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Cretinism - reira .. tohu, maimoatanga, te ārai me te tātaritanga

Cretinism - he mate o te pūnaha endocrine, haere tahi nei i mahi te heke haere o te repe thyroid. Ko te mate tino noa e te tikanga puta i roto i te kōhungahunga tenei. Na te aha e nga tohu tuatahi? Ko te ofatiraa kino o te kōtuitui o hormones thyroid? He reira tetahi maimoatanga whai hua? ka waiho pahonoraa ki enei pātai o te pānga ki maha kaipānui.

mōhiohio Poto e pā ana ki te hanganga me te mahi o te thyroid

Cretinism - he mate e pā e te ki te mahi thyroid waimaero. Na reira, ki te timata ki reira ka kia whai hua ki te kia maheni ki te kōrero whānui e pā ana ki te mahi o tenei tinana.

Thyroid pā ana ki te repe o secretion ā-. Ko reira pātata ki ngā te wheua ngohe o te paeoro o te matau me te taupa maui, me te Tāmaki tūhono ratou. E hoatu ana te hormones repe matua thyroxine me triiodothyronine, puta noa ki te rawaka moni o iodine nei kōtuitanga. I tua atu, tenei tinana hua etahi atu matū kaha, rawa calcitonin (he taiaki kawenga mō te konupūmā pākia i roto i te tinana).

Tei hoki thyroid mahi i runga i te mahi o te pūnaha hypothalamic-rapae o roto i te roro. Te repe kaituku taiaki thyroid-whakaongaonga, e whakahohetia te tukanga o te ariā o hormones thyroid. He taonga whakaputaina i roto i te hypothalamus, e whakahaere te rapae o.

Ki te whai wāhitanga o te thyroid taiaki puta tukanga pērā i:

  • pākia o adipose kiko mimiti, ariā me te rärangi o ngā rāpoi ngota pūmua;
  • te hanganga o te pūngao, i te mea e tika ana mo te uaua me te pūnaha io;
  • ake i ngā taumata toto kūhuka;
  • Mahi pūnaha io me endocrine (pā hormones thyroid te mahi o ētahi atu repe endocrine);
  • Transport o matū ngā ki ngā pūtau.

Ki te whakaiti o te nui o te thyroid taiaki whakawhanake te mate i huaina hypothyroidism. I roto i te tahuri, ka taea e tenei mate arahi ki cretinism, myxedema, me ētahi atu kōtītiti i runga i te wahi o te pūnaha endocrine.

Hypothyroidism me ona rerekē

I roto i te meka, i reira e maha ngā pūnaha o te whakarōpū o te mate. Nuinga o ngā wā, mamae tamariki cretinism, rite te mate to ratou he hohonu. I te tahi atu te ringa, e taea te whiwhi reira - puta i raro i te mana o etahi āhuatanga.

Tei runga i te take e rave rahi ngā momo o te māuiuitanga:

  • hypothyroidism tuatahi, e pā nei te ki te mahi thyroid waimaero;
  • puka tuarua o te mate e puta i runga i te whakamārama o te arā o te rapae o;
  • hypothyroidism Tuatoru, i roto i nei i reira ko te arā i roto i te ture i runga i te wahi o te hypothalamus;
  • takahi o te tūtohutanga o te pūtau ūnga (i roto i tenei āhuatanga e hua nga hormones i te nui, engari e kore e tairongo enei pūtau).

mohiotia whānuitia ko te ahua o te mate rite cretinism te kōtore - he āhuatanga kitea e te roto i noho o ngā rohe ki te iti rawa iodine.

Cretinism: Take

Tonu ko reira utu mea e reira e maha ngā āhuatanga e taea arahi ki taua mate. Ka rite ki kua whakahuatia, pā cretinism tamariki e whai thyroid taiki hē. A taea e rānei congenital riro ranei te kāwanatanga taua.

Hoki ngā take o te hypothyroidism congenital ngā:

  • hypoplasia congenital ngaro o te repe thyroid o te tamaiti ranei;
  • irradiation o te wahine hapu tango rongoā e whakaiti te mahi o te repe ranei;
  • mate thyroid i roto i te whaea i roto i te hapū;
  • mate ira, i hua i roto i te ärai takahia konutawa thyroid kiko;
  • wātea i te mate ira ki te mate pukupuku o te hormones rapae o;
  • mate congenital e faanane te pūnaha hypothalamic-rapae o.

I roto i te tahuri, puka riro o te mate kia hoki puta i raro i te mana o ngā āhuatanga rerekē:

  • nui iti o iodine i te kai o te wahine hapu he tamaiti ranei;
  • thyroiditis o Hashimoto;
  • mumura o te repe thyroid;
  • whētuki pokanga ranei i roto i te repe thyroid;
  • whara, mumura, me pokanga runga i te roro, e kua haere tahi e pāpaka o te tuaka hypothalamic-rapae o;
  • puku roro.

Tūkinotanga o te tūtohutanga pūtau ki hormones, thyroid

He congenital ka e pā ana ki etahi ira āhuatanga, disorders me te hanganga pūira DNA te huru taua. I roto i tenei mate kua synthesized hormones i roto i te nui noa, engari e kore e he tairongo ki a ratou te pūtau ūnga. Riro i ngā mātua, me te tata untreatable.

Cretinism i roto i ngā tamariki: he aha te mea te ati?

I roto i te meka, he tino kino tenei mate, no te mea hormones thyroid ki etahi whānuitanga whakahaere te mahi o te tata te tinana katoa. Na te aha i te mau hopea e meinga mate?

pānga Cretinism te whanaketanga o te roro, tērā i te reira iho. I roto i ngā, ki te whakamārama o te mate i reira ko te mate whanaketanga o te muka karere, me te he hekenga i roto i te katoa maha o neurons me te hanganga o ngā matū e tautāwhi i te mahi o te roro.

Noatia, meinga te rerekētanga i hormones thyroid me ētahi atu raruraru i roto i te tinana, i roto i ngā:

  • tērā tukanga tupu;
  • uaua ngoikore;
  • iti i roto i te pūmua production me te mana hononga;
  • ngangau i roto i te whanaketanga kōhiwi;
  • tukanga hemodyscrasia;
  • he pūnaha ārai ngoikore;
  • arā o te pūnaha endocrine, rawa te repe adrenal, gonads;
  • he te arā o nga whatukuhu, ate, whēkau, puku;
  • takahi o nga mahi o te kiri.

O te akoranga, ki te ara ake taua raruraru i roto i te kōhungahunga, i roto i te ngaro o te maimoatanga i reira ko te takahi o te mahi o tata pūnaha okana katoa.

Ko te tohu tuatahi o te mate i roto i ngā tamariki

Ko te ara anake ki te kitea te mate i roto i te whanau hou ko te whakamātautau toto mo te taiki. Cretinism i roto i te marama tuatahi 2-3 o te ora, tata kore e puta. Otiia, kia kite i te tākuta he hekenga i roto i te hiahia, hāhā o nasal manawa, raruraru kūnatu auau, auau ngakau iti, me fontanelles nui i roto i te angaanga e te hunga roa tupuria.

Ka rite ki te tupu o te tamaiti e taea te kite, me te tahi atu, tohu atu nui. Kei te whiwhi i te tamaiti taimaha āta engari titiro kiko rite e pängia ana ki te edema. I te tahi taime i reira he arero puku nui. rahi upoko taikaha rite te tinana i muri i roto i te whanaketanga. Ēnei tamariki ahu ki te hei piriti whānui nasal me kanohi kuiti, me te kaki poto, me te matotoru. kia kite koe i te tahi atu te whakararuraru, - tonu tunewha te tamaiti, lethargic, uncommunicative. Ki te tau, kia kite koe i te roa o te whanaketanga hinengaro.

tohu Cretinism i roto i tūroro pakeke

Ki te kore maimoatia, te tohu anake hei kino ki te tau. Iwi e mate ana i te cretinism, whai āhuatanga tinana rawa āhuatanga, pērā i poto roa, ngā wāhanga o te rerekëtanga tinana. Kei te hoki āhuatanga i te reira e te puku tamau, clumsiness tika ki te hanganga tinana, clubfoot, nekeneke waimaero i roto i ngā hononga. He hoki ngā āhuatanga motuhake, pēnei i rae tiketike, ngutu nui, cheekbones tiketike, kohuki tonu arero, kohuki taringa.

Tata tūroro katoa ki te tātaritanga taua mamae i te retardation hinengaro ki tu'unga kehekehe. Ano, i reira e he momo o rongo me te kupu, i ētahi wā ki runga ki te turi-mutism. Mai iti te mahi o repe fakasekisualé ko, ko reira taea te pākoko. I tua atu, he puhoi, kiripiro, ia tau'a enei iwi, me te mamae i etahi ahua o te mate hinengaro.

tikanga Modern o tātaritanga

Ki te kahore he kia kōrero tonu i te māharahara te tākuta. Anake te tohunga mohio e he hypothyroidism, tohu me te maimoatanga e e te aparauraa tatou i teie mahana. Hoki tika tātaritanga whakawa tirohanga anake tafe'anga iti.

Hei timata, whakamātautau toto whakahaere mō ngā taumata taiaki me te thyroid repe. E te ara, kia whakawhanake te tahi mau tūroro i te hypothyroidism rangitahi pera-ka karanga, na haere ano nga whakamātautau etahi wa i muri mai. I roto i te haumanu maha tango toto i whanau hou mō te rangahau ārai.

I muri puritia hoki repe ultrasound thyroid, a hoki, ki te tika, a Doppler Matarua matawai. Ēnei whakamātautau hanga reira taea ki te whakatau i te rahi o te repeure, ko te piki wātea, huringa i roto i te kopa o te pukupuku thyroid repe, me te te āhua o te rere toto.

E whakaatu ana hoki ngā tamariki wheua X-ray, pera i roto i ngā tamariki ki te mate, ko te puhoi ossification kōhiwi. Ki te tika, tirohia hoki te manawanui rata ranei tākuta tamariki, toketā neave, orthopedist, tākuta - kitea āwhina kaiwhakaako te aroaro o pōauautanga, a ki te utu ake te talena maimoatanga.

Methods o te rongoā i te mate

Anake to koutou tākuta mohio ana he aha te mea hypothyroidism (tohumate me te maimoatanga o tenei mate, pōauautanga taea - kia kōrero ki te ngaio enei mea katoa), me ia anake e taea te āwhina ia koutou. Na reira, i roto i tetahi take, e kore e whakarerea e te tohutohu o tohunga.

Ka rite ki te tikanga, kia riro tūroro whakakapinga therapy - tango ratou drugs hormonal e hanga ake te tarepa o tūturu hormones thyroid. I roto i ngā, he reira tino whai hua te te L- thyroxine tarukino «". I tua atu, kia whakaurua ai te talena maimoatanga complexes huaora, taero nootropic ( "cerebro", "Pyracetam", "Nootropil"), me te he medicament mo te whakapai ake i te mahi o te tiaki me te mana te kopa neural ( "Lipotserebrin", "Pantogam", " encephabol ").

He wae nui o te maimoatanga he kai tika, e ka whakarato rawaka moni o iodine. Tei runga i te huru o te manawanui kia hiahia āwhina toketā neave tākuta ranei. I roto i te heke mai, me mamae tonu te tamaiti i te whakamātautau hauora, me te tango i te whakamātautau, te hua o nei e te tākuta e taea te whakatika i te talena maimoatanga.

He aha te mea te outlook mō ngā tūroro?

Cretinism - Ko te tino kino te mate, ka rite ki ara e taea arahi i te reira ki te hauātanga. Otiia, tino maha i roto i te tātaritanga wawe me te maimoatanga tika o te manawanui taea ki te āwhina. Māori o te thyroid me rapae o repe arata'i ki te whakakorenga o disorders pūkoro tinana.

Heoi, e kore take katoa, e taea te karohia pōauautanga. Hei tauira, noho ka tīmata roro mutunga kino therapy. Ae, he uaua ki ara maimoatanga symptomatic me etahi mate ira.

He reira tikanga whai hua o te ārai?

E tano ia tapao e cretinism - he mate tino nui, e kore i roto i tetahi take e taea te waiho. Ki te kite wawe, me te maimoatanga wā taea te karohia e te fifi taimaha tika. Mahino, He hiahia i roto i te pātai o mehemea e taea tatou te ārai i te whanaketanga o te mate maha iwi.

He etahi ture ohie, e tūtohu tohunga ki mau. Hei tauira, i roto i ngā wāhi i reira he noa te mate, e ti'a ia tatou ki te kawe i roto i prophylaxis whānui, i roto i ngā ki te aroturuki i te ihirangi rawaka o iodine i te kai.

No te mea pā tamariki, ko tona thyroid taiki hē cretinism, he reira tino nui ki te whakarongo ki tenei wāhi i te wāhanga whakamahere o te hapūtanga. Hei tauira, kei te tohutohu ngā mātua ki te kia whakamatauria, ka haere i roto i te tahi mau whakamātautau mo te aroaro o disorders pūkoro tinana, me te etahi mate ira. I tua atu, kia te wahine hapu āta aroturuki i te nui o iodine pau. A ko reira nui ki te whakahaere whakamātautau tātari i muri i tonu whanau, no te mea kitea te wawe te mate te, te nui te tupono o te maimoatanga angitu i mua i te ahua o pōauautanga nui.

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