HauoraDiseases me ngā Here

ALS (mate): Tohu me ngā tikanga tātaritanga

Ko te pūnaha io te tangata ko te tino whakaraerae. Ko te aha i reira e maha mate rerekē e taea pā tenei wahi ngā o te tinana. I roto i tenei tuhinga e hiahia ana ahau ki te kōrero e pā ana ki te mea ko ALS (mate). Tohu, take o te mate, me te tikanga o te tātaritanga me te maimoatanga taea.

He aha te mea te reira?

I roto i te timatanga, e hiahia ana koe ki te matau i te ariā taketake. Ko te hoki reira tino nui ki te matau ki ta te BAS (mate), tohu o te mate ka e kōrero he iti i muri mai. Whakamārama o whakapotonga: atrophic sclerosis lateral. A, no te pānga o te mate te pūnaha io o te tangata, ara mamae neurons nekeneke. E tū ana i roto i te uho kaka me i te haona he mārōrō, o te ua. Ko hoki reira utu te whakahua e ko te mate ma'i me, kāore, i te kau e kore e mahu.

momo

E hoki e toru ngā momo o te mate pērā i ALS:

  1. aronui tāmutumutu. E kore te reira riro. E pūkete reira hoki e pā ana ki 95% o te wā katoa o te mate.
  2. Tuku (whānau ranei). Ka rite ki meinga, kua mārama, kua riro te reira. Heoi, hoki tenei momo o te mate āhuatanga e te faaiteraa i muri o tohu.
  3. Guam-momo āhua o te Mariana ranei. whakakitea Ko tōna āhuatanga ahurei te aroaro o te rua i runga. whanaketanga puhoi o te mate.

Ko te tohu tuatahi

Ko reira utu mea e taea te tukinotia nga tohu tuatahi o te mate me te i roto i tetahi atu mate. Ko tenei ïa te raruraru o te tinihanga: ki te tātari tonu ko reira tata e taea. Na, ko te tohu tuatahi o ALS e whai ake nei:

  1. ngoikore uaua. Fele mai te reira ki te ponapona me waewae.
  2. Atrophy o nga ringa, ngoikore o uaua. Ka taea hoki te puta te reira i dysmotility.
  3. Tūroro i roto i nga tīmatanga o te mate kia paku ngehe kau mutu.
  4. Āhuatanga e wā mamae uaua. E taea tākiri ona pokohiwi, nga ringa, arero.
  5. whakawarea wahi. He manawanui ki te uaua e taea te haere atea roa.
  6. Ko reira ano hoki dysarthria ahua āhuatanga, i.e. whakararuraru, kupu.
  7. puta hoki horomia uaua tuatahi.

Ki te ALS (he mate) te manawanui, i nga tohu o te whanaketanga o ka whakawhanake te mate, tupu. Next, wā kia te manawanui ite ngahau gratuitous ranei pouri. Ka taea e Atrophy puta te reo, me te disequilibrium. Ko tenei katoa no te mea kei te te mamae te tangata mahi teitei hinengaro. I roto i ētahi wā, i mua i reira he tohu nui e taea whakapōrearea i mahi hinengaro. ie puta tupu (tenei puta Varavara, āhua 1-2% o ngā take).

haereraa i mate

He aha atu nui ki te mohio te iwi e hiahia i roto i ALS (mate)? Ka taea te mea tohu e puta i roto i te manawanui rite te mate e pā ana ki te mea rite tona momo o te mate:

  1. alangá ALS. Ko te waewae tuatahi e wahi hinga. Atu kauneke e alangá mo takahi mahi.
  2. ALS Bulbar. I roto i tenei take, nga tohu matua he mahi kupu takahi, me te raruraru ki te horomia. Ko reira utu mea e he nui iti noa atu i te tuatahi tenei momo o te mate.

hua i roto i te tohu

He aha e mohio i te manawanui e he mate rite ALS? Ka āta whakanui i tohumate, ka kia heke taumahinga alangá.

  1. Āta reira pathological Babinski, ka pāngia e neurons nekeneke o runga.
  2. oro uaua, ka kia whakarei reflexes ki kia ake.
  3. Ina e ka miharo, me raro neurons nekeneke. I roto i tenei take, ka ite te manawanui te jerking tumu o te wahi.
  4. I roto i tino maha i roto i tūroro tangata tenei whakawhanake korekore, i reira he wā. Katoa no te mea ngaro te tangata te kaha ki te ora, kahore tetahi awhina, ngaro reira te kaha ki te neke.
  5. pā hoki ALS tohu ki te pūnaha romahā: tīmata te manawanui te kupukupu tonu pōrearea.
  6. Hoki, e kore e taea ki te whaiaro te whakatutuki-. Kei te maha te manawanui whakaurua he ngongo i roto i nei te manako te tangata me te tika katoa mo te oraraa o te kai.

Ko reira utu mea kia puta ALS pretty wawe. Ko te tohu i te taitamariki tau e kore e waiho hei rerekē i tohu o te manawanui, nui i muri puta nei tohu tuatahi. Te reira i katoa tei runga i te tinana, kia rite ki te pai rite i runga i te momo o te mate. Ki te whanaketanga o te mate āta whakihauā tangata mona te kaha mo te ora motuhake. Neke atu i te wa, tino whakakahore te e alangá.

Ko te atamira whakamutunga

I roto i te wāhanga whakamutunga o te mate, ko te maha te manawanui mahi romahā waimaero, kore taea o nga uaua romahā. I roto i ngā take pēnei i, Me ventilation tūroro. Neke atu i te wa, ka taea e te whakawhanake i te mahi pana o te tinana, e maha arata'i ki te meka e honoa he mate tuarua, e atu whakamate te manawanui.

tātaringa

Ka whakaaro he mate rite ALS, tohu, tātaritanga - e te aha e hiahia ana ahau ki te korero ano hoki. Ko reira utu mea e kitea te mate te tino maha he tukanga o te whakakorenga o te tahi atu mau fifi ki te tinana. A, no te he manawanui e whai ake tikanga tātaritanga kia whakaritea ai:

  1. whakamātautau toto.
  2. unuhanga uaua.
  3. X-ray.
  4. Whakamātautau ki te whakatau mahi uaua.
  5. CT, MRI.

pārōnaki

Ko reira utu mea e he tohu e puta me ētahi atu mate te mate. reira i te mea e tika ana ki te rerekëtanga ALS ki te raruraru e whai ake nei:

  1. myelopathy waha.
  2. Haurangi i te konuoi, mata, konupora.
  3. pae wuruhi Syndrome.
  4. syndrome Malabsorption.
  5. Endocrinopathy et al.

maimoatanga

whakaaro Moka he mate rite ALS, tohu, maimoatanga - ko tenei te mea e hiahia ana hoki ki te utu i tokanga makehe. Ka rite ki kua whakahuatia i runga ake, e taea e kore te tino ora te reira. Heoi, i reira he taero e te tauturu i pōturi te akoranga o te mate. I roto i tenei take, maha tango tūroro rongoā pērā i "Riluzole", "Rilutek" (i nga ra katoa e rua he ra). He mea e taea ki te ārai i ngā rerenga o paku glutamine, he taonga e pā neurons nekeneke. Heoi, he pai hoki a reira e ngā tikanga o te maimoatanga, tona whāinga matua - te whawhai ki nga tohu matua:

  1. Ki te he te tumatatenga te manawanui, pōuritanga ia, kia kia whakaritea tranquilizers.
  2. A, no te mea nui uaua spasm ki te tango i relaxants uaua.
  3. Ki te hiahiatia, e taea te whakaritea rehunga, i te mutunga o te wā o te mate - opiates.
  4. Ki te mea kua ohorere te manawanui moe, Me taero benzodiazepine.
  5. Ki te reira te mea e hiahia ana he pōauautanga kitakita paturopi horomanga (ki bass maha whakatika mate bronchopulmonary).

Aids:

  1. Kōrero therapy.
  2. Slyunootosos te fariiraa i te tarukino pērā i "Amitriptyline" ranei.
  3. kai ngongo, kai.
  4. Ko te whakamahi o ngā whakaaro e taea whakarato kaupapa manawanui: moenga, tūru, e haere ana nga tokotoko, poroporo motuhake.
  5. Kia Me ventilation aunoa.

rongoā tuku iho, mahi werowero ngira hoki tenei mate e huakore. kia hoki kia mea te reira e ano hiahia maha e kore anake te manawanui ko tona utuafare te āwhina ki te kaihaumanu.

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