Beck sarcoidosis: tohumate, te ārai, take me ngā āhuatanga o te maimoatanga

Ko te rārangi o mate e kore e taea te huaketo e tangata kararehe ranei, me e kore maranga fakamahino'i noa te mutunga o ngā take, e kore iti rawa ko te mate Beck. Sarcoidosis - Ko tona ingoa nāianei. Kei te pāngia te reira i tino maha, kaua e nui ake 150 i roto o te 100 000 tangata, engari pānga ki te iwi i runga i fenua katoa, i roto i te hononga ki i whakaritea e te reira i te waehere ao i roto i te pūnaha o te whakarōpū o te ICD-10. Ko tenei ki te whakarite kia tākuta i roto i tetahi whenua reira māmā ki te whakatere ki te whakamāramatanga o te mate haavare e, tautooraa tahi ki te kitea maimoatanga hou, me te hohoro kitea te otinga tika, ina ko te manawanui i roto i te hinaaro i te tauturu.

Sarcoidosis - he aha te mea tenei?

Puta Beck Sarcoidosis ka ohorere timata te ngā whēkau tangata ki te wehe me te taui i ngā rōpū o ngā pūtau e taea o phagocytosis. Ko te nodules (granulomas) e hanga e e tenei tukanga, e kore ai e faaite mai ano i roto i tetahi ara meinga te ino nui i roto i te āhua o te hauora ranei. Ka taea e Granulomas tupu i roto i tetahi okana, tae atu i te ngakau, kanohi, whatukuhu, ate, engari te nuinga o maha paetata i roto i te pūkahukahu. He onge i roto i te sarcoidosis me tuhia anake i roto i te tino whakawarea tūroro ki te mate iti, e kore nei e i tukinotia aituā. Tata 10% o tūroro granulomas fakapapau i runga i to ratou ake, kahore rongoā. Te nuinga o te iwi e mate ana i te sarcoidosis, e rapu maimoatanga motuhake, me te kōrero i te pulmonologist, mafatu, ophthalmologist, toketā neave, dermatologist, rheumatologist.

History o whakahura

i whakaahuatia tuatahi Sarcoidosis e Beck (Bock), taote Ingarangi, dermatologist J. Hutchinson. I roto i te 1877, kite ia e rua tūroro: tangata-tau 53-tau, me te wahine-tau 64-tau, ko tona kiri i runga i nga waewae me ringa, he granulomas papura. I muri i 12 tau, te tākuta French Besnier whakaahuatia te akoranga o te mate i roto i te manawanui nei i rite granuloma o te ihu. I tua atu, i tenei manawanui he puku grayish-puru o nga taringa me maihao. Ahakoa o Besnier, he tākuta Norwegian Tsezar Bok whakamana histological whakamātautau rite granulomas a hoatu ana ratou e te ingoa o "sarcoidosis kiri Koló." Ia ite ano e taea puta i te nodules papura i mucous i roto i nga pūkahukahu, a tamata i te rata Swedish Schaumann ki systematize raraunga i runga i te mau faaiteraa rerekē o sarcoidosis. Ka rite ki te hua o te mate i huaina "mate o Besnier - Bock -. Schaumann" Tenei wā, me inaianei taea kitea e koe etahi tuhinga hauora.

whakarōpū International

Ko te ICD-10 pūnaha sarcoidosis Beck ai ngā rite tuatoru-piha mate. Tenei te tikanga e i roto i tona etiology whai wāhi wātea i te mate waimaero. E ai ki te waehere Putumōhio International whakaritea ki tenei mate D 86. granulomas Sarcoidosis motuhake tinana mate kua te tokomaha e whai ake nei:

• i roto i te pūkahukahu - D86.0;
• i roto i te taikiri - D86.1;
• e rua i roto i te pukapuka, me te i roto i te taikiri - D86.2;
• kiri - D86.3;
• pathogenesis kāore - D86.9.

Ki te pāngia sarcoidosis atu mate, te whai ake taua:

• tahi e te iridocyclitis mārōrō uveitis ranei - D86.8 + H22.1 *;
• pāpāngia o raru cranial - D86.8 + G53.2 *;
• ka arthropathy - D86.8 + M14,8 *;
• myocarditis - D86.8 + I41,8 *;
• i roto i myositis - D86.8 + M63.3 *.

Ko te whakarōpū o te āhua o te rere

Sarcoidosis Boeck nehenehe e tupu mai i roto i toru ngā:

1. tonu. I roto i te tūroro kua he whānui ino o te hauora, hopukanga ngoikore, mate o hokohoko ai kaha.

2. Koi. āhuatanga tēnei puka e peke pāmahana ohorere, taikiri rahi, pupuhi o te hononga iho e alangá.

3. Subacute. He he he kirika poipoi-rite, whānui tika.

Tohatoha hoki hanga whakangutungutu (e kore e taea te maimoatanga e).

Whakarōpū i te pakeke

rerekëtanga whakaahuatia te mate e toru nekehanga o te pakeke:

Tuatahi. Kua whakanuia te manawanui taikiri uma (bronchopulmonary, tracheobronchial, paratracheal, bifurcation).

Tuarua. Sarcoidosis Boeck tohu 2 āhuatanga i roto i taua e kitea te aronga inflammatory interstitial i roto i te pūkahukahu.

Tuatoru. Puta kakakīrehe (kakakīrehe) o pūkahukahu kikokiko, e kore e whakanuia te kōpuku intrathoracic, engari i hanga emphysema. Ratou, tahi ki te aronga o te kakakīrehe hanga conglomerates nui tatau. amuamu Tūroro o te mamae pouaka, hiahia rawakore, rohirohi nui, ngoikore, mare maroke, hāhā o te manawa, mamae i roto i te hononga.

He he he whakarōpū, e tāutu ana e rima ngā wāhanga o te sarcoidosis:

• Kore. timata te mate, engari kahore te pouaka X-ray whakaatu.
• Tuatahi. tīmata taikiri Intrasternal ki te tupu.
• Tuarua. He rahi taikiri, i roto i te kikokiko pūkahukahu timata ki te puta granulomas.
• Tuatoru. I roto i te pukapuka huringa kiko puta.
• A maha. kakakīrehe pūkahukahu.

etiology

e pā ana Sarcoidosis Beck ICD 10 whakahounga ki te mate e pā ana ki te mate waimaero rite ki te hua o ngā tūhuratanga maha whakakitea te tūranga o Hľa (antigens leukocyte tangata) i roto i te ahua o granulomas. Ko te kupu, te huanui kitea ki te Pare ki sarcoidosis ranei, i runga i te anga ke, i te reira tāpae e take te whakakitenga o te kino ki te roro, kanohi me ētahi atu whēkau.

Mārama whakapumautia e kore he ma'i pee sarcoidosis. Ko te meka e puta tenei mate i roto i te mau melo o te utuafare, e kore e whakahaere tikanga i roto i tona tuku tuku.

Pea tenei ko katoa e ko tino etahi e pā ana ki te etiology o te mate. whakahoki äta ki te pātai e pā te whanaketanga o te mate, ano. Scientists whakaaro e taea e ngā āhuatanga mōrearea:

• hopuhopu fungal ranei mate;
• hae;
• kino hau matū me kohu;
• kai tōtika rawakore;
• rauropi kino.

mātai tahumaero

Ki te kahore ano i whakapumautia ïa take o sarcoidosis Beck, te mātai tahumaero o te mate kei te pai mohiotia. Na, kua whakamatauria te reira e pā tenei mate iwi o reanga katoa, tae atu ki ngā tamariki taitamariki, engari atu maha e kitea i te reira i roto i te tūroro 20-40 tau te pakeke, me he wahine atu e pängia ana ki reira. Ngā iwi hoki kua etahi rerekētanga. Sarcoidosis iwi uaua mate i roto i te Middle Te Tai Rāwhiti ko Japan, me i India e pāngia reira i roto i te 150 o te 100 000. I roto i te wahi raki o Europe, whiwhi mate i 100 000 40 iwi i roto i te wahi tonga o nga whika e paku teitei. I roto i Ahitereiria pāngia mate Beck i roto i 92 ia 100 000 i roto i te United States i roto African Amelika ahua he 40-64 take, a i roto i te iwi ataahua-kiri whiwhi mate noa 10-14 take ia 100 000 tangata.

Ko reira maere e kaipaipa mamae i sarcoidosis iti pinepine atu i te hunga e kore e nei i tenei peu.

tohutanga

Sarcoidosis i roto i te tīmatanga o te wāhanga maha e kore tohumate. Ko te tikanga e kore te tangata e ara mōhio e whai ratou i tenei mate. Kei te tino mārama e kitea tenei nga tohu o te mate noa i te 3 nekehanga, ka reira mai te pera-ka karanga pūkahukahu me te ahua mediastinal o sarcoid o Boeck. I roto i tenei take, te nuinga o te tūroro tohu reira:

• mate o te hiahia;
• tau'a, lethargy;
• rohirohi (tuhia i te wa o te ti'ai te);
• pāmahana;
• mamae uaua;
• mate o te taimaha tinana;
• mare e kore te e tukinotia ki taero antitussive.

Taua amuamu Kei te maha kitea te tātaritanga o "matao" ranei "ARI", engari i te ahunga whakamua o sarcoidosis riro e tautohetia ana mare, hemoptysis itehia i runga i te kiri hei kitea granulomas. I roto i te heke mai, kia kore maimoatanga kanohi pāngia, ate, ngakau, me te tahi atu whēkau. Tohutanga i ia puka He āhuatanga āhuatanga. Hei tauira, momo i roto i te sarcoidosis D86.8 + H22.1 * taumaha kite, kamo matia, puta kanohi waiwai. A, no te pato koe D86.8 + I41,8 * whakaatu tohu o te kore ngakau, hāhā o te manawa, arrhythmia. A, no te pato koe D86.3 puta i runga i te nodosum erythema kiri. kia rite ratou he ohorere. Pāngia mata, ata horoia, shins.

tātaringa

He tohu rite ki tohu o ētahi atu mate Sarcoidosis Beck. I roto i te tikanga ki te tika rerekëtanga ki reira, titau te manawanui whakamātautau me te kōrero o te maha kaiwhakaako kōtaha kuiti, me te maha o ngā whakamātautau ki te tutakina:

• kohi;
• berylliosis (puta i roto i te whakapā ki te teriuma);
• rūmātiki;
• lymphoma (neoplasm mārere o te waitinana kōpuku);
• pāwera tauhohe ki tetahi mea;
• mate fungal.

Ko te manawanui mahi te tātari:

• toto (a matüora);
• mimi (katoa);
• ECG;
• bronchoscopy;
• ako wai horoi arahau;
• TB tauira;
• X-hihi (reira e taea te mahi i roto i te taha ki te he CT scan o te romahā pūnaha), ngā pai hua e whiwhi i multislice CT, me ki te Rapu granulomatous huringa o ngakau whakahau MRI;
• taroskopiya (whakamahia i roto i te wā uaua rawa).

US sarcoidosis Beck mahi transesophageal homaitanga pai hua i roto i te whakamātautau o intrathoracic taikiri ngā kōpuku. I te wa ano kawe i te unuhanga.

Ko tētahi atu momo o te rangahau - matawai ki gallium. Tenei whakarewa ahu ki te whakaemi i ngā pae o te mumura. I muri 2 ra i muri i whakahaere rō-uaua o te taonga karapa te manawanui te. Ko te ngoikoretanga Ko e taea gallium kohikohi i roto i tetahi o aronga inflammatory, ahakoa o ahakoa e meinga ratou e sarcoidosis atu mate ranei.

Maimoatanga o te sarcoidosis Beck

Ko te whāinga o te therapy mo tenei raruraru ko ki tiaki te mahi o nga whekau pāngia. Ki te he tohu pūkahukahu o te manawanui, kia whakakahoretia atu o ratou a muri ake.

A, no te rite ki te hua o nga whakamātautau katoa whakapumautia te tātaritanga o "sarcoidosis", whakatakoto te tākuta steroids. Ko te hua matua - "Prednisolone". Ko te akoranga o te maimoatanga he roa, ki runga ki te 8 marama. I roto i tenei take, i reira kia kia pānga taha:

• huamo;
• taonga taimaha;
• puku mamae;
• hīrere huru;
• takawhita;
• hakihaki.

I tango i te raau taero rawa hohoro reira ko te pānga pai, engari i muri i kia hoki tohu korenga atu o te mate.

Kua whakaritea e te pūnaha "Pentoxifylline", "Methotrexate" "Chloroquine."

Homai te meka e kia ngaro granulomas runga ratou ake, e kore e tūroro e whai sarcoidosis meinga tetahi hūhi mamae ranei, e kore e whakahau maimoatanga, engari he aroturuki auau o ratou mana hauora.

outlook

Ki te he te tātaritanga o "sarcoidosis Beck" e CT karapa, pouaka X-ray, unuhanga tātaritanga, hapa kēne kore Kia, engari koutou meatia e kore hiahia ki ngakaukore. E kore e te mate ki te maimoatanga tika whakaiti i te paerewa o te ora e kore e pā te kaha ki te mahi, me nga wahine me te mate, kahore tetahi raruraru hoatu whanau ki ngā tamariki hauora.

whakatika pōauautanga anake i roto i te wahi o nga tūroro e kahore i tukinotia i roto i te wā. kia whai ratou:

• iti hoki romahā;
• waimaerotanga kitenga nui, tae atu te matapo;
• whakahōhā o mate ā-.

Kua kore i whakawhanakehia Prevention o sarcoidosis tika ki te papu ore o tona etiology. Doctors hoatu anake whānui tūtohutanga:

• mau i te aratau tika o te ra;
• kouma ki te kai;
• e kore kino i te waipiro;
• karo whakapā ki matū mōrearea, tautautefito ki he pähekeheke nui, me te hau me te puehu.