Amyloidosis - he aha te mea te reira? Amyloidosis: take, tohu, maimoatanga, tātaritanga

Amyloidosis - he aha te mea te reira? Ko reira he mate o te pūmua pākia i roto i nei te hanganga me te waipara i roto i ngā kopa me whēkau o te taonga pūmua-hukarau motuhake - amyloid.

Ko te whanaketanga o te mate

Whakawhanake amyloidosis (he aha te mea te reira - kua kite kē matou) i roto i te ofatiraa o te kōtuitanga pūmua i roto i te pūnaha reticuloendothelial. Ko te wē , ko te haaputuputuraa o pūmua rerekē. Ko tino ēnei pūmua antigens whaiaro, me te meinga te mate pāwera rite ki te hanganga o autoantibodies.

Na, enei paturopi ki te antigens me huru pūmua grubodispersionnye te hohenga ka. Mai te hanganga o te amyloid. whakatakotoria ana tēnei rauemi kei i runga i te taiepa oko me whekau rerekē. Āta piki, arata'i amyloid ki te mate o te tinana.

Momo o te amyloidosis. take

He maha ngā momo o amyloidosis. Ko te take o te mate, ko te tika ti'aturi i runga i te aha te momo o amyloidosis. He aha te mea te reira? kawea Whakarōpū i roto i rite ki te pūmua taketake, e ngā o fibrils amyloid. Kei raro he whakaaro o te mate.

1. amyloidosis Tuatahi (AL-amyloidosis). A, no te puta tona whanaketanga i roto i te wē mekameka immunoglobulin marama rerekē, e e taea ki te noho i roto i ngā kopa o te tinana. Waihoki ke i roto i ngā pūtau wē o myeloma maha, macroglobulinemia a Waldenström, hypergammaglobulinemia monoclonal.
2. amyloidosis Tuarua (AA-amyloidosis). I roto i tenei take ki reira he tuku nui o ate pūmua ārepa-globulin. Tenei pūmua wāhanga whakapeka synthesized e te i roto i te mumura ma'i. Ko te taea tenei i roto i te tini o nga mate, pērā i kaikōiwi, malaria, bronchiectasis, te tapû, repera, kohi.
3. amyloidosis Family (AF-amyloidosis). Ko te mate tuku ki tupu ngoikore autosomal. Kei te karanga a hoki reira Mediterranean kirika whānau taratahi paroxysmal ranei poliserozita. Faaite tenei whakaeke mate o kirika, te takanga o te mamae puku, rashes kiri, rumati, me kiripūkahu.
4. Ko te amyloidosis tātari (AH-amyloidosis). Kei te hono te reira ki te meka i tikanga te pūmua beta-2 microglobulin MHC i roto i te iwi hauora e o e nga whatukuhu, me kore e tātarihia reira i roto i te tātari toto, a pera ko tona whakaeminga i te tinana.
5. AE-amyloidosis. Kei te whakawhanake te reira i te tahi mau huru o te mate pukupuku, pērā i thyroid.
6. amyloidosis taipāpā.

tohu

A, no te whakawhirinaki te tātaritanga o "Amyloidosis" tohu i runga i te localization o putunga. Ki te taea te kitea te hinga o te wahi gastrointestinal arero rahi, mahi horomia waimaero, kōroke korere ranei. He pea putunga puku-amyloid i roto i te piro puku ranei.

amyloidosis o te whēkau tahi e te mana'o o te pouri, me te hūhi kia ngawari mamae puku. Ki te patua e te repe taiaki, ko te whakaatu i te taua tohu rite i roto i te pancreatitis. Ki te kite ate whara tona hua, whakapairuaki, te paowa, ruaki, haurangi, jaundice.

puta Amyloidosis romahā e whai ake:

• reo whango;
• tohu o te Bronchitis;
• amyloidosis puku pūkahukahu.

kia puta te tohu e whai ake nei i roto i amyloidosis o te pūnaha io:

• mania tahu sensation i roto i wahi, te kōpā (polyneuropathy piringa) ranei;
• ānini, whanoke;
• disorders sphincter (taikaha mimi, fecal).

Amyloidosis - he aha te mea te reira, kua arotakehia e matou ona take me tohu. Na titiro tatou ki te pehea pāngia te mate kei te me aha ngā tikanga o te maimoatanga te tīari.

tātaringa

I roto i te mate pērā i amyloidosis, he matatini tātaritanga. Whakaritea e te taiwhanga me taputapu rangahau.

I roto i te akoranga taiwhanga, kite he arotake whānui o te toto hua i roto i ESR, leukocytes ka heke tatau mōtepe. Ko te tātari whānui o te mimi pūmua he reira i roto i te waipara - rango, leukocytes me erythrocytes. I roto i te coprogram tapae nui o māngaro, ngako me te uaua muka. I roto i te mataora toto i roto i pāpaka o te ate whakakitea he cholesterol, bilirubin, phosphatase kawakore nui ake.

I roto i te amyloidosis tuatahi i roto i te mimi me te toto wē whakakitea te ihirangi tiketike o te amyloid. A, no te te tuarua i roto i ngā whakamātautau taiwhanga whakaatu tohu o mumura ma'i.

whakahaere hoki atu mehua tātaritanga:

• whakamātautau X-ray;
• echocardiography (i roto i te take o te whakaeke ngakau whakapae);
• assays mahi ki waikano;
• tinana unuhanga.

maimoatanga

A, no te kawea te mate te maimoatanga i roto i-manawanui. Amyloidosis, i roto i nei i reira he tikanga nui, pērā i täkihi ma'i kore ngakau kino tukinotia i roto i te hōhipera ranei.

I roto i te amyloidosis tuatahi tuatahi whakaritea taero pērā i "Chloroquine" "Melphalan" "prednisolone", "colchicine".

I roto i te amyloidosis tuarua hamani i te mate e whāriki ana, hei tauira, te tapû, kohi, pleural empyema et al., Tohu katoa o te amyloidosis maha riro i muri i rongoa.

Ki te whakawhanake i te mate rite ki te hua o te tākihi tātari toto, ka te whakawhitia te manawanui taua ki tātari peritoneal.

I roto i te take o uwhi korere whakamahia rongoā, pērā i "subnitrate bismuth," adsorbing kaihoko ranei.

kia hoki kia ratou maimoatanga symptomatic:

• teuteu whakaiti pēhanga;
• huaora, Diuretics;
• huhu wē, me ētahi atu

I tua atu, kia tono ai, me te maimoatanga hāparapara. amyloidosis o te kōateate kia taui i muri i te whakahekenga atu o te okana. I roto i te nuinga o te wā, arata'i tenei ki te whakapai ake i roto i te huru o te tūroro me te whakaiti i te hanganga o te amyloid.

kai

titau Amyloidosis kai tamau. Ki te whanaketanga o te mate tākihi ma'i e whakawhāiti horomanga tote, me ngā kai pūmua pērā i te kai, te ika, hua. Ki te whakawhanake ma'i kore ngakau, kia waho i te kai o te tote, he paowa me kai î.

amyloidosis cardiac

Kei te karanga a hoki tenei mate amyloid cardiomyopathy. Ki te taea tona whanaketanga o amyloid waipara puta i roto i te myocarditis, pericarditis, endocarditis, i runga i nga taiepa o te haoraora me iatuku pūngākau ranei. Ko te take mō tenei mate ngakau kia amyloidosis tuatahi, tuarua ranei te utuafare. E mea pinepine amyloidosis o te ngakau - e kore te mea he mate taratahi, a kei te whakawhanake i te reira i roto i te whakarara ki amyloidosis o te pūkahukahu, tākihi, whēkau kōateate ranei.

Tohu o amyloidosis cardiac

E mea pinepine te tohu o tenei mate he rite ki te cardiomyopathy hypertrophic mate ngakau coronary ranei. I te wāhanga tuatahi, he nuinga ki tohu. Kia wheako kārangirangi me te rohirohi, etahi mate taimaha, pupuhi o te kopa, me te whanoke.

te tikanga puta te ino koi i muri i tetahi ahotea mate romahā ranei. I muri i taua tikanga puta ngakau momo mamae angina pectoris, arrhythmia, edema korerotia, dyspnea, ate whakarahi. Kei te nuinga o te wā tuku iho te pēhanga toto.

kauneke tere te mate, me tona āhuatanga motuhake ko te ātete (ātete) ki therapy. I roto i ngā take kino, kia wheako tūroro ascites (haaputuputuraa o te wai i roto i te kōhao puku) effusion pericardial ranei. Nā ki te infiltrates amyloid whakawhanake pakohu bradycardia. Tenei e taea e arahi ki te mate ohorere.

outlook

I te ngakau amyloidosis waitohunga rawakore. kore ngakau Congestive i roto i tenei mate kauneke tamau a he tata te mate. I roto i Russia reira he kahore pokapū motuhake e pā ana ki tenei take.