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Kakā Autoimmune. pikitia haumanu

Autoimmune kakā i roto i nuinga o te wā whakawhanake ohorere, me ona mau faaiteraa haumanu e rerekē i te tohu o te kakā whakapeka kahore. I te wāhanga tuatahi o te mate tohua mana'o tangata ngoikore. mimi pouri, jaundice kaha - he tohu e tahi autoimmune enei kakā. Tohu puta kanapa nui noa i te wāhanga tuatahi. Hoki te maha o nga marama, e te reira tuu te pikitia haumanu oti atu.

I roto i te wā onge, āhuatanga kakā autoimmune e te rere āta. Heoi, i roto i tenei take, kua pule'i e mamae me te pouri i roto i te hypochondrium tika, he tangata mana'o hūhi, puta jaundice paku. He maha o te tūroro ki te kakā autoimmune tīmata ki te whakawhanake i te kirika, me te mau faaiteraa extrahepatic.

āhuatanga Taipitopito pikitia haumanu e ngoikore nui, pruritus, whakapairuaki, lymphadenopathy. Hoki te mate Kei te hoki āhuatanga e jaundice (e kore e tamau, engari piki i roto i exacerbations), he hua i roto i te rahi o te kōateate me ate. tahi Kotahi-toru o te wahine kakā autoimmune e amenorrhea (ngaro o te paheketanga) me hirsutism (tupu makawe rite te tangata). I roto i nga tangata, kia whai pānga te māuiuitanga ki gynecomastia (whanaketanga o repe mammary i roto i nga wahine). I roto i te tauhohe kiri nui kia tuhia hakihaki, tōiti me lupus palmarnuyu erythema me ētahi atu pāpaka.

kakā Autoimmune Ko te pūāhua lesion whakamua ma'i ki te aroaro o, autoantibodies serum ate-whai pānga. e te tukanga wahi ki te mumura tika whānui, hypergammaglobulinemia.

kakā Autoimmune. maimoatanga

therapy Pathogenetic o te mate ko te therapy glucocorticosteroid. therapy Immunosuppressive taea whakaiti i te mahi o ngā tukanga pathological tupu i roto i te ate, reira te whakarei ake i te mahi o T-suppressors, heke te kaha o nga tauhohe e whai wāhi ana ki te whakangaromanga o hepatocytes.

Ko te tikanga, whakamahia te therapy te raau taero pērā i "Methylprednisolone" ranei "prednisolone". Ko te horopeta rā tuatahi - e ono tekau milligrams - i roto i te wiki tuatahi, e wha tekau - tuarua, e toru tekau - i roto i te tuatoru-hauwhā. I muri, heke te inenga e ki e rua tekau milligrams, i te mea te horopeta tiaki. kawea therapy tautoko i roto i rite te roa rite te māori o haumanu, taiwhanga me tawhā histological.

Whakaiti i te nui o tarukino riro whakamana āta. e tenei ki pūkete te kaha o te akoranga haumanu me te taumata o tohu serum.

taea te papaki kakā Autoimmune i roto i te hawhe tau. Heoi, i roto i te maha ngā take, pumau therapy he wā roa, i ētahi wā mo te ora. I roto i te take o te kore o te monotherapy whakaratohia whakawhiti taka iahiko "delagil", "Azathioprine", "Ciclosporin".

Ki te kahore i hua immunosuppressive therapy te hua e tūmanakohia ana mō te wha tau e, te aroaro o auau maha, pānga taha i te therapy taea te whakaarahia te pātai o te transplant ate.

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