HauoraDiseases me ngā Here

Mate Myeloproliferative: take, tohu, tātaritanga

take Myeloproliferative mate, tohu, te tātaritanga o nei e kia kōrero i muri, kėia he rōpū o āhua, ki nei te hinu wheua wheua, i reira te nui haere te hanga o thrombocytes, erythrocytes leukocytes ranei. I roto i te katoa i reira e ono ngā momo o pathologies.

Overview

Wheua wheua tikanga mahi whakatupuranga kakau (teeki) pūtau. I muri i te wa pakari ratou, riro tonu. pea te pūtau kakau he tīmatanga mo te hanganga o e rua momo o ngā tūemi: he tokomaha o te lymphoid me myeloid ngā pūtau. pūtau teeki Ko nga pikitia mo te hanganga o leukocytes. I roto i te āhuatanga o te raupapa myeloid e hua:

  • Erythrocytes. kawe ratou hāora me ētahi atu ngā matūkai hononga ki whēkau me te kopa.
  • Leukocytes. He kawenga mō te pato'iraa, me ētahi atu pathologies hopuhopu ēnei āhuatanga.
  • Platelets. Ēnei pūtau ta◊ofi hono toto, puka clots.

Me mua ki te hurihanga ki ngā pūtau toto whero, ma pūtau toto platelets ranei, aukati pūtau ki te haere i roto i te maha o ngā wāhanga. Ki te reira, mate myeloproliferative, he nui nui o te rauemi tīmata i hanga e tetahi atu ranei momo o ngā pūtau i hanga. Tikanga kauneke āta nui māuiuitanga ki te whakanui ake huānga toto taikaha.

whakarōpū

Momo e kia whai mate myeloproliferative tei runga i te nui o erythrocytes, platelets leukocytes ranei. I roto i ētahi wā, te tinana he taikaha tohua o ngā āhuatanga o neke atu i te kotahi momo. Kei te wehea māuiuitanga ki:

  • Ma'i kanisā neutrophilic.
  • Polycythemia.
  • Ma'i kanisā myelogenous.
  • thrombocytopenia faufaa.
  • Idiopathic (tonu) myelofibrosis.
  • kanisā Eosinophilic.

atamira pathological

Ka taea te puta ke te mate myeloproliferative ma'i ki kanisā whakapeka. āhuatanga tēnei huru e te taikaha o ngā pūtau ma toto. Ma'i mate myeloproliferative e kore kaupapa atamira motuhake. mehua haumanu whakawhirinaki i runga i te momo o te māuiuitanga. Ki te whakaaro ki nga ara, ka taea e te mate myeloproliferative puta i roto i tetahi o ara e toru:

  • Germination i roto i te tahi atu te kopa. I roto i tenei take, horahia te mate pukupuku ki te wāhanga hauora e karapoti ana, patu ratou.
  • ara Lymphogenous. Ka taea e te mate Myeloproliferative tomo ki te pūnaha lymphatic me tohaina ona kuhunga i te tahi atu te kopa, i nga okana.
  • ara Hematogenous. Pūtau repara tomo ki te tōiti me uaua e whangai nga kopa me okana.

A, no te he horapa o ngā pūtau puku, pea hanga he hou (tuarua) pukupuku. huaina ana tēnei tukanga ko metastasis. Tuarua ki te pukupuku tuatahi, ko te momo taua o te mate pukupuku. Hei tauira, i reira ko te horapa o ngā pūtau leukemic i roto i te roro. kitea te reira i huānga puku. kōrero ratou ki kanisā, e kore mate pukupuku roro.

tohu o te māuiuitanga

Nahea mate myeloproliferative? Tohu o te mate e whai ake nei:

  • mate taimaha, hārukiruki.
  • Ngenge.
  • hūhi puku me te tikanga o te tōpuni kai nohopuku. whakapataritari Last kōateate rahi (splentomegaliey).
  • Predisposition ki te toto, hono laiki, tohu o Thrombosis ranei.
  • te mahara waimaero.
  • mamae tahi, puku, whakapataritari rumati gouty.
  • Waea i roto i te taringa.
  • Tetahi raru i roto i te hautahi o runga maui o te pokohiwi puku, me te maui, i te mea he putanga o te mumura infarction ranei o te kōateate.

rangahau

kitea te whakararuraru, toto Myeloproliferative te i runga i te pūtake o ngā hua taiwhanga. Ko te rangahau ngā te mahi e whai ake nei:

  • Examination o te manawanui. I roto i tenei take, i te tohunga whakatau whakaatu te huru whānui tohu o māuiuitanga (huamo, mo te tauira), me te whakaaturanga, i reira ko kahore he tangata hauora. ui ano te tākuta e pā ana ki te āhua o te manawanui, māuiui me peu kino, whakahau.
  • Toronga KLA. kawea toto tauira i roto i ki te whakatau:

    - te maha o platelets me pūtau toto whero;
    - ōwehenga me te maha o leukocytes;
    - te taumata o te pūtoto;
    - nohoia te rōrahi o nei e pūtau toto whero.
  • Wawata me te wheua wheua unuhanga. I roto i te tukanga, kua whakaurua he ngira tuwhera matotoru ki te whaturei ranei iliac wheua. Tenei whawhe taea ki a koe te tango i te tauira wheua wheua, me te kikokiko me te toto. te uiui e te rauemi te i raro i te karu mo te aroaro o ngā pūtau rerekē i roto i reira.
  • tātari Cytogenetic. Tenei tukanga taea ki a koe kite huringa i roto i te pūira.

mate myeloproliferative ma'i: Treatment

Ki te rā, i reira e rave rahi whakaora mate. whiriwhiri Kotahi ranei te atu kōwhiringa kei runga i te huru o te manawanui me te mau faaiteraa e haere tahi mate myeloproliferative rānei. Ka taea te whakahaere i te maimoatanga paerewa - mahi kï, whakamātau ranei. Ko te kōwhiringa tuarua ko te ki ako i te whakamahi o ngā tikanga hou.

phlebotomy

Kei te tango i tēnei tukanga te toto i te rua. Kei te ka tono tangata te rauemi ki te tātaritanga matüora noa. I roto i ētahi wā, whakaritea phlebotomy ki tūroro e pāngia ki te mate myeloproliferative. Treatment i roto i tenei take whakahaua ki te whakaiti i te maha o erythrocytes.

apheresis mōtepe

Ko rite ki te tetahi o mua i tēnei tikanga. Ko te rerekētanga ko e reira te kawea i roto i te tango o te platelets anō te whakamahi i ngā taputapu motuhake. Ko te manawanui e te toto haere e te roto i te whakawehe. mau e ia platelets. "Tuku" toto hoki ki te manawanui.

huhu

Tenei tukanga Ko te huhu toto. I roto i tenei take i te whakauru o etahi atu āhuatanga. I roto i ngā, i te manawanui hei utu o ratou pūtau huna, ka pakaru whiwhi te huhu o ngā pūtau toto ma, pūtau toto whero me platelets.

hahau

Ko tā te tikanga te whakamahi o te raau taero cytotoxic. whakatika nei ia ratou mahi i te whakangaromanga o ngā pūtau puku tērā te tupu o te pukupuku ranei. Hoki-waha, rō-uaua intramuscular ranei tono o taero, tomo ratou kai kaha ki te tohanga nahanaha, te whakakore huānga pathological. huaina ana tēnei ko te hahau pūnahanaha. technique rohe ko te tikanga he whakataki ki te awa filosilivá, te okana tinana ranei kōhao tika pānga.

therapy radiation

kawea maimoatanga i roto i te whakamahi i te auau nui x-ray atu radiation ranei. Radiation therapy taea te whakatutuki i te whakakorenga tino o ngā pūtau puku, me te pōturi te tipu o te pukupuku. I roto i te mahi, he rua momo o te maimoatanga. therapy radiation waho ko te puaretanga o te kōwae, kei muri ki te manawanui. A, no te kawea he tukanga whakakī ā-i roto i te matū iratuki ngira, catheters, korere, e e ka patia tika ki te puku ranei ki te kopa kei a tawhio reira. E ka te tono tikanga mātanga, i runga i te tohu o repara o te tukanga rānei. Tūroro e pāngia ki te whakararuraru, toto myeloproliferative te irradiated, rite ki te tikanga, te wāhi kōateate.

Hahau ki transplantation o ngā pūtau

Tenei tikanga o te maimoatanga te tono o raau taero i roto i te pota tiketike, me te whakauru pānga mahi antitumor o ngā pūtau hou ko. huānga teeki e i te kaituku takoha te manawanui ranei me tio. I muri i te mutunga o hahau, kua whakaurua ki roto ki te rauemi tinana rongoa. tīmata Innovations pūtau ki te pakari me te whakaongaonga i te hanganga o ngā pūtau toto hou.

wā whakaora

I muri i te maimoatanga, kia kite i te manawanui koutou tākuta wā. Hei arotake i te hiahiatia ai te whai huatanga o te therapy ki te whakahaere i te raupapa o ngā tukanga e whakamahia ana i mua i te aroaro o te whakarite. I roto i runga ki te hua, whakatau i runga i tonu, otinga huringa o te maimoatanga talena ranei. kia korerotia ētahi rangahau i runga i te wā, tae noa i muri i te otinga o te akoranga haumanu. tukua ratou ki a koutou te aromatawai i te pānga o ngā, me te kitea matahoki.

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