HauoraDiseases me ngā Here

Aortoarteriit nonspecific: Tohu me Methods Treatment

I tēnei wā, i reira e he maha nui o mate e taea pā ngā whēkau me ngā pūnaha tinana. Otiia i roto ia ratou i reira ko te hunga e hiahia ana ki te whiriwhiri i te takoto ngā. I roto i tenei tuhinga, kia maheni tatou ki tetahi o enei mate - he aortoarteriit nonspecific, e maha mamae i te sex wahine, me taitamariki pakeke. Ko te mate tino nuitia pāngia i roto i nga whenua Āhia. Kia titiro a ki ona take, tohu, a te wā kotahi aparau i ranei he reira taea ki te akakoromaki i tenei māuiuitanga.

Ko te ngako o te mate

aortoarteriit Nonspecific Ko te mate rūmātiki i roto i nei i reira he ngaronga mata i roto o pera me ratou manga. Ki te kauneke te tukanga inflammatory, te thickening taiepa iaia, haamata apa uaua maeneene ki te wahi i raro, ka whakakapi i te kiko tūhonohono, me i roto i te toto puta oko granulomas arā, o te pūtau nui.

Ka rite ki te hua o taua tukanga oko toto ki te whakawhānui me te whakawhanake matakoma te aneurysm. Ki te kore e te tukanga mutu, ka mutu te reira i te memeha atu o te muka rapa o te kiko uaua maeneene. A haamata ki mamae nga okana me te kopa tika ki te rere toto waimaero. I roto i te pūnaha ao o whakarōpū o mate, ia mate he ona ake waehere, e kore te okotahi aortoarteriit nonspecific. whakawhiwhia ICD M31.4 ia te waehere (te pūtahi o syndrome kikorangi).

Ko te take o te mate

Heoi tawhiti, kihai i i whakapumautia nga take e whakapataritari te whanaketanga o tenei mate, me. Te nuinga kairangahau e whai wāhi i roto i tenei take, ko o te whakaaro e kore ko reira te tūnga whakamutunga i roto i tenei takaro e mate, e arahi ki āhua ārai. he whakaaro taua i hanga e tika ana ki te meka e maha e pā ana aortoarteriit kore-motuhake ki mate, e hāngai ana ki disorders ārai.

I tēnei wā, i reira te mea he rōpū o pūtaiao e kua tahuri ki te paingia te ariā o te whanaketanga mate autoimmune. Tohu o e ko te rapunga o te tūroro ki te paturopi wē antiaortalnyh.

Ka taea e tatou te mea e taea te whakapumautia te huarahi o te mate autoimmune, engari ahakoa he reira tuatahi, kei roto i te whakautu ki te tukanga inflammatory ranei - mea na tawhiti uaua.

whakarōpū o mate

Ka taea e Aortoarteriit nonspecific kia o ngā momo rerekē i runga i te wāhi kua pā rānei:

  1. Ko te momo tuatahi - i roto i tenei take patua kikorangi, me te iti noa manga te pūtahi o e whakawhānui i reira.
  2. I roto i te rua i te momo he iatuku pāngia i roto i te rei me te puku.
  3. Ko te momo tuatoru - pānga kikorangi te pūtahi o ki rei, me te puku.
  4. āhuatanga tuawha e pāpaka o te iatuku pūkahukahu.

Hoki nga mea katoa kaupapa ranei whakawhanake aortoarteriit nonspecific (mate o Takayasu), fakamanamanai mate hauātanga rawa maha. Rawa, ki te pāngia te mutunga rawa.

tohutanga o te mate

He rerekē Aortoarteriit tohu nonspecific, tei reira ki runga ki te ahua o te mate. kia mate Takayasu wāhanga ma'i, me te whakapeka.

whakakitea te wāhanga whakapeka o te mate e te tohu e whai ake nei:

  • ngenge General.
  • I roto i te mahi, te mamae i roto i uaua me hononga.
  • puta te reira i ponana haemorrhagic.
  • Whakawhanake erythema nodosum.
  • Ki te whakanui koe i te rohe o te ngakau.
  • puta te reira i amuamu systolic, me te wā diastolic.
  • take Rare o mamae puku.
  • Ki te tatou kawe i whakamātautau taiwhanga, whakakitea ratou anemia āhua, te aroaro o te pūmua C-urupare.

Tino maha, te faaiteraa o taua tohu misdiagnosed - "kaikōiwi", "TB" ranei "sepsis." Tenei, heoi, puta i roto i te 95% o te wā.

Ko te ahunga whakamua o te atamira ma'i o te mate

Ki te kore e tangohia e te wāhanga tuatahi o te mate mehua whai hua ki te whakaora i te reira, māuiuitanga hohoro riro ma'i. Ko kua rerekē i taua i roto i te wāhanga whakapeka tohutanga:

  • I whakaritea i reira he kahore pini i runga i te ringa kotahi, a ētahi wā e rua.
  • Tūroro pinepine amuamu o te mamae i roto i nga topito, e ki te whakanui ake kawenga rahi roa'tu, anake.
  • Ringa hei ngoikore, uaua hoki ki te iwi te pupuri i ngā taonga.
  • Pinepine riro āmai, e kia hua i roto i te mate o te mahara.
  • A, no te toro koe i kitea huringa i roto i te fundus te ophthalmologist.
  • Mai te mea maha te tukanga whai wāhi te iatuku pūngākau, e taea te kite i te reira patua rere pūroto.
  • Ki te hinga o te haoraora puku timata ki te mamae tākihi.
  • E whakakitea disorders Neurological rite whakarongo waimaero me mahara, heke kaha mahi.
  • Ki te pāngia te faatae te te, ka mamae te kite, puta rua kite, kia matapo kotahi kanohi i roto i.
  • Ko te whai wāhi o te iatuku pūkahukahu ārahi ki te whanaketanga o te hāhā o te manawa, mamae i roto i te pouaka.
  • Tukua hononga o te ringa.
  • A, no te tīmata nonspecific tukanga whakatö aortoarteriit ki te pera matua, e te nuinga o arata'i ki te pēhanga toto nui haere tika ki te whāiti o oko toto.

Tikanga, te wāhanga whakapeka o te mate riro ma'i mō te 6-8 tau. kia tūpato tūroro ki te e tonu whakamamaetia ratou i te ngoikore, ānini, mamae i roto i te akoranga o te pera nui, ruruku waimaero me mahara. Me koe ki te mamae i te whakamātautau tonu i roto i te tikanga ki te whakatū i tētahi tātaritanga tika.

tātaritanga

Ki te reira te mea he māharahara o aortoarteriit kore-motuhake, he tino nui tātaritanga wawe. mohio ana tēnei mate e tākuta, ki te reira ko te tohu e whai ake nei:

  • Ki te reira te mea he rerekētanga nui i roto i te pēhanga toto i roto i te ringa rerekē.
  • Pulse tino ngoikore ranei kahore detectable.
  • He he claudication taratahi.
  • A, no te whakarongo ki te haruru kitea i roto i te haoraora.
  • whakakitea te whakamātautau uaua whāiti.
  • Iti hoki o te piha te pūtahi o.
  • hua tamau i roto i te pēhanga.
  • Kei te nui haere ESR mo etahi take.

I te pae hopea, ki te āwhina i te tātari i te akoranga e whai ake nei:

  1. tātari matüora o toto whakaatu i roto i te abnormalities toto e te hunga āhuatanga o tenei mate.
  2. Ultrasound whakamātautau o nga oko ki te aromātai i to ratou huru, me te auau o te rere toto.
  3. Angiography ki te rerekē werohia kitea matua constriction.
  4. Aaka X-ray kitenga o wāhi o pāpaka o te haoraora me iatuku pūkahukahu.
  5. Echocardiography te aromatawai i te mahi o te ngakau.
  6. Na roto i te electroencephalography taea kitea raruraru i roto i te oko toto kaka.

Ko te kupu, mo tetahi mate, tae atu i roto i te pērā i aortoarteriit nonspecific, haamata hītori hauora ki te rangahau tonu, e whai ana ki te whakatika i tātaritanga.

tātaritanga pārōnaki

He mea tino nui mō te ki te tātaritanga rereke aortoarteriit kōhikohiko congenital o te pūnaha iaia me thromboembolism. Hoki te whakamutunga āhuatanga e te akoranga whakapeka o te hanganga taea o te katinga toto i roto i te kōhao o te uaua ngakau.

He āhuatanga nui ko e pānga te motuhake-kore aortoarteriit rōpū o oko, i hoki kōhikohiko congenital mamae etahi pera.

Ki te whakawhirinaki koe i runga i te takawhita tātaritanga renovascular, he mea e tika ana ki te mahara e taea te whakawhanake i te reira atherosclerosis me tākihi oko. Ki te whakawhanake aortoarteriit nonspecific te nuinga i roto i te taitamariki wahine, pā atherosclerosis tangata pakeke.

he whakamātautau oti, me te mātanga tohu anake ka āwhina i hanga i te tātaritanga me te ki timata maimoatanga whai hua.

syndromes Haumanu i roto i māuiuitanga

Hoatu e i roto i tenei māuiuitanga kia pā ngā wāhanga rerekē o te oko i tuku toto ki nga whekau, ko reira taea ki te tohatoha e rave rahi syndromes haumanu:

  1. hē syndrome o te rere toto piringa. I te wa taua i reira he mamae i roto i te ringa ki te mana'o o te kōpā i te maihao. Ki te patua e te pera vertebral, te mamae i roto i te hoki ki reira.
  2. syndrome Cardiovascular - e pā ana te ki te whanaketanga o te tohanga hei utu. Ka taea e tātari te tohu o myocarditis, ischemia.
  3. Ki te te kikorangi te pūtahi o pā, te whakawhanake syndrome iaia roro. Whakakitea e pāhoahoa, kite iti, te ngangau i o tohatoha kaka.
  4. syndrome puku whakakitea e mamae i roto i te puku, i te mea paroxysmal i te natura. e kore he nohinohi i roto i pāpaka o te haoraora puku tenei faaiteraa.
  5. Takawhita syndrome - puta rite te putanga o pāpaka o nga pera tākihi.

therapy

Ki te tikanga te tātaritanga o "aortoarteriit nonspecific" maimoatanga te ki:

  1. Nui pānga i runga i te arotahi o te mumura, pea na roto i te whakaiti i te reira ki te iti.
  2. Whawhai ki pōauautanga rere pūroto.
  3. Tangohia nga faaiteraa o takawhita.

He aha te ki te he aortoarteriit kore-motuhake te tangata? Tātaritanga kawea i roto i whakamātautau whakahau ano, he mahi motuhake - ki te hanga i te talena maimoatanga. kia Therapy e whai ake:

  • Rongoā.
  • Surgery.

Whakaaroa te taunakitanga me te āhuatanga o ia kōwhiringa.

maimoatanga ki te taero

Rongoā i whakaritea aortoarteriit ka whakaaro te pakeke o te huru o te manawanui, me te āhuatanga rere o te tukanga inflammatory. E whakaritea te nuinga o maha nga raau taero e whai ake nei:

  • "Prednisolone" i roto i te nui o 1-2 mg ia manokaramu o taimaha manawanui. kawea whakauru i roto hoki 1-2 marama.
  • Ki te te mumura he pūāhua ngoikore, whakaaturia te fariiraa i aminohinolinovogo taero, mo te tauira, "meatia Lago" ki 0,25 g
  • hāngai therapy taketake kei i runga i te fariiraa o "methotrexate". Ko te inenga Ko 7-10 mg ia wāhi mata tinana mita tapawha. Fariiraa - kotahi te wiki.
  • āpiha Ngaahi Houalotú He anticoagulants, cardiac me taero e te raro pēhanga toto.

Drug therapy he pūāhua tu'uloa, ki te kahore he whakapai ake ranei i reira ko te rangirua i tohua o wahi, roro, e tūtohu ana ki te huihui ki wawaotanga hāparapara.

maimoatanga hāparapara

Ki te kore maimoatanga momo e te āwhina, a ka noa whiwhi kino te āhuatanga, i ki huihui ki te tiaki hāparapara. tauturu pokanga whakahoki rere toto ki whēkau me te kopa. Ko me whanau te reira i roto i te ngakau e kia mutu te tukanga inflammatory i mua i pokanga. He maha ngā tikanga mō tenei ahua o te therapy:

  • Endarterectomy. Kei te whakamana te reira i roto i te aroaro o te occlusion segmental taratahi o te pera, e rere tika ana i te haoraora.
  • kawea Agnioplastika i te mea i reira he huringa i roto i te oko takitahi o nga whatukuhu.
  • kawea Karo täpiritanga i roto i te whakamahi i te prosthesis iaia waihanga. he whai hua i roto i te pāpaka iaia maha peheé wawaotanga.

I muri he nui wā pokanga whakanohonoho, tautukunga ki tūtohutanga tākuta.

Tohutohu mō te tūroro

kitea e matou i roto i te mea i te aortoarteriit tohumate nonspecific me te maimoatanga i whakaaro hoki, engari ko rite nui te manawanui ki mau i te aratohu e whai ake nei:

  1. kia mōhio ia manawanui e titau te maimoatanga o tenei mate wā me te haapa'oraa o wāhui o tākuta katoa.
  2. He mea tika ki te piri ki te kaupapa me te inenga o te rongoā, kua tohutohu e te tākuta.
  3. Mai te tango moni nui o taero, i reira ko te mōrea o ngā pānga kino i roto i therapy. Hei whakaiti ratou, he mea e tika ana ki te mamae whakamātautau auau me ngā whakamātautau haere.
  4. A, no te te ino o te hiahia ki te whakamōhio i te mātanga.

Ki te piri koe ki enei tūtohutanga, ka kia angitu atu te therapy o te mate.

Ko te waitohunga mō ngā tūroro

Kia aroha mai, ki te pehea e aortoarteritis kore-motuhake taea, engari ngā taunakitanga katoa o te tākuta, me te maimoatanga whai hua hauora e taea ki te whakatutuki murunga. Tenei ka tukua tūroro ki ngā i roto i te mau ohipa mua, me te kore e ite mamae.

Ko te whai huatanga o te maimoatanga tei runga i te pakeke o te mumura me te aroaro o pōauautanga, a kua pāngia ai e te tika, me te tere o te tātaritanga. Na rite i pai ki te hua o te therapy, he mea e tika ana ki te kitea te mate i roto i ona tīmatanga.

e kore e āraihia Motuhake whakaratohia.

titau Tetahi mate he huarahi nui, te ara anake ki te whakatutuki i whakapai ake ranei ara hinga te mate. Tangohia tiaki o te hauora koutou me te kia āta wā - kia taea e koe te kitea abnormalities i te wā wawe, me te ki te whiriwhiri i maimoatanga whai hua.

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