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Cholangitis sclerosing Paraimere: tohu, Te tātaritanga me te rongoā

cholangitis Sclerosing - he mate o nga aerodynamics ate ate i roto i nei haamata ratou taiepa mumura ma'i. Ko te hua o tona takenga he tukanga sclerosis, m. E. Whakakapinga ki nawe kiko. Tenei māuiuitanga e kore hononga causal ki ētahi atu mate ate, engari maha arata'i ki te ahua o pōauautanga i tenei tinana. I roto i te tuhinga o tenei ra, ka whakamārama tatou he aha te whakawhanake sclerosing cholangitis. Ka hoki te aroaro tohu me te maimoatanga o te mate ki tou whakarongo.

tohutoro kikokiko

Ate Ko te wāhanga nui o te tukanga kūnatu. Kei te whai wāhi ia i roto i te rärangi o te ngako, faarahi te mahi o whākōkī pancreatic me whakaihiihi ioio. Ate tonu hua pūtau ate - hepatocytes. Per ra rite ki te hua o to ratou mahi kaha whiwhi te pā ana ki 1 rita o te wai. I muri i taua, tomo te ate te tōngāmimi, me te duodenum.

secretion matamua whakaritea i roto i aerodynamics motuhake. Ka rite ki mai ratou i roto i te intrahepatic me extrahepatic runga i te wāhi rānei. Ka rite ki te hua o ngā tukanga whakaroau, kătahi o tukumate atu take ranei, kia meinga te aerodynamics matia. I te wa ano kōrero e pā ana ki te whanaketanga o taua mate rite cholangitis. He tonu tukanga pathological te etiology rerekē. Na reira, kua taratahi reira momo e whai ake nei: paitini, kitakita, helminthic, sclerosing. Ko te tino onge Last, engari e āhuatanga e kino.

cholangitis Sclerosing wehea ki e rua ngā: tuatahi, me te tuarua. āhuatanga Ia o ratou e te huinga motuhake o tohumate me te akoranga. I roto i te take tuatahi tikanga reira he mate ma'i tahi e te i popoketanga o ate , me te kore purulent aerodynamics mumura, ratou whakangaromanga, me te whakakapinga i te kiko tūhonohono. whakawhanake puka māuiuitanga Tuarua i raro i te mahi o ngā matū paitini. I roto i te wā onge, meinga tona takanga e supply toto iti. I roto i tēnei tuhinga ka arotahi tatou i roto i te taipitopito ake i runga i te kē tuatahi o te mate.

Whakaahuatanga Poto o te mate

cholangitis sclerosing te Paraimere whakarōpūtia te rite pathologies onge o te pūnaha biliary. E ai ki nga raraunga tatauranga, kua pāngia te reira i roto i te kotahi i roto i te wha iwi ia 100 mano taupori. Tikanga o te whanaketanga o te mate te whakaiti i te ahua o te mumura i roto i te aerodynamics iti ate. Ko te kupu i reira ko te pakeke o ratou. Āta Inaki me takere haka i roto i nei rere ate ki te mirumiru. te tono tukanga whakaroau ki te wāhi intercellular o te ate, hua i roto i te cirrhosis.

Ahakoa i te mutunga o te rau tau whakamutunga ko reira taea ki te tātari i te mate i muri anake tafa tūpāpaku ranei. Ngā mihi ki te whanaketanga o te teie mahana mate rongoā e taea te kitea nui mua. Ki te whānuitanga nui i haria ki reira e te tangata 25 ki te 40 tau te pakeke. Ko te tino herenga enei rohe, no te mea e taea e asymptomatic mo te wa roa i te mate. I te tahi taime pohehe nga tohu o te mumura mo mate autoimmune, colitis ulcerative me te kakakīrehe whēwhē.

Ko te take o te cholangitis

He mōhiotia nga take tangohia o te mate. Doctors tawhiti rōpū o ngā āhuatanga e whakanui i te tūponotanga o tona tupu. I roto ia ratou he:

  • predisposition ira;
  • mahi Virus i roto i te tinana;
  • keno ki mate autoimmune;
  • te rongo ki matū paitini.

I roto i enei āhuatanga hoatu te matua huarahi ira. tohu sino o tenei meka e maha rangahau o te mate i roto i te mau melo o te utuafare.

pikitia haumanu

I runga i te raruraru mo nga tau maha kia asymptomatic ranei ki tohumate ngawari. Tūroro kore e taea e maha mea rite ka puta reira tohu sclerosing tohu cholangitis. Kei te nuinga o te wā māuiuitanga kitea e tupono ki te kite i te tākuta e pā ana ki ētahi atu raruraru hauora. I te wa o te tātaritanga whakakitea te tohu tuatahi o te mate - nui haere auau o whākōkī ate.

Ka rite ki nga Rikiraken te mate me te huringa pikitia haumanu. I roto i ona tohu matua o te whai me te miramira:

  • rohirohi, sleepiness tamau;
  • hiahia rawakore;
  • kōwhaitanga o nga kiriuhi mucous me kiri;
  • te whakatairanga i te pāmahana ki te subfebrile uara;
  • maru mamae i roto i te rohe subcostal tika, whakawhānui ki te kaki pokohiwi ranei;
  • minamina;
  • xanthomas maha;
  • hūhi i roto i te hautahi o runga maui, hua i te whakarahi o te kōateate;
  • ähua whakarei o te kiri.

I te tahi taime, cholangitis sclerosing tuatahi tahi mate whēkau inflammatory. Ko ētahi o ēnei colitis ulcerative, mate a Crohn.

tikanga o te tātaritanga

Ki te whakapae koe e rapu tonu te mate tokoni i te tākuta. Examination o te manawanui haamata ki te ako o ngā tohu tuatahi tona hītori, amuamu, me te. I muri i taua, puta ki te whakamātautau tinana. pea te manawanui rapirapi i runga i te kiri, jaundice nui. Kei te nuinga o te wā kitea Palpation te hua o te ate, me te kōateate.

I roto i te tikanga ki te whakaū i te tātaritanga tuatahi o tono tangata hoki whakamātautau anō i te manawanui. Kei roto te reira i te mahi e whai ake nei:

  • whakamātautau toto (i roto i te i te taikaha o tohu o leukocytes me tohu ESR mumura);
  • ultrasound puku;
  • elastography ate (ka taea ki te whakatau tata elasticity tinana);
  • cholangiopancreatography retrograde (Radiography te whakamahi i rerekē);
  • toto mataora (i roto i te cholangitis sclerosing tuatahi kitea whākōkī ate nui);
  • MRI;
  • Ate unuhanga (tenei tikanga o te rangahau āwhina ki te tāutu i ngā wāhi o te kakakīrehe).

Enei tikanga tukua te rangahau ki te whakaū i te cholangitis sclerosing tuatahi. tauturu hoki tātaritanga o te mate whakatau te pakeke o te tukanga pathological. I roto i te katoa i reira e wha:

  1. Portal. Kei te āhuatanga i te reira e te ahua o te puffiness me kakakīrehe ate aerodynamics.
  2. Periportal. E kīnaki Tohu o te atamira tuatahi i te kakakīrehe atu korerotia, me te tukanga whakangaromanga aerodynamics.
  3. Septal. I tenei wā o te mate i reira he tohu tuatahi o te cirrhosis.
  4. Cirrhotic. Āhuatanga e te whanaketanga tonu-parirau o te cirrhosis biliary.

I runga i nga hua o te whakamātautau matatini whakatakoto te tākuta therapy.

Aratohu maimoatanga

hāngai Therapy i roto i tenei mate ko i herea te tukanga inflammatory, te ora o te rere ate me te detoxification o te tinana. Ki tenei mutunga, nga tikanga momo, me te mana o te maimoatanga e whakamahia ana i roto i te rongoā hou. I roto i te take tuatahi tikanga rongoā me te ū ki te kai tino. tohua Pokanga te i roto i ngā take kino, ina hemo maimoatanga momo. Tīpakonga o te tikanga ngā o te maimoatanga he ki runga ki te tākuta.

Ko te whakamahi o te raau taero

Tei runga i te pakeke o te mate, e taea te whakaritea te reira ki te moenga okiokinga me te waho tetahi mahi. Ki te āwangawanga te manawanui kei e pā ana ki te mamae kino, whakaritea ia antispasmodics ( "No-kaukau", "Spasmobru").

Ki te mutu te tukanga inflammatory tauturu i te raau taero e whai ake nei:

  1. Immunosuppressants ( "Azathioprine"). tautāwhi ratou te mahi o te pūnaha ārai mate.
  2. Antifibrogennye tikanga. whakatika nei ia ratou mahi matua te i te whakakorenga o te kakakīrehe, me te ārai o ratou whanaketanga atu.
  3. taiki Glucocorticosteroid ( "Prednisolone"). tauturu i ratou whakaiti mumura.

Ko te whakamahi o enei rongoā taea ki te hinga i te wāhanga tuatahi o te whanaketanga o te cholangitis sclerosing tuatahi. maha ārai Tohu o te mate te ora noa mata mō ngā tūroro. kiri oranga, raruraru wahi kūnatu me te dyspepsia - enei maumaui katoa i te pā tōraro i runga i to ratou hauora. Na reira ato'a whakaritea therapy symptomatic. Kei roto te reira i te fariiraa i ate ( "Essentiale"), whākōkī pekitīlia ( "Creon") me ngā rongoā ki te whakakore minamina. E tīpakohia tonu Drugs takitahi, tango ki pūkete te pikitia haumanu whānui, me te huru o te manawanui.

Āhuatanga kai

i tohaina Tūroro ki te mana "tau tepu 5". A, no te e whakawhāiti i tenei kai te kohi o fatty, parai me rihi raukikini. ngako kararehe he pai ki te whakakapi i te whakato. I tua atu, he mea e tika ana ki te whakakore i tino i te pōhā kai me rare, hua kawa me hua, tiakarete, waipiro, kai me marinades.

whakaaetia whakaaetanga te ki te whakamahi i kikokore kai / ika, etahi momo o te taro, pāreti i runga i te wai. Ka taea hoki te kai e koe hua miraka, te honi, hupa rimurapa hupa huawhenua.

A, no te homai i te tātaritanga o "sclerosing cholangitis tuatahi" maimoatanga ki rongoā, me te kai i te hua pai anake i roto i te wāhanga tuatahi. Ki te ngaro tenei wa te, ka rapu utu pokanga.

wawaotanga hāparapara

tīkina tūpato whakamahia i roto i ngā āhua ngāwari o te tukanga pathological. Ahakoa e kore e te tohutoro wā ki te tākuta hoatu tonu te hua pai i roto i te whakahaere o te therapy muri. A, no te kore e maimoatanga ki taero arahi ki māori o te huru ranei kore ki te whakahoki nāianei noa o te ate, huihui ki wawaotanga hāparapara.

tākuta teie mahana hiahia ngā mahi endoscopic. whakaaro ratou hanga whawhe katoa i roto i vahi iti i roto i te kiri. Heoi, he taua ngā tukanga i roto i te nuinga o te wā hoatu he pānga wā-poto, me he mahi wehe ki pōauautanga. whakahaere hoki poihau pītore me aerodynamics stenting. I roto i te tukanga, fakalahi te rata nga takere o ipurau motuhake, me te whakatakoto ana te mata, te ārai ratou i whāiti. Ki te kahore he ki kia whakarewahia sclerosing cholangitis, te tikanga maimoatanga ate transplant.

pōauautanga taea

huru no te mate e te rere puhoi. pahono te reira i painga ki therapy, me te nui o mau faaiteraa pūnahanaha anake aggravates te tukanga. I roto i te fifi tino noa ona ko te whai ake:

  1. takawhita Portal. haere tahi ana tēnei māuiuitanga e te hua i roto i te pēhanga i roto i te rere toto ate. whakaaro tōna faaiteraa matua te ascites.
  2. syndrome Cholestasis. Ki te puipuitua o pakeke o te aerodynamics ate āta taper i roto i to ratou ripeka-waimaero. whakamārama tenei te ahua o te jaundice me pruritus. Ka rite ki vāofi te ahunga whakamua o te lumen mate ake me te ake. puta Steatorrhea, haere tahi nei i osteoporosis.
  3. sclerosing kitakita cholangitis ate.
  4. pancreatitis ma'i.
  5. Holangiokartsionoma (aerodynamics puku ate).
  6. Cholelithiasis.

Taua pōauautanga puta i roto i te wāhanga 3-4 o te tukanga pathological.

Matapae me te ārai mehua

whakarōpūtia cholangitis sclerosing Paraimere te rite āta ahu mate. Tona hua i roto i te nuinga o te wā he ma'i kore ate. Tino pōhara kē te waitohunga whakanekehanga tau o te manawanui, aroaro o pathologies te rere o te whēkau, te takanga o pōauautanga. Tikanga, me te ahua o nga tohu tuatahi o te mate i mua i te wā whakamutunga toro i 7 ki te 12 tau.

He reira taea ki te ārai i te cholangitis sclerosing tuatahi? Reviews o taote mea e kore kua whakawhanakehia e tika ana ki te iti ako o te ārai motuhake o te mate.

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