Mate o Caroli: Tohu me te rongoā

mate o Caroli ko te ngangau mahi rawa matatini o te ate, te tātaritanga me te maimoatanga e ai fifi nui mō tākuta.

He aha te mea he mate

Caroli mate - onge mate ate congenital meinga e te roha o te aerodynamics ate, kei roto i te tinana. Kei te āhuatanga i te reira i roto i taua aukati i te waka noa te ate stagnation puta me tona mate rironga. E mea pinepine te mea noa i roto i nga tangata te mate, a haamata i te reira ki te tamarikitanga te taiohitanga ranei. Ko te ahunga whakamua o te tukanga pathological tei runga i te nui me te tohu o te kino ki te aerodynamics roto te ate.

momo o te mate

Ki te rā, kei te ngaro te whakarōpū motuhake o te mate o Caroli i rongoā. Heoi, ahakoa tenei, i reira he momo rerekē e rua o te mate. āhuatanga te puka tuatahi i roto i taua i te patency biliary pakaru, me te hanganga muri o kohatu.

Ko te puka tuarua e pā ana ki kakakīrehe ate congenital. I roto i tenei take, i reira he he roha iti o te aerodynamics me he taea te hanganga o te kohatu, ahakoa kia ētahi wā puta ai i roto i nga wāhanga i muri mai o te mate.

kia hono aerodynamics ate Arā ki ngā wāhanga o te ate whēwhē, me te kupu feruri noa'i i thickening taiepa e arai ana i roto i lumen whēwhē.

take o

E pā ana te mate Caroli ki te mate congenital puta tika ki te autosomal aratau ngoikore o te tupu. Ki te whai koe i whanaunga tata ki te māuiuitanga rite, i muri i te whanautanga o te tamaiti e hiahia ana tonu ki te whakahaere i te whakamātautau whānui, rite reira he he tupono nui o haere i runga i mate tuku.

I roto i ētahi wā, kei te hoki honoa te mate e te tahi atu disorders pathological o te ate, i nui fakafaingata'a'ia'i te maimoatanga.

Ko te tohu matua

Ka taea e tohumate mate o Caroli faaite mai ratou i roto i te tino i tetahi tau i roto i ngā tamariki me te iwi taitamariki. Ko taea ki te kawe i te āhuatanga matua o te mate pērā i:

• mamae puku;
• kirika;
• yellowness iti o te kiri;
• whakarahi ate ki runga ki palpation.

Kei te maha tohua faaiteraa haumanu o te mate e pā ana ki te takanga o te mumura. Fele pāngia mate Caroli te i roto i ngā tamariki tane. I te exacerbation kua he hua koi i roto i te taumata o te bilirubin me tatau pūtau toto ma.

Servicing ko

Ahakoa te meka e makona whakahuatia nga tohu o te mate, engari he āhuatanga o maha atu disorders ate hoki reira. tātaritanga Accurate me ki te whakatau mate taea o te Caroli i te US me i roto i CT. whakaaro tomography computed te tetahi o nga tikanga tino kōrero o te whakamātautau, no te mea ka taea e koe te kite i te pai nui nga maumaui katoa o te ture. I tua atu, kia kia hiahiatia cholangiography endoscopic mō te tātaritanga.

whakamātautau ate mahi mo te wa roa e kore e huri, Heoi, ki te ahunga whakamua o te mate, me te tukanga inflammatory auroa i roto i te tātari matüora o toto e taea kitea nga tohu katoa o te cholestasis.

No te mea he tūroro i mōrea o cholangiocarcinoma, kia kawea te tua i roto i, me te āta serological mo te aroaro o tohu puku.

Āhuatanga o te maimoatanga

I roto i te aroaro o Caroli mate aratohu maimoatanga me kitea mahue te, no te mea he mǎrû i roto i te natura tenei māuiuitanga. Treatment tikanga i te tono o paturopi whanui-hihinga, me mana whakahaere waikawa ursodeoxycholic ki te ārai i tuanaki hanganga.

I tua atu, Kei roto te maimoatanga:

• Pë;
• kohatu litholysis;
• pana i te wai biliary.

Ki runga ki rironga, cholangitis, te tahi atu pōauautanga o purulent therapy ranei he kahore rerekē i te maimoatanga o te cholangitis kitakita. He mea nui ki te tango i te pirau, me te ka kawea purenga te roto o te tau mahani ate, ka tono paturopi ki te āwhina tango mate.

whakamana ana te mahi kei te anake i roto i te take o exacerbations auau whakamahi whai hua o ngā tikanga momo ranei. Ko te rōrahi o te wawaotanga hāparapara kia rerekē tino. Ka taea te nekehia atu kohatu anake ranei irava biliary.

I roto i te take o irava roha rawa kaha, me te stagnation ate biliary, ka taea e te tākuta whakahaere te tango o tetahi taupa o te ate. I roto i ngā take kino, iti hoki ate i roto i te aroaro tohu o e hōloa i roto i te puku mārere ranei, kia tūtohutia te transplant ate i te whanaunga tata.

No te hua pai, te nuinga o ngā tākuta tūtohu roaroa transplantation ate ara i roto i te ngaro o ngā tohu nui i roto i te wāhanga tuatahi o te mate. E mea pinepine, Heoi, ko te aroaro o te mate ko te contraindication ki transplantation. tūroro auau oranga i muri i transplantation ki kakakīrehe congenital e kua ato'a pāngia cholangitis i roto i transplantation, he pai iti.

Waitohunga o tenei mate rawa kino, mai kia puta relapses i runga i te maha o nga tau. Heoi, tino uaua ngā reira i roto i te mate o te manawanui.

mate Caroli

tino maha Caroli mate e pā ana ki kakakīrehe ate congenital, hua i roto i te mate Caroli. Rua o enei pathologies e hanga e e te disorders puka biliary tata ngā i roto i te ate kikokiko i te taumata o te whanaketanga embryonic. riro te syndrome e te whanaunga tata, me te mamae puku whakakitea me toto i varices esophageal. kia waiho Neonates he huinga o nga tohu matua o te kakakīrehe ate congenital, mate Caroli me mate tākihi polycystic.

E pā ana tēnei mate ki te whēwhē ate tau mahani congenital, Heoi, ko reira tino onge, me te nuinga i roto i te iwi kei raro i te 30 tau. I roto i te torutoru nga tau tuatahi o te māuiuitanga puta tata asymptomatic, rite te roa rite te roha o te aerodynamics ate kore e whakapataritari stagnation o te ate, e ka hanga tikanga mo te hanganga o kohatu, me te rironga mate. Ki te whakamahia tahi me ētahi atu tohu i kitea ai o jaundice, tohu te reira i te aroaro o te cholangitis.

whakanui te reira i kino ate te nuinga maui-taha, engari ka taea e hoki kia he rua-ara i roto i ētahi wā reira.

I roto i ētahi wā, ko na kaha te ate e taea pā reira te tahi atu whēkau. Na e taea te whakaaro tetahi o nga pōauautanga rite te takanga o te täkihi.