HauoraDiseases me ngā Here

Polycythemia pono. Take, tohu, Diagnosis, Treatment

Polycythemia - Ko reira te mate e taea te whakaritea mā te titiro anake i te mata o te tangata. A, ki te kawe tatou i whakamātautau tātaritanga, te feaa, me te kore e noho. I roto i te tuhinga hauora i reira he ingoa atu hoki tenei māuiuitanga: erythremia, mate Vakeza. Ahakoa o te wā, notemea te mate he riri nui ki te ora te tangata. I roto i tēnei tuhinga ka aparau i tatou i roto i te taipitopito nui te huarahi o tona tupu, te tuatahi tohu, ngā wāhanga, me te maimoatanga tapaea.

mōhiohio whānui

I raro i polycythemia pā myeloproliferative pukupuku toto i roto i nei te hinu wheua wheua hua pūtau toto whero i roto i rahi. Ki te whānuitanga iti te kitea atu wāhanga whākōkī hua, ara leucocytes me platelets.

pūtau toto whero (RBCs te kore) kukū ki te hāora, ngā pūtau katoa tangata, tuku i te reira i te pūkahukahu ki te pūnaha o te whekau. E hoki ratou kawenga mo te tango o te hauhā i te kopa, me te kawe i te reira ki te pūkahukahu mō launoa muri.

E hua tonu Erythrocytes i roto i te hinu wheua wheua. Ko he kopa spongiform plurality paetata roto te wheua, a ka he kawenga mo te tukanga o te hematopoiesis.

Leukocytes - ma pūtau toto e te tauturu i mate whawhai. Platelets he whatiwhatinga pūtau anuclear i te tapatahi iaia ngangau. E ratou te kaha ki te piri ki tetahi ki tetahi, me te occlude te whakatuwheratanga, reira tu i te toto.

Polycythemia pono āhuatanga e production nui o ngā pūtau toto whero.

nuinga

Kei te nuinga o pāngia tenei māuiuitanga i roto i ngā pakeke, engari ka taea e puta i roto i taiohi me ngā tamariki. e kore e taea te ua e te mate mo te wa roa, e te mea asymptomatic. E ai ki ngā akoranga, te tau toharite o te tūroro pae i 60 ki pā ana ki 79 tau. He nui iti pea ki te tiki mate iwi Young, engari rere ratou i te mate nui uaua. Ko te māngai o te sex kaha, ki te whakapono koe i te tatauranga, e rave rahi taime atu pinepine pāngia ki polycythemia.

pathogenesis

Te nuinga o nga raruraru hauora e pā ana ki te mate, puta tika ki te hua tonu i roto i te maha o ngā pūtau toto whero. Ka rite ki te hua, riro te toto rawa matotoru.

I te tahi atu te ringa, nui haere tona pokey whakaoho te hanganga o clots (thrombi). Ka taea e ratou te pokanoa ki te rere toto noa i roto i nga pera, me uaua. Ko te maha he āhuatanga taua te take o whiu me whakaeke ngakau. Ko te mea, ko te taua toto matotoru i rave rahi oko wa pōturi. kua ki te faaitoito atu kaha ki te pana mo'oni ia te ngakau.

Tērā o te rere toto e kore e tukua te whekau ki te whiwhi i te nui e hiahiatia ana o te hāora. e faatupu tenei te whanaketanga o te kore ngakau, pāhoahoa, angina, ngoikore, me te tahi atu mau fifi hauora, e kore e tika kia mahue tautahi.

whakarōpū o mate

  • I. Ko te wāhanga tuatahi.
  1. pumau reira hoki 5 tau, neke atu rānei.
  2. Te kōateate rahi noa o.
  3. whakaatu whakamātautau toto he hua āhua i te maha o ngā pūtau toto whero.
  4. uaua pāngia pōauautanga.
  • II A. taahiraa polycythemic.
  1. Roa i 5 ki e pā ana ki te 15 nga tau.
  2. He he he hua o te tahi mau whekau (kōateate, ate), toto, me te Thrombosis.
  3. Ngā wāhanga o te puku i roto i te kōateate kore ano e.
  4. Ka taea e toto whakapataritari hē rino i roto i te tinana.
  5. I roto i te tātari o te toto i reira ko te hua tamau i roto i ngā pūtau toto whero, ma pūtau toto me platelets.
  • II polycythemic taahiraa B. ki kōateate metaplasia myeloid.
  1. Tātari whakaatu i te nui haere ihirangi o ngā pūtau toto katoa, ki te kahore lymphocytes.
  2. He he he tukanga neoplastic i roto i te kōateate.
  3. Ko te pikitia haumanu o kēkeno puta, Thrombosis, toto.
  4. Ko te hinu wheua wheua ko te hanganga māmālie o pokapoka.
  • III. atamira Anemic.
  1. I roto i te toto, i reira te mea he heke koi i roto i erythrocytes, platelets me leukocytes.
  2. He he he hua korerotia i roto i te rahi o te kōateate me ate.
  3. te nuinga o whanake ana tēnei wāhanga i roto i te 20 tau i muri i te haamauraa o te tātaritanga.
  4. Ka taea te puta te mate ki te kanisā whakapeka ma'i ranei.

Ko te take o te mate

Kia aroha mai, i teie nei e kore nga tohunga e taea te mea te mea ngā āhuatanga arahi ki te whanaketanga o taua mate rite polycythemia pono.

Te nuinga i tahuri ki te ariā viral-ira. E ai ki a ia, kua whakaurua wheori motuhake (i reira e pā ana ki 15 nga wahi) ki te tinana tangata, me te i raro i te mana o te tahi mau āhuatanga e pēhia ngā te parepare ārai, tomo ki te wheua wheua, me te waitinana kōpuku. i reira nga ngā pūtau hei utu o te maoa tere timata ki te wehe me te tini, hanga he whatiwhatinga hou.

I te tahi atu te ringa, kia polycythemia take e piri i roto i te predisposition tuku. Kua kï Scientists e he pängia ana ake ki te kati whanaunga o te tangata mate, me te iwi ki te hanganga waimaero o pūira tenei mate.

Predisposing ki āhuatanga mate

  • irradiation X-ray, ionizing radiation.
  • mate intestinal.
  • Viruses.
  • Mate kohi.
  • Surgery.
  • ahotea auau.
  • whakamahi wā-roa o etahi rōpū o raau taero.

pikitia haumanu

Tīmata i te wāhanga tuarua o te mate, i roto i te tukanga pathological e unu tata pūnaha katoa o whekau. Tabulahia i raro nei te mana'o tuakiri o te manawanui.

  • Ngoikore me he tikanga onoono o te rohirohi.
  • sweating nui ake.
  • Te heke whakaari i roto i te mahi.
  • pāhoahoa Taumaha.
  • waimaerotanga mahara.

kia hoki Polycythemia pono kia haere tahi e te tohu e whai ake nei. I roto i ia take rerekē ratou pakeke.

  • Uaua me te huri i te hue o te kiri. Tūroro mōhio te aroaro o uaua mārama. I roto i tenei mate i te kiri āhuatanga e here-whero Āroha, he reira rawa kitea runga i te wahi kitea o te tinana (arero, ringa, mata). He puru ngutu, whakaaro whero ona kanohi. Tenei huringa i roto i te ahua ko e tika ana ki te waipuke o nga oko toto mata, me te āta tohua i roto i tona whakatairanga.
  • kiri oranga. puta tenei tohumate i roto i 40% o te wā.
  • Rodonalgia (mamae tahunga tūao i te tohutohu o nga maihao, me matimati, e kua haere tahi i whero o te kiri). e pā ana te putanga o tenei tohu e ki nui haere ngā taumata o platelets toto me te hanganga o mikrotrombov.
  • Te whakanui ake i te rahi o te kōateate.
  • Ko te ahua o keha i roto i te puku. No te mea o te tinana oko Thrombosis mucosa iti ngaro tona ātete ki Helicobacter pylori.
  • clots toto. E faataa e ake te pokey toto me huringa i roto i te taiepa iaia ratou take. Ka rite ki te tikanga, arata'i te āhuatanga taua ki te rangirua o te tohanga toto i roto i te wahi o raro, kaka me oko coronary.
  • Mamae i roto i te waewae.
  • toto taumaha i te pae.

tātaringa

Matua kohikohi te tākuta te hītori oti hauora. Ka taea e ia ui i te maha o haamaramaramaraa pātai: ka puta reira hūhi / breathlessness / hūhi mamae, me ētahi atu He mea rite nui ki te whakatau i te aroaro o mate mau, peu kino, whakapā taea ki matū paitini ...

Na, he whakamātautau tinana. Ko te mātanga whakatau te tae o te kiri. Na roto i te palpation me patopato heheu te kōateate rahi ate ranei.

Hoki te haamauraa o te mate e whakaritea he whakamātautau toto whakahauanga. Ki te he tenei māuiuitanga te manawanui, ko nga hua whakamātautau e whai ake:

  • Te whakanui ake i te maha o ngā pūtau toto whero.
  • hematocrit tawhā mā'olunga (ōrau o ngā pūtau toto whero).
  • tawhā pūtoto High.
  • taumata iti o te erythropoietin. Tenei taiaki te kawenga mō te whakaongaonga o te hinu wheua wheua i roto i te hanga o ngā pūtau toto whero hou.

titau hoki tātaritanga te unuhanga roro me te aspirate. Ko te putanga tuatahi o te ako tā rōpū o te wahi wai o te roro, me te unuhanga - wāhanga mārō.

mate polycythemia whakapumautia e whakamātautau mō te irakētanga ira.

He aha kia tukinotia?

Mutu hinga te mate pērā i polycythemia pono, e kore e taea. Ko te aha arotahi te therapy te anake i runga i te whakaiti i nga faaiteraa haumanu, me te whakaiti pōauautanga thrombotic.

Tūroro i matua whakaritea e totó ko. Tenei tukanga titau te tango o te nui iti o te toto (i 200 ki pā ana ki 400 ml) ki te whakaaro curative. Ko e tika ana hoki te māori o nga tawhā ine o te toto te reira, ka whakaiti i tona pokey.

Kei te nuinga o tūroro whakaritea "ahipirini" i roto i te tikanga ki te whakaiti i te tūponotanga o te whakawhanake i ngā momo o pōauautanga thrombotic.

whakamahia hahau te ki mau tonu hematocrit noa, ka reira he minamina nui, nui haere thrombocytosis ranei.

Ko te tino onge wheua wheua transplantation e whakamana i roto i tenei mate, mai kore he whakamate te māuiuitanga i te take o te maimoatanga tika.

Me kï hoki te talena maimoatanga ngā i roto i ia take i tīpakohia takitahi. Ko te therapy i runga-whakaahuatia he mō ngā take mōhiohio anake. E kore e tūtohu ana ki te ngana ki te akakoromaki i tenei mate.

pōauautanga taea

He nui te mate nui, na e kore e whakarerea e tona maimoatanga. Te kore, kei te piki haere te reira i te tūponotanga o pōauautanga kino. Ko ētahi o ēnei te whai ake:

  • clots toto. kia Take o tukanga pathological kia piri i roto i te whakanui ake i pokey toto, te whakanui ake i te maha o ngā pūtau toto whero, me platelets.
  • Urolithiasis me te kauti.
  • Toto, ara i muri i ngā tukanga hāparapara iti. Ka rite ki te tikanga, he raruraru taua fehangahangai muri niho tangohanga.

outlook

mate Vakeza - he mate onge. Tohu e puta i roto i te tīmatanga o tona whanaketanga, kia waiho meinga hoki te whakamātautau tonu me te therapy whai-ake. I roto i te ngaro o te maimoatanga tika, ki te kahore i pāngia te mate i roto i te wā, puta mate. Ko te take matua o te mate maha mahi pōauautanga iaia huringa o te mate ranei ki te kanisā ma'i. Heoi, maimoatanga mātau me te pipiki tino ki ngā taunakitanga katoa i te tākuta e taea tino whakawhānui i te ora o te manawanui (15-20 tau).

Te ti'aturi nei tatou e te kōrero katoa ngā i roto i te tuhinga e kia tino whai hua ki a koutou. E noho hauora!

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