Syndrome o Gilbert: he aha te mea te reira? Take, tohu me te maimoatanga o te mate

tahi te mate e te ngangau o bilirubin pākia, i whakaahuatia ai te tuatahi i roto i 1901 i te A. N. Gilbert (Gilbert). E ai ki ngā tatauranga, me mate rite anga e pā ana ki 5-7% o te taupori ao. Heoi he aha i reira he syndrome o Gilbert, he aha te mea reira me aha e ona tohu? He reira taea ki tino whakaora te mate?

syndrome o Gilbert: he aha te mea te reira?

I roto i te tikanga ki te matau te mea rite he tika te mate, he mea e tika ana ki te tuatahi kitea ētahi āhuatanga o te bilirubin pākia. Tenei ngarahu kōwhai, i hanga nei e i roto i te ate e te pirau o pūtoto (te ngarahu romahā o te toto). Kei te tahuri te reira i ki te noa kōwhai ngarahu puka herea i roto i te kopa o te ate. taka bilirubin conjugated pērā ki te gallbladder, a ka neke tahi ki te ate ki te wahi kūnatu me excreted ki feces. A, no te tenei mate he bilirubin herekore i roto i te piki toto.

syndrome o Gilbert te tino maha pāngia i noho o Africa, ahakoa he mea noa i roto i te iwi o te tahi atu Iwi. E te ara, mamae tangata i tenei mate ko e pā ana ki 10 ngā wā atu pinepine atu i te wahine.

syndrome o Gilbert: he aha te mea te reira, a he aha faatupu te reira?

Ko te mate riro e pā nei te ki te mahi o etahi ira tenei. Ka rite ki te hua, runningaway nga hepatocytes ate iti glucuronyl. Ko tenei whākōkī te kawenga mō te here o te bilirubin ki glucuronic waikawa. Nä, ko te kaimahi o te taonga kaha arata'i ki taumata teitei o free ngarahu kōwhai i roto i te toto.

syndrome o Gilbert: he aha te mea reira me aha e ona tohu?

Ko te tohu matua o tenei mate ko te jaundice. Me kï reira e te ähua o te mate e taea te pōreareatanga e āhuatanga rerekē. I roto i ngā, kitea te ino o te huru o te taata e rite ki te hua o te ahotea nui, te rohirohi tinana, pohokore ranei hemokai, te whakamahi o etahi rongoā, me te mua mate inflammatory myocardial.

I roto i te hononga ki te hua o te kukū noa o bilirubin i roto i te toto puta yellowness o te kiri, me te mā karu. Ki te whanaketanga o ētahi atu tohu o kia puta te mate. Ētahi tūroro amuamu o pāhoahoa, kukū waimaerotanga, whakama, whanoke, mahara waimaerotanga. I te tahi taime i reira he he ongo o manukanuka ranei wehi pokepoke ki raro, ki te whakaeke aitua, a ētahi wā whārua me te ohoroa.

Noatia, i reira he disorders o te pūnaha kūnatu hoki - ko te mate o te hiahia, whakapairuaki, mamae puku, cramps i te rohe o te tōngāmimi au, ate here, bloating me te korere. I roto i ētahi wā, tipu ātete o etahi kai, pērā i te warowaihā.

I roto i te ngaro o te āwhina wā ki te whakaatu tohu o te kore cardiac matehā ranei, tremors, matewai nui, ruaki tamau, te mamae uaua, taikiri tetere. I roto i te wā tino nui o te kore ate whakapeka whakawhanake.

syndrome o Gilbert: Treatment

Kia aroha mai, te rongoa o mate ira kore he wā e taea. I te tahi atu te ringa, he mārire te nuinga o te mate - he rota o te iwi mō ngā tekau tau e kore e ara mōhio o tona mate. hiahiatia wawaotanga Medical te anake i roto i wā o exacerbation. Na reira, i te tuatahi tohu o jaundice kia kōrero te tākuta. Bed okiokinga, nui o fluids, huaora me te kai tika inu ki te āwhina haerenga i te pākia e. I roto i ētahi wā, whakaritea te manawanui e phenobarbital, i te whakaiti i te taumata o te bilirubin (whakamahi tarukino kore e taea e murua e, mai inenga hē noa te pōauautanga taea o te kore ate). E kore e te kai ngā hua kei roto korotutu me waipiro - Me kia hou, me te pai koromamao kai.