudarthrosis, clubfoot, tāutanga wahia rerekē, me ētahi atu).

take o te koha

He aha e tamariki te whakawhanake i tētahi tumuaki tuarua taua, rite matimati tauta? Ko te take o tenei ine e taea e rerekē. Tohunga whakapono e i roto i te 20% o te wā he tika ki ngā āhuatanga tuku tenei. I roto i te mau parau te tahi atu, te tetahi he katoa o te autosomal tauira tino o te tupu.

Ki te ngaro te aamu utuafare o te syndactyly, me riro te reira e puta maumaui o pārōnaki me te hanganga o nga wahi o raro o te kukune i roto i embryogenesis. Ko te tikanga tenei tupu ka reira ko te pānga o ngā āhuatanga kino.

whakawhanake te koha?

Aha tauta waewae maihao, me pehea ki te whakamārama i te taua whanaketanga alangá? puta ripa pēpi waewae poho i te wiki 5 o te whanaketanga intrauterine. Ko reira i tenei wā i roto i te kukune kia whakawhanake syndactyly whaiaroaro.

I roto i te ngaro o te koha kē i roto i te wiki 7 o nga maihao e hanga e. Ko te tika tenei ki te tupu o hihi maihao, me te pōturi te whanaketanga o ngā wāhi interdigital. Ki te pakaru te whakaiti o nga taiepa interdigital, ka kore e wehea te phalanx, e ko, i reira he syndactyly.

Pea take whanaketanga rerekē

matimati tauta, ka taea e te tamaiti puta i roto i ngā pānga paitini i runga i te tinana o te wahine hapu. I roto i te nuinga o te wā puta tenei i roto i tango rongoā, inu i te kava, me te rauropi kino, ngā tikanga, X-ray irradiation me mate hopuhopu (hei tauira, rewharewha, pakewakewa, kohi, me ētahi atu).

E mea pinepine noho nga take o te whanau o te tamaiti ki te syndactyly mārama.

matimati tauta - Kei te maha i te reira kitea koha i roto i te hanganga o te pūira me syndromes ira.

E te ara, kei te tino uaua kitea i roto i te tangata whiwhi syndactyly. Tikanga, whakatika te māuiuitanga taua i muri i ngiha waewae (waiariki matū ranei).

Tauta matimati - e te tikanga tenei māuiuitanga?

He tokomaha te iwi e kaha pai ngaro, kua whakapono reira e kore tenei māuiuitanga whakawhanake tika. Kei te whakapono te reira e tenei momo o te irakētanga he tama'îraa. Ko e mo'oni, ko tino haamana'oraa o te matimati maihao tauta.

Heoi, tākuta mea e kore tetahi mea ke, me te whakamataku i roto i taua ko te waewae whanaketanga. Ko te tika te alangá Pākatokato, i te mea rawa ngāwari ki te pehea e o, rawa i roto i nga tīmatanga o te ora o te tamaiti tenei.

Heoi e kore e manukanuka kia nui ki te he koe matimati tauta. He aha e taua toharite, ka taea e koe te mea i te tākuta anake, e kore te hunga i aroha tama'îraa tapanga.

whakarōpū o mea kohakore

I roto i te orthopedics mākahia syndactyly rite ki te roa, te momo o te tui, me te te āhua o te maihao.

kitea tēnei wā:

  • āhua wheua (ka puta wheua titi);
  • puka kiko ngohengohe (ētahi wā membranous me te kiri).

Tei roa koha whakarōpū i runga i te maha me te roa o phalanges tauta tui.

No nia i te āhua o maihao tauta, ka taea e te syndactyly e matatini, me te ohie. I roto i te take whakamutunga i reira ko te hononga o te maihao noa, a i roto i te tuatahi - ki abnormalities o wheua, tahi, iohere nape taputapu ranei.

momo ira

Syndactyly whakarōpūtia a ira momo:

  • Ko te momo tuatahi - zigodaktiliya. hononga Motunga oti ranei (membranous) 2 me te koromatua 3. Hoki e kore kingi i roto i te tahi atu maihao huirapa.
  • Ko te momo tuarua - sinpolidaktiliya. Hononga o nga matimati 4, me te 5 ki te tuaruatia ai o te 5. Hoki tenei māuiuitanga āhuatanga e: he takahi o kapu hiako reliefs me hypoplasia o te phalanx waenganui.
  • Ko te momo tuatoru. syndactyly oti më o te 4 me te maihao 5. I roto i tenei take, e kore e pāngia i te waewae.
  • Ko te tuawha momo - Strip syndactyly. Tonu më ringa syndactyly waihakihaki. I te wa ano i reira he kore mate mutu.
  • tuarima i te momo. Hanumi metatarsal me wheua metacarpal. I runga i te ringa, ko te ake noa 3-4 hononga o maihao, me nga waewae - 2 me 3.

tohu koha

A, no te te tino maha kitea syndactyly o te waewae i roto i te tamaiti hononga o nga matimati 2, me te 3. I te phalanx rorona taua taea e rānei underdeveloped whakawhanakehia tikanga ranei. I roto i ētahi wā, i reira he he hekenga i roto i te maha o maihao, no te mea o ratou tapuhia waimatū.

Rerekē tamariki ki syndactyly i nga ringa o tamariki ki syndactyly o nga waewae whakawhanake tino tikanga. E ratou kahore raruraru ki te whakatinanatanga o te whānui o ngā mahi whānui. I roto i tenei hē mahi o te waewae e kore e koretake i ratou akoranga, me te tata kore tauwhāiti te kōwhiringa o te tikanga a muri.

Me pēhea te ki te tātari?

Me pēhea te ki te tātari matimati tauta (he tohu i kua taua koha kua whakaahuatia tika i runga)? kitea Syndactyly neonatologist i muri tonu whanau o te tamaiti. kawea kitea atu o te tamaiti te orthopedics pediatric tafa ranei. Hei tutakina pūira me te taea te hono abnormalities ira me te geneticist.

Ahakoa te meka i hanga he tātaritanga taua te i muri i te tirohanga ataata ki te whakamārama i te momo o te koha, me te te whanaketanga o te rautaki maimoatanga, he mea e tika ana ki te whakahaere i te taputapu ako.

Radiography waewae i roto i te rua haurangi taea tohunga ki te whakatau tata i te kiato o te wheua, hauora tahi, te roa me te aroaro o te wheua hononga. Ki te tautuhi i te āhuatanga o te rere toto me te whatunga iaia i roto i te maihao mahi UZDG, reovasography, angiography me te ine hiko.

maimoatanga mate

He reira he rongoa matimati tauta? Mahi ki te wehe i te phalanges - ko te otinga taea anake tenei. Heoi, kia tuhia te reira e whakamahia te tukanga hāparapara te anake, no te syndactyly o te maihao. No nia i phalanges tauta mutu, ka kore e whakaaturia te mahi. Ki te poka taua pīari ki haere noa, kei te tonu kawea te wawaotanga i roto i.

A, no te te haere i te mahi i runga i?

Ngā me tikanga o te wawaotanga hāparapara kua oti te whakarite i runga i te āhua me te āhua o te koha. Ko te whakaaro o tenei maimoatanga ko ki te whakakore i te koha Paku, me te whakapai ake i te mahi o te waewae ringa ranei.

Ko te wa tino arotau mō te mahi - te tau o 4-5 tau. Ki te kitea he tamaiti hou mutunga syndactyly, kawea te wawaotanga i roto i roto i te hawhe tuarua o tona ora. ārai ana tēnei deformation o maihao tuarua, me te tupu pāhiwihiwi o te phalanges.

huarahi hāparapara

I roto i ngā mahi hāparapara kia whakamahia ai te huarahi e whai ake nei:

  • wehenga o maihao conjoined ki plasty kiri ki te kopa rohe;
  • kirihou skinless wehenga tui membranous;
  • tauta maihao wehenga, kīnaki nei i te whakamahi ngā o te kiri meangia ki autografts free me te kopa rohe;
  • wehenga o maihao conjoined, kīnaki nei i te kiri noa ratou tuara polnosloynym uhi kiri wahia ranei;
  • pokanoa multistage ki iohere-uaua, te kiri me te wheua täpiritanga.

Ko te wā postoperative

I muri pokanga ki immobilize te maihao wehea i runga i te alangá tangohia te kiri te raima te tango. E tūtohutia ana ki te kakahu i te iti rawa 3-4 marama.

Tata tīmata 15 ra i muri i te mahi ki te whakaora o te manawanui. Ki te mahi i tenei, te whakamahi i te ringa mirimiri waewae ranei, mahi therapy, phonophoresis ki Lydasum, whakaongaonga hiko o uaua o maihao, ozokerite, parawini me te paru wraps.

Ko te hua o te mahi

Methods whakamahia i roto i te maimoatanga pokanga hou o te syndactyly hoatu Paku pai me ngā hua mahi. Ki te te tino faaho'ihia mai wawaotanga wā te hanganga noa e kore e anake, engari ano hoki te mahi paraihe o te waewae.

Pokanga ki te tango syndactyly i angitu ki te te manawanui kahore tohu tightening me hira lateral o nga maihao, me i reira ko te ki tonu i ngā o te motini i roto i te interphalangeal tahi (adduction, kāhakitanga, toronga me te flexion), pupuri i te mahi (i roto i te take o te paraihe), te tūtohutanga pai me te puka tūturu nga mokowā i waenganui i nga matimati.

Ki te whakaritea e te maimoatanga o te syndactyly kore ki te kawe i roto i, i taea whai reira he pānga tōraro i runga i te whanaketanga me te tupu o nga wahi tamaiti.

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