HauoraDiseases me ngā Here

Kua raruraru te etiology o sarcoidosis me he aha mate ki te syndrome Lefgrena

Lefgrena syndrome - he kōpuku hilar pūnaha lymphatic bronchopulmonary hangarite i runga i ngā taha e rua. Mate tahi e te faaiteraa kiri (erythema nodosum), nui te kirika, me te arthralgia. He āhuatanga o te sarcoidosis enei tohu.

A, no te pānga o te mate whekau rerekē - pūkahukahu, kōateate, taikiri. Lefgrena syndrome sarcoidosis kore tuku me te mea e kore te mate ma'i pee. E kore e ki te e raruraru ki te tukanga mate oncologic me te mate kohi.

pikitia haumanu

Kua Sarcoidosis kua he roa rawa te wa he mate onge, engari i tenei ra ke te āhuatanga kua, horahia māuiuitanga i te auau tere huri noa te ao. E ai ki ngā tatauranga, neke atu i te tangata atu ki te mamae i te wahine Lefgrena syndrome i te 20 ki te 40 tau, engari ka taea e te mate haere mai ki tetahi tangata.

Ka taea e tupu te reira i waho tohumate, riirii ranei i roto i te puka whakapeka. whare hauora Asymptomatic te tikanga kitea e tupono noa i runga i te whakamātautau fluorography ārai. Ko te tino noa ko te haereraa äta o te mate, me te mo te tohu e whai ake nei:

  • dyspnea runga tautooraa;
  • he mamae puhoi i roto i te pouaka;
  • mamae i waenganui i te matatahi pokohiwi ;
  • mare maroke;
  • kirika iti-kōeke ;
  • ngenge me te ngoikore;
  • sweating nui;
  • mate o te hiahia;
  • mamae tahi i roto i te hoki o raro.

Koi mō te sarcoidosis huaina syndrome Lefgrena, e haere tahi ai, i tana whakaarahanga i te pāmahana ki te 38-39 ° C, mamae tahi, pāpaka kiri i roto i te puka o te erythema, mamae uma me te hāhā o te manawa. Ehara i te mea nohinohi i roto i te whakapeka i roto i te ora tonu, kahore te whakamahi o te maimoatanga hauora tangata, me te tahi atu wawao.

Ko te etiology o te mate

Tae noa te mutunga o te rongoā mohiotia take o tenei mate, ko reira pea e whakapataritari ai i nga āhuatanga e whai ake nei kia whakawhanake:

  • mate, Mycobacterium kohi, kakā C;
  • āhuatanga o waho kino, ngongoa puehu whakarewa;
  • kai paipa, e kore ko te take pakiaka i, engari nui fakafaingata'a'ia'i te akoranga o te mate;
  • whakapapa.

Prevention o sarcoidosis

syndrome mate Lefgrena nui ki te mutu kai paipa, ki te tere ake ora. wa e tika ana ki te titiro whēkau o te pouaka i roto i te 2 tau. Ka mau ia ki pūkete te meka e kore te te etiology o te mate mohiotia ra ano te mutunga, ki te kia whakawhanakehia te mau parau tumu o te mahi ārai. tūtohu tohunga ki te karo whakapā ki te puehu whakarewa me te aronga o te mate.

Lefgrena sarcoidosis syndrome kitea e whai ake nei te tukanga localization extrapulmonary - hinga te kiko subcutaneous, kiri me taikiri piringa. He he he hua waha, subclavian, axillary me kōpuku inguinal. I roto i ētahi wā, te pāngia taikiri o te puku.

E pāngia Bone me te pūnaha io pokapū nui iti pinepine, engari he uaua hoki te mate puta. Sarcoidosis o te ngakau puta i roto i 20-30% o te wā he asymptomatic. E iti taha Mauī o te ngakau i roto i te rōrahi, te piki ana roro tika.

whakamātautau wawe me te maimoatanga hoatu tūponotanga ki te whakawhirinaki i runga i te putanga pai. I roto i te tahi atu take, i reira he huringa i roto i te pukapuka kikokiko, e te mutunga arata'i ki hauātanga.

syndrome Lefgrena ahua sarcoidosis whakapeka

E mea pinepine raruraru ki sarcoidosis, kohi hoki o te ōrite o ngā tohu. Me whiwhi tēnei he whakamātautau tino, no te mea te take, me te therapy rerekē. I roto i kore take e kore e taea te whai wāhi i roto i te whaiaro maimoatanga-, rawa ki te tango taero tikanga mō ngā tūroro ki kohi, ka taea e arahi i te reira ki te mate.

Lefgrena syndrome (he tauira matarohia) - ko tenei ka huru whānui o te manawanui ko te aromatawai pai. He huringa i roto i te kiri. Kia puta:

  • papules me whakatū papa;
  • Chilblains lupus;
  • pokapoka keloid;
  • infiltrates;
  • erythema nodosum;
  • SKD ko CKD sarcoid Beck;
  • kōpuku mātotoru maha i roto i te kiko subcutaneous.

tātaringa

Aromātai o tūroro Lefgrena syndrome ko ki te mahi i X-ray. Ka rite ki te tikanga whakamahine te whakamahi i tomography computed. Whakahaere tatau matüora me te toto.

Ko te raruraru o te maimoatanga he ki te pehi i te tukanga inflammatory. Ko te ara tino pai ko te whakamahi o corticosteroids mō te ono marama. Ki te pānga ki te whekau faufaa e hiahiatia te therapy ira glucocorticosteroid.

Tere tukinotia akoranga ahu whakamua te ki akoranga poto o te whakahaere rō-uaua o te raau taero anti-inflammatory. I roto i te wā i reira kahakore noa iho te therapy, puritia plasmapheresis (purenga toto). I te mate atamira pūkahukahu kino rapua e huaranga ki te okana. Course o te mate me te maimoatanga hua te nuinga pai, engari e kore e tika ana ki te tīmata i te tukanga.

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