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Polyneuropathy demyelinating ma'i: whakaahuatanga, momo, take, tohu me te maimoatanga

Demyelinating polyneuropathy - mate kino haere tahi nei i mumura o te pakiaka karere ki te whakangaromanga o āta te takotoranga myelin. Ki te whakahaere tika, me te wā o te maimoatanga o te mate e taea te whakakorea ki te karo i mau hopearaa kino. Ko reira he mea nui ki te mohio ki nga take matua me tohu o te mate, i roto i te wa ki te kite i te tākuta.

He aha te mea mate? Overview

Tonu ko reira ia tapao e he onge te mate - 100 mano iwi 1-2 anake mamae i te ma'i rite. He atu e pängia ana ki tenei mate tane pakeke, ahakoa kia kia fehangahangai wahine me ngā tamariki ki te tātaritanga taua. Ka rite ki te tikanga, demyelinating polyneuropathy tahi e te lesion hangarite o nga pakiaka karere, hua i roto i te tipu haere ngoikore o nga topito uaua distal me proximal. E te ara, tino maha, e pā ana te mate te ki Guillain-Barre syndrome. A ki tenei ra ko te reira unknown ahakoa ma'i polyneuropathy demyelinating inflammatory, he mate motuhake ranei he puka o nga tohu i faahitihia.

Ko te take matua o te mate

Kia aroha mai, e kore te te take me te tikanga o te whanaketanga o te mate ki te rā mohiotia ra ano te mutunga. Otiia, Kua whakaaturia ngā wā roa-e polyneuropathy demyelinating inflammatory - he mate autoimmune. Hoki ngā take, ka tīmata te pūnaha ārai mate ki te riro o te tinana ake ngā pūtau rite ke, hua i roto i te whakaputa antibody motuhake. I roto i tenei take, enei antigens patu i kiko pakiaka karere, meinga te whakangaromanga o te takotoranga myelin, meinga mumura. Nä, ngaro te raru ko ratou āhuatanga taketake, e tika ana ki te rangirua o te innervation o uaua me etahi okana.

I roto i tenei take, kia rite ki ki tata tetahi atu mate autoimmune, i reira te mea he kainga ira. I tua atu, i reira e he maha o ngā āhuatanga e taea te whakaputa ke i te pūnaha ārai mate. Ēnei ngā taupatupatu pūkoro tinana, me te hormonal, ahotea nui tinana, me te aronganui, te whētuki, te ahotea tamau, mate nui, mate o te tinana, kano, pokanga.

polyneuropathy Demyelinating: whakarōpū

I roto i te rongoā hou, i reira e rave rahi kaupapa o te whakarōpū o te mate. Hei tauira, i runga i te take rānei, taratahi mate pāwera, ngaukino, inflammatory, paitini, me etahi atu momo o te mate. E ai Pathomorphology taea te wehewehe ake demyelinating me momo polyneuropathy axonal.

kia kōrero hoki tatou e pā ana ki te āhua o te mate:

  • hohoro polyneuropathy demyelinating whakapeka whakawhanake - nga disorders tairongo, me te nekeneke whakawhanake i runga i te maha ra wiki ranei.
  • I roto i te ahua subacute o te mate e kore e tipu rite vitiviti, engari āhua hohoro - i te wiki torutoru ki ono marama.
  • whakaaro polyneuropathy ma'i te te tino kino te mea e taea te whakawhanake i te reira huna. Kauneke o te mate e taea muri mo te maha o nga tau.

Ko te tohu matua o te mate

Ko te pikitia haumanu i roto i taua mate, tei runga i ngā āhuatanga maha, tae atu i te ahua o te mate, me te take o tona whanaketanga, manawanui ngā me tona tau. Demyelinating polyneuropathy, te tikanga i roto i te tīmatanga o te wāhanga e haere tahi i te uaua ngoikore me etahi raruraru tairongo. Hei tauira, i ētahi wā amuamu tūroro o te tūtohutanga iti i roto i nga wahi, tahu sensation, me te mania. Hoki te ahua whakapeka o te mate āhuatanga e te ahua o mamae tīwai kaha. Otira ka tae mai te reira ki te whakangaromanga ma'i o nga pakiaka karere, e kore e taea e te mamae e korerotia rawa, ngaro mai ranei i toe.

Na roto i te paresthesias o pito puta rite te tukanga kauneke. I roto i te tirohanga, ka kite koe i te hekenga ranei ngaro o reflexes iohere ranei ratou ngaro oti. Nuinga o ngā wā kei te reira e hipokina te tukanga demyelination nga raru o wahi, engari he reira hinga taea atu raru. Hei tauira, amuamu te tahi mau tūroro o te kōpā o te arero, me te rohe a tawhio noa te mangai. He nui iti pinepine kitea paresis rangi. I roto i tenei ahua, ko uaua te manawanui ki te horomia kai huware ranei.

Axonal-demyelinating polyneuropathy: Types me Tohu

Ko te whakangaromanga o axons e te nuinga o meinga e te pānga paitini i runga i te tinana. Kei te wehea puka Axonal o te mate ki te maha ngā momo taketake:

  • meinga polyneuropathy koi i roto i nuinga o te wā e kaiao paihana nui (hei tauira, he waikura o te ateneke me te tahi atu tāoke mōrearea). puta tika hohoro Tohu o disorders o te pūnaha io - i muri i 14-21 ra e taea te kite i te manawanui paresis o wahi o raro, me te runga.
  • kia meinga puka Subacute o te mate na roto i te poisoning, a nui arā pūkoro. Ka taea e te tohu matua whakawhanake i runga i te maha o ngā wiki (i ētahi wā ki runga ki te 6 marama).
  • whakawhanake āta ma'i neuropathy axonal, i ētahi wā i te tukanga e neke atu i te rima tau. Tikanga, e hāngai ana tenei puka e ki te aroaro o te predisposition ira, a ka roa haurangi o te tinana (i reira he, hei tauira, i roto i te waipiro ma'i).

tikanga o te tātaritanga

Ka taea e te tākuta mātanga anake tātari "demyelinating polyneuropathy." Tātaritanga o te mate - he tukanga matatini, e ngā he torutoru ngā. Ki te timata, kia whakamātautau tinana mahi, me te kohinga o te hītori oti tino. Ki te he sensorimotor neuropathy e whakawhanake kore iti iho i te rua marama te manawanui, na ko reira he take pai mo te tātaritanga tika atu.

I muri mai, ka rite ki te tikanga, i raro i tūhuratanga atu. Hei tauira, inenga o karere kawenga tere o ponana haere nga raru pūkaha taea whakaatu te whakaiti i roto i te tohu matua. A i te ako taiwhanga o cerebrospinal inu nui haere ngā taumata pūmua kitea.

He aha te maimoatanga tuku rongoā hou?

E therapy titau demyelinating polyneuropathy? Treatment i roto i tenei take ngā o te maha kaupae, ara te tango o mumura, te pehanga o te mahi pūnaha ārai mate, me te hua te tautoko.

I roto i exacerbation o mumura me te aroaro o te tūroro kaha whakaritea hormonal taero anti-inflammatory, ara corticosteroids. Ko te whai hua tino ko "Prednisolone" me ona analogues. haamata therapy ki te horopeta tiketike, e heke rite te ngaro o ngā tohu. Tikanga, tīmata uaua kaha ki hoki mai i muri i te wiki ruarua. Ko te mea ia tapao e te whakamahi wā roa-o te tarukino kia arahi ki ngā pānga taha nui.

Tūroro ki ma'i mate Kei te maha taunakitia ki plasmapheresis, i homai pai hua me tae noa te whakatutuki i te murunga. Ano, kei te whakahaere tūroro taero e taea tautāwhi i te mahi o te pūnaha ārai mate - me tango e ratou akoranga mo tata te ora. Ko tētahi o nga tikanga hou o te therapy hou he immunoglobulin rō-uaua.

Ko te waitohunga mō ngā tūroro ki polyneuropathy

Ko te hua i roto i tenei take, tei runga i te puka o te mate, te kounga o te maimoatanga, me pera me etahi o nga āhuatanga takitahi o te rauropi. Hei tauira, he tangata ki te ahua whakapeka o te mate, i hohoro ka te maimoatanga tika, mamae i te mau hopearaa o te mate nui māmā. A ahakoa e taea te ora tonu e tutuki e kore rawa nga wa katoa, hoki maha tūroro ki te ora noa.

Ko demyelinating ma'i polyneuropathy, e whakawhanake āta me mo te maha o nga tau, ka taea e arahi ki te kino tina heke ki te pūnaha io, hauātanga, me te ara te mate. E te ara, whakawhitia te mate te tūroro paari tino nui.

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