Hauora, Diseases me ngā Here
Syndrome o Goodpasture: Okú, Tohu me Methods Treatment
syndrome o Goodpasture - he mate autoimmune onge tahi e te i te whakatupuranga o te paturopi mohiotia e te whawhai i te pūtau o te pūkahukahu me whatukuhu. mate e rite te nuinga pānga tangata i waenganui i te tau o te 12, me te 35 tau. Kei te whakapono te reira e etahi tūroro i te keno ira ki te ngangau taua.
syndrome o Goodpasture: te take o te mate
O te akoranga, te manawanui tangata kua he predisposition ira ki te mate. Otiia, i reira he āhuatanga e tīmata i te tauhohenga autoimmune.
Ki te whanaketanga o te mate hua te pūnaha ārai mate paturopi e patu i te membrane basal o nga tōiti o alveoli pūkahukahu me te tubules tākihi. Ka rite ki te hua o tenei tukanga pāngia te ka pakaru tōiti, meinga toto ā, me tohu e pā ana.
Hoki te wā tuatahi kua he mate taua kua tuhia i roto i te 1919. Ko ki tenei ra e kore e mohiotia ai te mea ka pāngia e te whakautu ārai. Kei te whakapono te reira e pā ana syndrome o Goodpasture te ki ngā mate hopuhopu. I te tahi taime te faaitoitoraa o te mate meinga e etahi matū me paihana. tuhia te reira i te maha o ngā take i roto i i timata te syndrome ki te whakawhanake i muri i tango rongoā.
syndrome o Goodpasture: tohumate
Tikanga, nga tohu tuatahi o te pūnaha romahā. amuamu te manawanui o te mamae pouaka, mare auau me te hāhā o te manawa i runga i tautooraa. E ai hemoptysis tīmata ki te whanaketanga o te mate. Ka taea e te pūkahukahu rongo te wheezing mākū maroke ranei. kia wheako i te manawanui rohirohi tamau, me te momoe. I te tahi taime i reira he he mate taimaha whakaari e tika ki te hekenga i roto i te uaua papatipu. Anga ke ki te whakapono rongonui, kahore e te tōiti i roto i te kanohi pāngia e te mate.
Mai i reira he nui toto iti, te tohu muri - ko reira anemia, anemia ranei. Ki te tirohia e koe i te manawanui, e taea te kite i te reira e te mea ha ma rawa tona kiri. He he cyanosis o te kiriuhi mucous. I roto i ētahi wā, pupuhi o te mata puta. Kei te tikanga nui haere te pāmahana.
puta tohu o te mate i roto i nga whatukuhu paku muri mai. Kia kite koe i te kōwhiringa o te nui iti o te toto i roto i te mimi. kauneke tere täkihi me te haere tahi i ona ake tohu.
syndrome o Goodpasture: tikanga tātaritanga
I roto i te tikanga ki te hanga i te tātaritanga, me āta titiro te tākuta te manawanui ki te kite i te hua me ngā whakamātautau ECG. I roto i te whānui, e taea te kite tātari o toto anemia hē rino , me te tatau leukocyte nui haere, nui haere ESR. Urinalysis kitea mimi i roto i moni nui o te pūmua, me te pūtau toto whero. kia tino tirotiro koe te sputum, kia rite ki te mea ka kitea hoki reira pūtau toto whero. E kia whai hua, me te spirography e tauturu kitea maumaui o respiration waho. Vahe ki hoki ako ECG o hau toto, x-hihi, me te unuhanga o te kikokiko pakaru, e hanga ana e ia taea ki te hoatu i te tātaritanga ení.
syndrome o Goodpasture: Maimoatanga
I roto i te meka, he kino te waitohunga mo taua tūroro. Na te mea tino nui i konei - ki te wa te tātari i te mate, me te timata maimoatanga hohoro.
Kia aroha mai, e kore e hakari drugs motuhake mō te taua mate. Otiia kï reira e i roto i nuinga o te wā, subsides rawaka mahi therapy syndrome i roto i 6-9 marama. Ki te taea e koe te aukati i te whanaketanga o te mate tākihi me te pūkahukahu, ka taea e te manawanui ora. Tikanga, whakahau kaiwhakaako he maha o te fariiraa i corticosteroids. Kei te whakamana Plasmapheresis, ki te tika - huhu toto , a tae noa tākihi transplantation. I roto i te tikanga ki te mutu i te whanaketanga o te anemia me hē rino makona whakahau rongoā e tika ana. Otiia ētahi wā, i roto i te wā tino kino, e hiahiatia ana he huhu toto e mo te whakakorenga o te anemia.
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