HauoraRongoā

Hypogonadism Hypogonadotropic: tohumate, maimoatanga

Ka rite ki te tikanga, e pā ana hypogonadism hypogonadotropic ki underdevelopment o whēkau fakasekisualé, me te tuarua āhuatanga fakasekisualé. whakawhiti ngako me te pūmua i roto i te māuiuitanga takahia ano, e ai mōmona, cachexia, disorders o te pūnaha kōhiwi me te arā o te ngakau.

Na roto i te ara i te rata hamani?

Me kï reira e toa rerekē, me te hypogonadism hypogonadotropic wahine.

kawea te tātaritanga me te maimoatanga o te mate i roto i tahi endocrinologists, obstetricians me gynecologists, endokrinolongami ki ko te manawanui he wahine, me andrology, ki te ko te manawanui - tangata.

Ko te pūtake o te maimoatanga o te ira therapy. Ki te hiahiatia pokanga whakaaturia, pokanga kirihou.

Ka rite ki whakarōpūtia te mate te?

Ka taea e Hypogonadism e tuatahi, me te tuarua. Ko te puka tuatahi o te kiko testicular i roto i te ofatiraa whakakiki taumahinga tika ki te koha i te testes. i te pūira kia whakapataritari abnormalities taumata hypoplasia aplasia testicular ranei kikokiko, whakakitea nei i roto i te ngaro iti ranei secretion o androgens mo ratou hanga o te hanganga tonu o nga whekau taihemahema, me te āhuatanga fakasekisualé tuarua.

whakahuatia hypogonadism Hypogonadotropic i roto i nga tane kei roto i infantilism ira tangata.

meinga te puka tuarua e te takahi o te hanganga repe, whakaiti tona mahi gonadotrophic hinga ranei pokapū hypothalamic e whai pānga i runga i te repe, ka regulates tona mahi. kitea te mate i roto i disorders hinengaro.

kia congenital riro ranei e rua puka tuatahi, me te tuarua. kia whai wāhi te māuiuitanga ki pākoko tane i roto i te 40-60% o te wā.

Ko te take o te mate i roto i nga tangata

Ka taea te meinga moni iti o androgens i te hekenga i roto i te nui o hormones whakaputaina e te huru pathological testes ratou, takahi hypothalamus me te rapae o mahi ranei.

Na roto i te etiology faaiteraa tuatahi o te mate e taea te whakaaro:

  • congenital repe fakasekisualé underdevelopment, e puta ka te hē ira o huru,
  • aplasia o komurumurua.

kia ngā āhuatanga Predisposing:

  • takahi o te uri testicular;
  • te rongo ki matū paitini;
  • hahau;
  • pānga whakarewa i runga i te pūtake organic, nitrofurans, patukīrea, waipiro, tetracycline, e hāngai ana i runga i te raau taero taiki i roto i pota teitei, aha noa.;
  • āhua hopuhopu o te mate (repe, karawaka, orchitis, vesicles);
  • te aroaro o te iraruke mate;
  • riro māuiuitanga o te testes;
  • kowiria o te aho tātea;
  • na Uri o te testes;
  • tukanga atrophic i muri i te pokanga;
  • excision o te whaturama;
  • pokanga i roto i te Tunaroa.

I roto i te heke hypogonadism tuatahi i roto i te taumata o androgens i roto i te toto kitea te. Whakawhanake te whakautu e vai o nga repe adrenal, faarahi hanga o gonadotropins.

Ki te hanga i te hypothalamus mata me te rapae o disorders tuarua (ngā tukanga inflammatory, pukupuku, te ngangau i o te māuiuitanga whanaketanga fetal iaia).

Te whakatairanga i te whanaketanga o te hypogonadism tuarua taea:

  • rapae o adenoma, whakaputa taiki tupu;
  • taiki adrenocorticotropic (mate o Cushing);
  • prolactinoma;
  • pōrearea o te repe hypothalamus ranei i muri i te pokanga;
  • te tukanga koroheke, e ai te hekenga o testosterone i roto i te toto.

I roto i te puka tuarua tohua whakaiti o gonadotrophins, hua i roto i te hekenga androgen hanga i te testes.

Ko tētahi ahua o te mate, pā tangata, ko ki te whakaiti i te hanga o te parāoa ki te taupū testosterone noa. Varavara i reira he he heke i roto i ngā taumata testosterone i roto i te taumata noa purapura moenga o.

Tohutanga o te mate i roto i nga tangata

hypogonadism Hypogonadotropic i roto i nga tangata kua ona faaiteraa haumanu. E meinga ratou e tau o te manawanui, me te taumata o te iti hoki androgen.

Ki te patua nga komurumurua i te tamaiti i mua i pūhuruhurutanga, ka hanga e te reira i te syndrome angamaheni. Skeleton kupu riro tä nui. Ko te tika ki te roa i roto i te ossification o te rohe tupu tenei. Kei te hoki ërä pokohiwi me te pouaka i muri i roto i te whanaketanga, ko te roa o nga wahi, kei te ruarua whakawhanakehia uaua kōhiwi.

Ka taea te kite mōmona i runga i te momo wahine, gynecomastia, gipogenitalizme whakaaturia e te roto i te ure rahi iti, kahore he kita i te Tunaroa, hypoplasia testicular, te underdevelopment o te repeure, ko te ngaro o te huruhuru i roto i te rohe tore, te underdevelopment o te paeoro, te reo tiketike o te reo.

I roto i te faaiteraa tuarua o te mate pinepine kite taimaha tinana tiketike, faateiteihia e mahi uho adrenal, mahi thyroid waimaero.

Ki te heke mahi testicular te i muri i te pūhuruhurutanga o, te tohu o taua mate rite hypogonadotropic hypogonadism, taea te takina ngoikore.

Kite nga ari e whai ake nei:

  • whakaiti o testes;
  • iti mata huruhuru te tinana, me te tinana;
  • mate o te elasticity kiri me te thinning;
  • heke mahi fakasekisualé;
  • disorders autonomic.

Te hekenga i roto i te rahi testicular te pā ana tonu ki te hanga parāoa iti. Tenei ai pākoko, i reira te mea he inenga o ngā āhuatanga fakasekisualé Tuarua, tohua uaua ngoikore, te rohirohi.

Tātaritanga o te hypogonadism i roto i nga tangata

hanga tātaritanga e anthropometry, tirohanga me te palpation o nga kikokiko, aromatawai o tohu haumanu tohu pūhuruhurutanga.

ka tauturu i te X-ray whakamātautau ki te arotake i te wheua tau. Hei whakatau whakamahia te waiwai o te wheua kohuke densitometry te. A, no te x-hihi o te turcica Tira whakaritea e tona rahi me te aroaro o te pukupuku.

I whakaritea e o wheua tau taea hoki ki te wā o ossification o te ringa tahi me te ringa whakatau ka te tīmatanga o te pūhuruhurutanga. kia tango te reira i ki pūkete te taea o te mua (mō ngā tūroro i whanau i roto i te tonga) me muri mai (mō ngā tūroro i whanau i roto i te raki) ossification, rite pai rite te meka e taea te meinga osteogenesis whakararuraru, e te tahi atu āhuatanga.

Rangahau i runga i purapura moenga taiwhanga taea ki tatou te korero e pā ana ki ngā āhuatanga pērā i te hauota oligospermia ranei.

Tohua e te ihirangi o taua hormones:

  • gonadotropins moepuku;
  • katoa, me te free testosterone ;
  • luteinizing taiki;
  • GnRH;
  • ira antimyullerovsky;
  • prolactin;
  • estradiol.

A, no te nui haere te ahua tuatahi o te taupū mate o gonadotropins i toto me te tuarua - tukuhifo. I te tahi taime Ko to ratou taumata i roto i te ture tohatoha anō.

Whakatau i o serum estradiol tika ka feminization symptomatic me faaiteraa tuarua o mate i roto i te take o te pukupuku i roto i te testes whakaputa estrogen, ranei pukupuku i roto i te repe adrenal.

Taupū kia noa iti ranei te ihirangi o ketosteroids i te mimi. Ki te whakapae koe whakaaturia te aroaro o te tātari Klinefelter syndrome pūira pupuri.

e kore e taea ki te whakarato mōhiohio mō te tātaritanga tika unuhanga Testicular.

maimoatanga

hāngai maimoatanga o te hypogonadism hypogonadotropic te i te whakakore i te take matua o te māuiuitanga. Ko te whāinga o te therapy takoto i roto i ngā mahi ārai e whai wāhi ki te māori o te whanaketanga fakasekisualé, te whakaiti muri o te kiko testicular me testicular faaore te pākoko. whakahaere Therapy te i raro i te te tirotiro o te roma mimi me te tafe'anga.

Kia pehea te to'o hypogonadism hypogonadotropic i roto i nga tangata? Tei Treatment i runga i te maha o ngā āhuatanga:

  • puka haumanu o mate;
  • pakeke o te arā o te hypothalamus, te repe me te pūnaha whakaputa uri;
  • wātea e noho tahi pathologies;
  • wa o te tupu o te mate;
  • tau o te manawanui.

Maimoatanga o te wā pakeke ko ki te whakatika i te taumata o androgens me te whakakore pōrearea fakasekisualé. Pākoko, i whakatika i roto i te puka o te hypogonadism congenital, e kore e taea e te maimoatanga e.

I roto i te take o te momo tuatahi o abnormalities congenital mate riro ranei i te haumaru ngā pūtau endocrine i roto i te testes whakamahia stimulants. E tukinotia Boys āpiha kore-hormonal, me tūroro pakeke - taero e hāngai ana i runga i taiaki (androgen me gonadotropins i roto i pota iti).

Ki te kore testicular mahi tārua whakaaturia e androgen therapy whakakapi me te testosterone. kawea tango hormones te puta noa te ora.

A, no te Me te ahua tuarua o te mate i roto i ngā tamariki me ngā pakeke ki te whakamahi i taiki gonadotropin. Ki te tika, e ngā ratou ki hormones sex.

whakaaturia hoki he maimoatanga whakahou, me te mahi.

Mahi ki te mate, ko te ki te transplant te kura kākano ki cryptorchidism, whakamahia pokanga kirihou i roto i te ure underdeveloped. Ki te huihui Paku whakaaro ki te hua manu implantation waihanga e hāngai ana (i roto i te ngaro o te raho undescended i roto i te kōhao puku).

whakamahia Pokanga te ka whakamahi i ngā tikanga microsurgical, me te mana o te pūnaha ārai mate, taumata taiki, me te te okana marire ki.

I roto i heke therapy nahanaha androgen iti hoki, timata i te whanaketanga o ngā āhuatanga fakasekisualé Tuarua, mananga wāhanga iti, faaiteraa iti o osteoporosis me wheua tau takamuri.

Kia pehea te ko te mate i roto i nga wahine

hypogonadism Hypogonadotropic i roto i nga wahine āhuatanga e underdevelopment o te mahi fakasekisualé, me te nui haere repe ovarian. puka congenital te Paraimere e tika ki te kino underdevelopment ovarian ranei i roto i te wā fā'ele'i.

Kei te e tukupu ana te reira i te hanga o hormones sex, e whakaoho he hua i roto i te taumata o gonadotropins, e whakaongaonga te ovaries.

I roto i te tātaritanga o te auau tiketike o hormones e whakaongaonga follicles me lutein, me te taumata iti o estrogen. auau iti o estrogen ai atrophy ranei whekau uri wahine underdeveloped, repe mammary, ngaro o te paheketanga.

Ki te waimaero mahi ovarian i te aroaro o te pūhuruhurutanga o, na reira ko te kore o ngā āhuatanga fakasekisualé tuarua.

hypogonadism Hypogonadotropic i roto i nga wahine i roto i te tuatahi i rite tohua i roto i te tikanga e whai ake nei:

  • disorders congenital i te taumata ira;
  • hypoplasia congenital o te ovaries;
  • tukanga hopuhopu (pakewakewa, kohi, repe pupuhi, irradiation, tango hāparapara o te ovaries);
  • te hinga o te natura autoimmune;
  • syndrome, feminization testicular ;
  • ovaries polycystic.

Tuarua hypogonadism hypogonadotropic i roto i nga wahine puta i roto i te māuiuitanga o te rapae o me hypothalamus. Kei te kitea te reira e te iti mutunga ihirangi oti ranei o te hanga o gonadotropins whakahaere mahi ovarian. rongo ana tēnei tukanga e mumura o te rohe roro. Ēnei mate i te pānga ino, me e tahi e te hekenga i roto i te taumata o te te rongo o gonadotropins ki te ovaries.

Kia pehea te e pērā mate rite hypogonadism hypogonadotropic i roto i nga wahine, me te hapū? taea hoki te pānga whanaketanga intrauterine kino o te kukune i te takanga o te mate.

Tohu i roto i nga wahine

tohu Bright o wā whanautanga tamariki - ko te takahi o te paheke, ranei kore ona.

Ko te taumata iti o hormones wahine arata'i ki underdevelopment o whēkau sex, repe mammary, takahi o te waipara o huruhuru tinana momona, me te he kikokore.

Ki te he congenital i te natura te mate, tuarua āhuatanga fakasekisualé kore e puta. tuhia nga wahine te aroaro o te papatoiake kuiti, me papa flat.

Ki te puta te mate i mua i pūhuruhurutanga, nga āhuatanga fakasekisualé e puta ana ki te noho ora, engari marama poroa atrophy kiko taihemahema.

Servicing ko

Hypogonadism ka reira te mea he heke i roto i ngā taumata estrogen me ngā taumata hua o gonadotropins. Na roto i te ultrasound whakakitea iti i roto i te rahi kōpū pāngia ostepoporoz me whakaroa hanganga o te tuahiwi.

maimoatanga mate i roto i nga wahine

Kia pehea te to'o hypogonadism hypogonadotropic i roto i nga wahine? Treatment tā whakakapinga therapy. Women whakaritea ki te farii i rongoā me hormones sex (ethinyl estradiol).

I roto i te take o te tīmatanga o te paheketanga whakahau te whakawhānau waha kei roto estrogens me progestins, me taka "Triziston", "Trikvilar".

Tikanga "Klimov", "Trisekvens", "klimonorma" whakaritea ki te tūroro i muri i te 40 tau.

contraindicated maimoatanga taiki e i roto i te tikanga e whai ake nei:

  • puku matepukupuku i roto i te uma me te kikokiko;
  • ngakau, me te iaia mate;
  • täkihi me te ate;
  • thrombophlebitis.

ārai

Taua mate rite hypogonadotropic hypogonadism, kua he waitohunga pai. Prevention Ko te mātauranga hauora o te taupori, me te aroturuki o te wahine hapu, me te i roto i ngā mahi hauora.

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