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Hyperplasia adrenal - he aha te mea te reira? Tohu me te maimoatanga o te mate

Endocrinologists i roto i to ratou mahi kei te maha fehangahangai ki abnormalities i roto i te whatukuhu. hyperplasia adrenal - he aha te mea te reira? Whatukuhu - takirua okana, e kei te repe adrenal i runga noa he puka glandular. He e hanga e tika ana mō te hormones tinana tangata (Adrenaline, noradrenaline, glucocorticoids, me takoto). Hyperplasia takahi ana nga hormones tika, a ka haere tahi tenei e tohu rerekē.

hyperplasia adrenal - he aha te mea te reira?

A, no te riirii E faarahi adrenal kiko hyperplasia pūtau repe takirua, te tino nui haere ki te tinana i roto i te rahi, ahakoa tonu te reira ona ake āhua. ngā taonga medullary adrenal o me te kiri.

Ko te tikanga ka pā te hyperplasia uho adrenal, i reira whakawhanake he tukanga pathological. maha pāngia Various puku i roto i te medulla.

faaite te reira i te mate i tetahi tau i roto i nga wahine, te tangata me te tamariki.

kitea congenital hyperplasia adrenal te i roto i te rongoā tino maha. Ko te tikanga te maua e te reira i te tuku, engari ka taea e hoki puta i roto i te maha o te tahi mau āhuatanga kāinga waho ranei kino. Ka rite ki kitea māuiuitanga hāngai ana te roto i te tūroro ki te syndrome o Cushing (40% o te wā) syndrome. Kei te nuinga o pāngia tenei syndrome i roto i te tau waenganui, me te koroheke.

e kore e taea te mahue tenei māuiuitanga nui. A, no te fakahohaasi hyperplasia te hanga o hormones tika. I roto i te wahine, i te reira maha ai te pākoko. He maha ngā momo o te mate: hyperplasia nodular o te repe adrenal, nodular, E ruia ana, congenital me micronodular, me hyperplasia o medial waewae. Nuinga o ngā wā puta tenei mate i roto i nga wahine.

Ko te take o te mate

Ai puta tohu ina ka rerekē hyperplasia adrenal i roto i ngā tamariki, te tangata wahine ranei. ka whakawhirinaki i runga i te momo o te mate katoa. pā ana hyperplasia ki tetahi o nga momo, kia ai taua mea idiopathic, solteryayuschey, muanga.

A, no te reira he he momo hanga hypertensive kaha o androgens me mineralocorticoids, he tukanga taua he mana kino i runga i oko tākihi me te fundus, maha arata'i ki takawhita syndrome.

A, no te nui haere momo solteryayuschem hyperplasia androgen production, te kupu i reira ko te kore o te tahi atu hormones whakaputaina e te uho adrenal. Mai hyperkalemia e suka ranei. Ko te ati ko e te tinana he dehydrated, ngaro taimaha.

A, no te virilnoe momo hyperplasia androgen ngaro superaktiven. taihemahema waho tino nui haere i roto i te rahi, i reira he hakihaki, nui haere makawe tinana, musculature rawa whakawhanakehia i roto i te nui.

Tuatahi o te māuiuitanga katoa haamata ki te ahu whakamua e tika ana ki te nui haere secretion o hormones pūtaiaki. he maha o ngā take matua he aha ka whakatika reira te ahua riro o te mate kua:

  • whakararuraru, pūkoro;
  • taumahatanga kaha;
  • mate o Cushing;

hyperplasia adrenal congenital tika ki te meka e noa i roto i hapūtanga, roto i te hapūtanga, huringa mahi whakawhanake. Ko tētahi atu mana'o - te tuku o te mate i te taumata ira. Āhuatanga whakapataritari i te faaiteraa o tohu o te mate: he arā o te hypothalamus me rapae o abnormalities i te taumata ira, he uho motuhake tumu takirua repe, riro i to ratou mau tupuna.

hyperplasia nodular

Doctors wehe te ahunga whakamua o te hyperplasia adrenal ki te maha ngā rōpū rite ki te pikitia haumanu, me te te momo o te rere.

Nodular hyperplasia adrenal. Ko te tuku tenei puka. Nuinga o ngā wā pāngia i roto i te paari, e hë ki te wā. A, no te whakahaere whakakitea tātaritanga te āhuatanga āhuatanga - i runga i te kiri o nodules adrenal i hanga. Ka taea e waiho ratou maha (hanganga lobed) me te kotahi, ki runga ki te 4-5 cm. Whanake syndrome o Cushing. Ko te māuiuitanga, ko te tika ki te kaha whakaongaonga o taiaki adrenocorticotropic, kua synthesized i roto i te repe. Ko te āhuatanga matua o te hyperplasia nodular ki syndrome o Cushing ngā:

  • ānini;
  • "Rere" i mua i te kanohi;
  • haehae;
  • whanoke;
  • ahuatanga whānui;
  • taonga taimaha (matua te kopu, kaki, mata);
  • nui haere te hiahia;
  • totoro tohu i runga i te kiri;
  • hakihaki;
  • hirsutism (i roto i te wahine);
  • houtanga rawakore;
  • hyperpigmentation;
  • pēhanga toto tiketike;
  • piere auau;
  • korekore.

hyperplasia E ruia ana

I roto i tenei puka o te repeure hyperplasia kihai i huri ona āhua, he ngāue māmālie te hua. Otiia i te wa ano i whai ahua ratou nodules. Te tāutu he uaua te momo o te mate. I roto i te tikanga paerewa o Tātaritia te ultrasound kahore hua. E kitea huringa i roto i te tinana anake i runga i MRI CT ranei. Mea pinepine whakawhanake puka ranu, e puta ka te tohu e whai ake nei: hyperplasia adrenal i roto i nga wahine maha arata'i ki te hua i roto i te huruhuru te tinana, whakakitea mataku patua, takawhita, te mōmonatanga. I roto i te tahi mau wāhi i reira he kino glomerular me te whakawhanake i hyperplasia më.

hāngai ana te māuiuitanga o te aldosteronism idiopathic te i runga i te hua i roto i te aldosterone secretion. A, no te whakaaturia hyperplasia rohe glomerular nga tohu e whai ake nei: takawhita, haehae, uaua ngoikore, herenga o kaupapa, e kekeva ake ki pāpāngia, matewai, nui haere putanga mimi, urination pô. Tūkinotanga ai he hua i roto i te toto pāhare pāporo, acidosis. kitea te pēhanga toto nui haere te tonu.

puka nodular me congenital

te tikanga kauneke puka nodular i roto i ngā tamariki me ngā taiohi. Ka taea e faaite mai te reira iho no te mea o kōtītiti ranei mahi adrenal tika ki tuwhena rawa o glucocorticoids. āhuatanga matua o te āhua nodular: putunga ngako kōhikohiko, uaua atrophy, ähua o te kiri, tohu o te mate huka, karere kino me te Cardiovascular, osteoporosis. Ki te kitea tamariki tohu o te mate i roto i te wa, kawea atu he maimoatanga hormonal, he pai te waitohunga. Hyperplasia o te repe adrenal maui - he aha te mea te reira? I roto i tenei take, e kore te mea ti'aturi i runga i te mahi o hormones hyperplasia. A, no te pihi te pukupuku e hiahiatia nui atu i te 3 cm mahi te. whakamahia Laparoscopy te ranei rite ki Fedorov tikanga lyumbotomicheskim uru ki te peritoneum i te taha ki maui.

pāngia congenital hyperplasia adrenal (VDKN) Kei te nui ake pinepine atu i te tahi atu momo. I roto i nga kohungahunga kitea i te auau o te 1 ki te 12 mano. I roto i tenei huru, te tamaiti pūkoro kite, me te ahua. E toru ngā momo matua o (kore-puāwaitanga, ohie puāwaitanga, muanga me te solteryayuschaya.

He solteryayuschaya te puka tino noa. Whakakitea i roto i ngā kōtiro reira germofroditizm rite teka, mau tamaroa kiri pouri huri noa te Tunaroa, piki ure i roto i te rahi. Hoki tūroro āhuatanga e tupu iti me tohu pērā i te momoe, whakapairuaki, lethargy, pēhanga toto iti, maroketanga, hiahia rawakore. Me tukinotia te mate ki nga ra tuatahi o te oraraa, te mate ka taea ranei.

I roto i te puka puāwaitanga kore he ki runga ake tohu, engari i reira he he hua i roto i te kōtuitui o hormones tane sex. Ki te te kore tukinotia te mate, atu raruraru tupu i roto i nga wahine hauora fakasekisualé, me te hinengaro i roto i.

puta te puka kore-puāwaitanga i roto i nga wahine, me taiohi pakeke. Ko te amuamu matua o pākoko, kōtītiti paheketanga, hirsutism me te hakihaki.

hyperplasia adrenal: tohu whānui

Tino maha, tamariki, te tangata me te wahine i kitea e murua ahua o te mate, i te mea kahore tohu korerotia, i roto i te wā, pērā he uaua ki te tātari i te mate. tautuhia puka congenital te i roto i ngā tamariki kē i te tuatahi, me te rua o nga tau o te ora.

I roto i te whānui, hyperplasia adrenal (he aha te mea te reira, kua kua faataa matou) kua te tohu matua e whai ake nei:

  • pēhanga toto iu (iti teitei ranei);
  • te tere o te ahunga whakamua o te mate huka mellitus;
  • hua taimaha;
  • faaiteraa o te osteoporosis;
  • te kōpā o uaua, ratou atrophy muri;
  • Women e "mata marama-rite";
  • waimaerotanga mahara;
  • breakdowns tailiili;
  • ähua;
  • totoro tohu i runga i te kiri;
  • raruraru i roto i te wahi gastrointestinal;
  • e tukupu o te mate;
  • tuku pō o te mimi;
  • matewai nui;
  • psychoses;
  • pākoko;
  • amenorrhea;
  • e kore tau-tika tupu tiketike;
  • timu hairline i roto i te rohe pae tino;
  • hirsutism.

rerekē tangata me nga wahine i roto i nga tohu haumanu o te mate.

Aratohu maimoatanga

Ko pono te pūtake o te maimoatanga te therapy hormonal. kihai i pūtaiao ano whakaritea e pehea pai ki te mahi i runga i te hyperplasia adrenal. Kei te maha ngā maimoatanga. Hoki e whakaritea taiohi tikanga e haerenga, faaiteraa o āhuatanga sex tuarua, kotiro whakaaturia estrogens me tamariki - androgens.

Whakamahia i roto i te maimoatanga o te ngā e whai ake o glucocorticoids:

  • tāpia cortisone;
  • hydrocortisone;
  • dexamethasone;
  • prednisolone.

I roto i te ra e tango te manawanui 2 ranei 3 pota o te hormones (i roto i rite moni). Rēhita me 5% otinga kūhuka. Girls, pērā tamariki, kua ki te hanga i te mau faaineineraa e titauhia ora katoa.

Hoki ia manawanui me kitea te tākuta he huarahi motuhake ki te tautapa tona rautaki maimoatanga (reira katoa tei runga i tona wheako me te matauranga). e kore e therapy Single i te maimoatanga o tenei mate te tīariari.

hyperplasia congenital o uho adrenal tukinotia nui e tākuta. He take e kore e taea te rerekëtanga nga kikokiko rite wahine tane ranei. No te kōtiro te kirihou tūtohu reira ki te āhua kōhikohiko o te labia. Kua i roto i te tuatahi o nga tau o te ora whakaatu te mahi taua, i ētahi wā (i roto i te huru nui) te kawea reira i roto i muri mai. Hanga te mahi, me te i roto i pukupuku.

Ki te hapa te tinana tote, kia whakapiki ake i te manawanui te horopeta rā o 1-3 karamu. Kia whakaritea i roto i ngā take pērā, me mineralocorticoid.

e kore e ruia ana therapy hyperplasia tarukino i nui pānga. Kei te hiahiatia te reira i roto i ngā take pēnei i adrenalectomy. maimoatanga whai hua me te aldosteroma ka ngā ki hyperplasia E ruia ana. He kino te matapae. Ko te kaupapa o te whiriwhiri he therapy tarukino me te zona glomerulosa hyperplasia më (hyperaldosteronism idiopathic). Mahi i roto i tenei take - he he mehua tino.

Ko te nui rawa o te maimoatanga IGA - te fariiraa i spironolactone, he reira he enemi o aldosterone. whai hua hoki ko te eplerenone tarukino. Kei te maha tangohia Spironolactone i roto i te huinga ki te enemi konupūmā. Ki te nga tohu matua hakari takawhita, hono maimoatanga ki inhibitors ACE te.

I roto i te take o te fariiraa o te virilization o raau taero tiaki i runga i te wā. Ki te pā te momo o te hyperplasia adrenal ki te virilizing, kia waiho te whakarite o te cortisol. Ka taea te whakamahi i te reira hei werohanga intramuscular. tangohia whängainga tākuta. kia whakamahi hoki ngā tamariki pakeke prednisolone.

Ki te kahore he maimoatanga tika, kia te hyperplasia arahi ki te whanaketanga o te mate Kona ranei mate o Cushing. I muri i te maimoatanga tātaritanga tika kia timata tonu.

tātaritanga o te mate

hyperplasia adrenal - he aha te mea te reira? Me pēhea te ki te tātari i te mate? hyperplasia nodular a ruia ana kitea i roto i te akoranga o te rangahau mauhaa me taiwhanga. Ko nga tātaritanga ngā: rangahau manawanui, whakamātautau tinana, whakamātautau haumanu, whakamātautau radiological ranei atahanga te kōwarotanga autō, matawai radionuclide. E ai ki nga hua uara aromatawai, me te ahua o e rua repe adrenal. whakamana Radioimmunoassay rangahau taiwhanga. Whakaritea i roto i te mimi me te toto cortisol. Hei aromatawai i te mana hormonal, mau-hono anga matou immunosorbent. I te tahi taime te mea e tika ana ki te whakahaere i wawata poka.

E ai ki nga hua o te tātaritanga fakae'a te tākuta te tātaritanga me vahe te tikanga tino tika o te maimoatanga.

pakeke hyperplasia: he aha ki te mahi i?

E pāngia te tikanga te totoa o te uho adrenal i aruaruraa, engari puta nga tohu o te mate i roto i ngā pakeke. hyperplasia adrenal i roto i nga wahine āhuatanga e te tupu nui o makawe tore, reo hohonu, hakihaki, te mamae i roto i te hoki o te matenga, haurangi po, kai rawakore, te pēhanga toto nui haere, syndrome adrenal.

Ki te kitea e koe koe i roto i enei tohu, e kore e tamata ki tātari koe. I roto i enei take e kore e te āwhina, me rongoā iwi. Wawe te whakatutuki ki tākuta. E mea titauhia ki te maimoatanga hormonal. Ko te tikanga, e kore te wahine ki te tātaritanga taua tūtohutia ki te whakamahere te hapūtanga. I roto i te nuinga o te wā, tae noa rāhuitia ki te hoatu whanau. I te tahi taime te otinga pai ki te raruraru - i te whakakorenga oti o tākihi mate, me ona konga katoa.

ārai

He aha te mea hyperplasia adrenal - he hiahia rawa ki te mohio te hunga faaipoipo e whakaritea te whanautanga o te tamaiti, me te i roto i te utuafare i ratou (ira) take o hyperplasia congenital. Tena tirohia ki geneticists - mohio, ngaio mōhio. Hoki te ārai o te mate ka Me ki kia tātaritanga o perinatal (te wā, ka te whakawhanake tonu te tamaiti, me te kei i roto i te kopu o te whaea). I roto i te huatū tuatahi o te hapūtanga kawea i roto chorionic villus tīpako. I roto i te hawhe tuarua o te tātari hiahiatia o waikahu, e ka whakatau i te taumata o hormones.

Kōwhiringa - IVF. I roto i tenei take, ka taea e hanga e koe he tātaritanga ira tuatahi o ngā pūtau iroriki i mua e wairakau ratou.

Roto i te hapūtanga te wahine pāngia ki hyperplasia kia kia i raro i te tirotiro tamau o te tākuta haere whakamātautau e hiahiatia katoa wā. Kia waho i te ora o te matū paitini katoa taea, me nga pānga o te radiation.

Hoki te ārai o te hyperplasia adrenal e whai wāhi me te āta nui whakamātautau ki te kia whakamana i roto i te tamaiti hou. Hoki te tātaritanga he mea e tika ana ki te tango i te toto i te capillary (he wahi whiriwhiri mō te poka rekereke koati).

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