Hauora, Rongoā
Ataxia - he aha te mea tenei? Tohu me ngā momo o te ataxia
Ataxia - e kore te mea tahi e pāpāngia dysmotility, e ko te āhuatanga āhuatanga o disorders manawataki me te nekeneke ruruku. Iritihia i te ataxia kupu Kariki tikanga "hepohepo" me "whakama".
Ki te riro taikaha, rorirori, hē tenei nekehanga tātaritanga, maha mamae i haere, a ka i roto i ētahi wā noa he kupu. Fakakaukau ki he me'a momo o ataxia tu me aha e ratou āhuatanga.
ataxia o Friedreich
ataxia o Friedreich - he mate neurological ira meinga, e whanau he pūāhua ahu whakamua. Ko te mau faaiteraa tuatahi o te mate hei kitea i roto i te tahi tau ahuru matahiti matamua o te ora.
Tuatahi, i reira he maumaui o ringaringa, me te kiwi e. No te tamariki, Heoi, te whakakite i he uaua te takahi o te ringaringa e tika ana ki te meka e kore te ia ano tino i hanga. Ki te, Me te manawanui i roto i tenei take whakaaro ki te kiwi e ki te tautoko, puritia ia piu. nekehanga katoa o te waewae he nui ake ka tuketuke te atu haere tonu.
whakawhanake te reira i runga i te wā ngoikore ki te tu (astasia) me tae noa haere (Abaza). Heoi, ko te whakamutunga ko te faaiteraa angamaheni o te akoranga tere ahu whakamua o te mate, me ona wāhanga whakamutunga.
ngā huringa i kitea i roto i te tuarā, i te mea nui rawa hoki taiohi, i roto i nei e kore e te tukanga o tona hanganga oti ano. He tau torutoru i muri i te manawanui hoki o rahunga i te mahi o nga repe taiaki whakawhanake mate huka. A iti i muri mai e tika ana ki ngā rerekētanga degenerative i roto i te gonads puta hypogonadism. I roto i te wāhanga whakamutunga o te ataxia hono raruraru ataata puta rite ki te hua o ngā whakarerekētanga degenerative i roto i te whatu, me te oculomotor raru. I runga o taua, e tika ana ki te tūkino ki neurons i roto i te roro whakawhanake tupu.
Ko te hinganga o te roro tuarongo
ataxia Cerebellar - he mate o te nekeneke te ruruku, te whakawhanake me te hinga o te kawenga matua te whanau mo reira, te tinana - roro roro tuarongo. I roto i ētahi wā whakawhanakehia huringa iti, a i roto i te tahi atu - atu nui, me te taimaha.
Ko te whanaketanga o taua ataxia puta tirohanga i karapoti a rohe rerekē o te tukanga pathological roro tuarongo. E mea pinepine cerebellar ataxia pāngia ki encephalitis, cerebellar mate iaia, sclerosis maha, te pukupuku roro mārere, poisoning, me etahi mate o te take mai ira. Tohatoha 2 momo o ataxia cerebellar - hikohiko me te hihiri.
Ko te āhua pateko o ataxia cerebellar
Ua faaite ataxia Cerebellar i roto i te tirohanga pateko o te whakaiti o te reo uaua. Te manawanui i roto i te tukanga riro te reira uaua mo ki he wa roa noho i roto i te kotahi te tūranga, pera i kua e ia maumaui iti o te nekeneke ruruku. Te tangata neke kaupae rawa whanui, me te wiri he i roto i te āhua o te haurangi rite. I roto i ngā take kino, e kore e taea ki te noho me te tu, no te mea, e kore e he noa te kaha ki te pupuri i tona matenga, kei te taka tonu ia te manawanui o te mate. ataxia Pateko i roto i nui whakaputa kaha o te manawanui ki te pupuri i te toenga i runga i to ratou ake. E tano ia tapao e runga i te nekeneke e kore e ruruku pā aha te mea he manawanui ki te kanohi tuwhera kati ranei.
Ko te āhua hihiri o te ataxia cerebellar
Amyotaxy whakawhanakehia ki te whai wāhi o te tuakoi cerebellar i roto i te tukanga pathological. Ki te kitea te momo o te disorders mate Coordination anake, no te te kaupapa tinana. Ngaro nekehanga maeneene me te pau, e heitia ratou me hauwarea. Discoordination me tērā o ngā nekehanga kitea i te taha pāngia. Hoki ataxia hihiri āhuatanga te hypermetric (nui, hoariri waka) adiadohokinez, promahivanie me te whakaaro faaati me kupu disorders (tūroro e korero pakanga e whawhati kupu ki ōna wāhanga).
I roto i te manawanui e tu, me te haere ana e whakakotititia ana te roto i te hāngai pakaru taha te tuakoi cerebellar. Ka huri i ringaringa o te manawanui: riro te reira taratara, maia, reta nui. Ko reira whakaiti taea o reflexes iohere.
ataxia rongo
Tenei ataxia - he mate o kaupapa, i roto i nei i te huringa o te kiwi e puta tika ana ki te mate o te sensation i nga waewae, i te mea he putanga o raru piringa, koropiko medial, pou muri, me pakiaka posterior o te ua. E kore e te manawanui ite te tūranga o te waewae, a reira he uaua e rua ka haere ana, me te ka tu. Ka rite ki te tikanga, kei te ia e tu ki te waewae whanui motu me i te wa ano e taea te pupuri toenga anake ki nga kanohi tuwhera, engari ki te kati ratou, ka tīmata te tangata ki te taihaere me he pea ki te hinga (tohumate pai o Romberg). A, no te haere ana, straddle te tūroro hoki, a ara ia ratou nui ki runga ake i tika, a rūhia piu reira hoki a puta. Ko o ratou takahanga o roa rerekē, me te waewae mo te patunga witi, te whakaputa ka papaki ai oro. Kei te haere ana i te manawanui tikanga whakamahi i te rakau mo te tautoko me te torutoru whakaiti i roto i te utumu hononga hope. Kiwi e ngangau whakahōhā hē ataata. ngaro tūroro maha ratou pūmautanga, tārere me te hinga, ka horoi i tou mata, rite katia e ia ona kanohi, ngaro ratou mana ataata wā.
ataxia spinocerebellar
E pā ana tēnei wā ki te plurality o disorders nekeneke puta te nuinga e tika ana ki rere pūroto wharanga CNS hypoxia perinatal ranei. taui kaha i roto i te kiwi e kia rerekē, me te tei runga i te pakeke me te āhua o te lesion. Ko te kupu, Ka taea e meinga whara iti Babinski, marama nui haere reflexes iohere, a kihai haere tahi e te huringa i tohua i roto i te kiwi e. pāpaka whānui me te ake kino te tikanga uta e hemiparesis taha. Huringa puta me kiwi e matua paraparesis āhuatanga.
pararutiki kaka mahia disorders kaupapa pau huringa i roto i te kiwi e. Tūroro kupu i reira he nekehanga tumu o te wahi, e kua haere tahi e pukana a ki runga ki te mata kaki ranei hurihanga nekehanga. Ka rite ki te tikanga, i whakaputa waewae, me te piko ringa, engari kia meinga tenei karawhiti alangá kitea i muri noa i te mātakitaki tupato o te manawanui. Hei tauira, e taea te whakaputa i tetahi ringa, me te pronated me te tahi atu supinated ka tu mai. Ko te tūnga hangarite o nga wahi, me te maha puta ina tahuri koutou matenga i roto i ngā tohutohu rerekē.
tātaritanga o te ataxia
Hoki tātaritanga whakamahi i ngā tikanga tātaritanga pērā i:
- MRI o te roro;
- electroencephalography roro;
- tātaritanga DNA;
- electromyography.
I tua atu ki tetahi o nga tikanga whakahuatia he tika ki te tango i te whakamātautau toto, ki te kia te uiui e tohunga pērā i te toketā neave, tākuta me te ophthalmologist.
maimoatanga ataxia
Ataxia - he mate nui e titau mahi wā. Treatment e whakahaere toketā neave mātanga, pai he symptomatic me ngā te wāhi e whai ake nei.
- Faaapî therapy (anticholinesterases, "te aau" ATP, B huaora).
- therapy tinana e hāngai ana te ārai ngā momo o pōauautanga (atrophy me contractures uaua, hei tauira) te whakapai ake haere me te ruruku, te pupuri tinana tinana.
omaoma Special mahi matatini therapy mahi, te whāinga o te mea ki te whakaiti i incoordination me te whakapakari i uaua. A, no te e taea tūmanakohia te tikanga tuwhena maimoatanga (pokanga pukupuku cerebellar, hei tauira) he ora wāhanga oti ranei ranei i te iti rawa mutu haereraa atu.
I roto i te ataxia o Friedreich, tango ki pūkete te pathogenesis o te mate, ka taea e te tākaro i te taero tūranga nui e hāngai ana te pupuri mahi punaraungao ( "Huapuhuikowhai", huaora E, coenzyme Q10, waikawa succinic).
Ko te waitohunga o te mate
Ko te tino kino matapae o mate tuku. Neke atu i te wa, tautautefito ki he taimi ko reira mangere, disorders neuropsychiatric anake te ahunga whakamua. Iwi ki te tātaritanga o "ataxia", te tohu o nei ki te tau riro atu korerotia, rite ki te tikanga, nui heke kaha ki te mahi.
Heoi, e tika ana ki te maimoatanga symptomatic, me te te ārai o te haurangi, whara, me ngā mate hopuhopu, te ora tūroro ki koroheketanga.
ārai
He mea tika ki te karo i te mau faaipoiporaa toto. I tua atu, kia mahara ai e te tūponotanga o te tuku o te ataxia tuku i te matua ki te tamaiti, a no te mea maha e tohutohu tūroro ki te mutu i te whanautanga o ratou ake tamariki, me ki te tango tamaiti o tētahi atu.
Ataxia - he mate neurological nui, ki e hiahia ana koe ki te tīmata maimoatanga tonu. Ko te aha kua tāutuhia te wawe tenei mate, ki te pai hoki te manawanui e matapae.
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